Entry
Name
gamma-butyrobetaine dioxygenase;
alpha-butyrobetaine hydroxylase;
gamma-butyrobetaine hydroxylase;
butyrobetaine hydroxylase
Class
Oxidoreductases;
Acting on paired donors, with incorporation or reduction of molecular oxygen;
With 2-oxoglutarate as one donor, and incorporation of one atom of oxygen into each donor
BRITE hierarchy
Sysname
4-trimethylammoniobutanoate,2-oxoglutarate:oxygen oxidoreductase (3-hydroxylating)
Reaction(IUBMB)
4-trimethylammoniobutanoate + 2-oxoglutarate + O2 = 3-hydroxy-4-trimethylammoniobutanoate + succinate + CO2 [RN:
R02397 ]
Reaction(KEGG)
Substrate
Product
3-hydroxy-4-trimethylammoniobutanoate [CPD:
C00487 ];
succinate [CPD:
C00042 ];
CO2 [CPD:
C00011 ]
Comment
Requires Fe2+ and ascorbate.
History
EC 1.14.11.1 created 1972
Pathway
Orthology
K00471 gamma-butyrobetaine dioxygenase
Genes
CJC : 100394422(BBOX1) 108588064
CSYR : 103252126(BBOX1) 110595261
SANH : 107663933 107664378(bbox1)
CCAR : 109063114(bbox1) 109068675
CAUA : 113051502 113052336 113106019
CGIB : 127961459 128016894
PPRM : 120490975 120490980
MASI : 127415608 127446986
AMEX : 103030022(bbox1) 111196817
HSP : 118108668(bbox1) 124852240
SASA : 106561934 106587091
STRU : 115167548 115202859
OMY : 110506302(bbox1) 110526182
SALP : 111969205 111974271
CCLU : 121534845 121573297
BFO : 118406318 118406880 118413080 118414311 118415037
BBEL : 109464228 109464368 109465590 109467348 109467591 109470077 109471674 109475641 109480214
CIN : 100177042 100180618 100182414 100186683
SPU : 100889965 575977 577138 577198 579623 583892 585058 587148 589740
LPIC : 129268012 129268018 129268444 129268731 129268732 129268908 129268912 129271375 129271910 129271912
APLC : 110974962 110974969 110974990 110975081 110975086 110975110 110975114 110977463 110977489 110977490 110978498 110978503 110978522 110978525 110979659 110983900 110983902
SKO : 100369969 100370368 100372811 100373291 100375284 100375436
DME : Dmel_CG10814(CG10814) Dmel_CG4335(Tmlh) Dmel_CG5321(CG5321)
DER : 6549465 6550626 6555792
DSI : Dsimw501_GD16541(Dsim_GD16541) Dsimw501_GD17176(Dsim_GD17176) Dsimw501_GD25765(Dsim_GD25765)
DYA : Dyak_GE13368 Dyak_GE16657 Dyak_GE17150
DSR : 110179632 110180797 110181902
DPO : 4803347 4811764 6902106
DPE : 6590266 6596658 6598191
DMN : 108152659 108157945 108165313 117191682
DWI : 6644779 6646280 6652911
DGR : 6559209 6565424 6569571
DMO : Dmoj_GI14867 Dmoj_GI15613 Dmoj_GI19441
DAZ : 108617584 108619147 108619371
DNV : 108655202 108657295 108657477
DHE : 111595753 111600219 111601890
DVI : 6626970 6631921 6635597
CCAT : 101451345 101452432 101454364
BOD : 106614399 106615580 106618321 118681510 118683030
BDR : 105222381 105223355 105228811
RZE : 108368923 108374840 108380499
AOQ : 129239089 129245095 129246101 129248631
TDA : 119662457 119671817 119675680 119681874 119681877 119684258
MDE : 101891259 101893754 101894750 101901706
SCAC : 106086134 106086193 106086424 106088752
LCQ : 111680683 111682797 111686389 111690369
LSQ : 119604779 119607040 119614918
ECOE : 129938532 129945566 129948842
CLON : 129611143 129618773
AARA : 120896309 120900684
AFUN : 125762890 125770944
AALI : 118458667 118466547
CQU : CpipJ_CPIJ017090 CpipJ_CPIJ017091
CNS : 116336704 116345422 116352378
BCOO : 119073563 119083632 119084099
CCIN : 107264740 107272779
AROA : 105688365 105688485
APLN : 108734955 108741047
PPYR : 116167504 116167505
MSEX : 115442174 115448305
BANY : 112047972 112056982
MCIX : 123654700 123670417
PRAP : 110993693 110994511 110994526
SLIU : 111353505 111358694
CFEL : 113376019 113376022
ACOO : 126843279 126844268
DVT : 126899569 126907448 126907449
MQU : 128985854 128991692 128991698 128992553
SGRE : 126335656 126335709
IEL : 124161839 124164324 124166406
DPX : DAPPUDRAFT_207173 DAPPUDRAFT_226211
PVM : 113805135 113805144 113810030 113814498 113815222 113825853 113827416 113828032 113828035
PJA : 122246670 122254394 122257250 122257399 122259157 122259158 122262247 122262250
PCHN : 125030738 125035789 125036116 125038177 125038190 125042433 125045149 125045150 125046264 125046914
PMOO : 119582636 119582637 119590027 119590597 119591569 119594337 119594384
HAME : 121854913 121855918 121864667 121865395 121865979 121877065 121877068 121877069
PCLA : 123758441 123762277 123766850 123768337 123769803
CQD : 128688583 128696905 128699607
PTRU : 123499459 123502521 123504064 123504153 123504657 123509641 123513856 123514360
ESN : 126990151 127000671 127004687 127005110 127006107 127007228 127007229 127007881
MNZ : 135197224 135220735 135221100 135221753 135221754 135221779 135224425 135224426 135224428 135224429 135224430 135224432 135224433 135224758 135224974
HAZT : 108665978 108673585 108679774
PPOI : 119093278 119108046 119108052 119108379 119110159 119112458
LPOL : 106463290 106470568
CEL : CELE_D2089.5(gbh-1) CELE_M05D6.7(gbh-2)
CBR : CBG_00615(Cbr-gbh-2) CBG_03032(Cbr-gbh-1)
CRQ : GCK72_004971 GCK72_005477
PVUL : 126816613 126821601
HRF : 124119266 124124252 124124259 124125027 124148499
HRJ : 124272863 124272870 124272871 124283682
PMAX : 117323167 117327120 117327668 117328112
LAK : 106151224 106152800 106161769 106171134
NVE : 5502526 5505091 5508199 5508203 5508209 5508786 5512084 5512115
EPA : 110233932 110238609 110242440 110247248 110247300
ATEN : 116288368 116301523 116301528 116304158
ADF : 107327306 107327319 107327320 107331124
AMIL : 114962821 114969251 114969252 114969267 114972035
PDAM : 113669897 113670005 113681509 113682405 113682406
SPIS : 111324369 111329098 111332334
DGT : 114524405 114524406 114526928 114533500 114533542 114535633 114535646 114541915
XEN : 124433681 124433682 124445566 124445567 124445568 124445569 124446777 124446848 124446854 124447000
TAD : TRIADDRAFT_13890 TRIADDRAFT_25346 TRIADDRAFT_25731 TRIADDRAFT_26039 TRIADDRAFT_33849 TRIADDRAFT_34256 TRIADDRAFT_34259 TRIADDRAFT_38529 TRIADDRAFT_61648 TRIADDRAFT_62652
NHE : NECHADRAFT_45388 NECHADRAFT_48822
CCAC : CcaHIS019_0202290(CcaverHIS019_0202290) CcaHIS019_0211440(CcaverHIS019_0211440)
ADL : AURDEDRAFT_140056 AURDEDRAFT_184813
SCM : SCHCO_02671376(SCHCODRAFT_02671376)
SMIN : v1.2.010310.t1(symbB.v1.2.010310.t1) v1.2.029451.t1(symbB.v1.2.029451.t1)
EHX : EMIHUDRAFT_313257 EMIHUDRAFT_357110
PAZO : AYR47_04540 AYR47_20405
PMAO : PMYSY11_3768 PMYSY11_3769
PNB : NK667_08170 NK667_29920
CSA : Csal_0540 Csal_2770 Csal_3171
CCAG : SR908_04770 SR908_10245
HEL : HELO_1569 HELO_2757 HELO_2759
HHU : AR456_09255 AR456_09265
HSI : BOX17_04605 BOX17_07480 BOX17_10405
HBE : BEI_0652 BEI_1556 BEI_1559 BEI_3127
HAF : C8233_03150 C8233_10025 C8233_14370 C8233_17355
HBH : E4T21_14335 E4T21_14350
HHAO : QWG60_02995 QWG60_09620 QWG60_09630
CMAI : BFX80_03010 BFX80_06240 BFX80_09875 BFX80_16080
CAMH : LCW13_01220 LCW13_08145 LCW13_11270 LCW13_14205
COBE : CLAM6_02410 CLAM6_13450 CLAM6_15520 CLAM6_22750 CLAM6_28910
COBB : H2O77_01115 H2O77_08130 H2O77_11585 H2O77_14610
PAUR : FGL86_03530 FGL86_03565 FGL86_07300
MARS : A8C75_16655 A8C75_21935
MRZ : KDW95_04220 KDW95_16910
LAP : ACP90_09620 ACP90_19975
LABR : CHH27_00295 CHH27_10980
LABT : FIU93_15180 FIU93_26520
LAGG : B0E33_03695 B0E33_21555
SIT : TM1040_0052 TM1040_2006
FAQ : G5B39_15310 G5B39_15515
HTQ : FRZ44_32130 FRZ44_47990
HADH : FRZ61_09040 FRZ61_15530 FRZ61_45660
SNEA : NBZ79_09335 NBZ79_14355
MMAE : MMARE11_06410(tauD_1)
MPRO : BJP34_15525 BJP34_27290 BJP34_30050 BJP34_34645
» show all
Taxonomy
Reference
Authors
Lindstedt G, Lindstedt S.
Title
Cofactor requirements of gamma-butyrobetaine hydroxylase from rat liver.
Journal
J Biol Chem 245:4178-86 (1970)
Other DBs
ExPASy - ENZYME nomenclature database: 1.14.11.1