KEGG   ENZYME: 2.4.1.275
Entry
EC 2.4.1.275                Enzyme                                 
Name
neolactotriaosylceramide beta-1,4-galactosyltransferase;
beta4Gal-T4;
UDP-galactose:N-acetyl-beta-D-glucosaminyl-(1->3)-beta-D-galactosyl-(1->4)-beta-D-glucosyl-(1<->1)-ceramide beta-1,4-galactosyltransferase;
lactotriaosylceramide beta-1,4-galactosyltransferase (incorrect)
Class
Transferases;
Glycosyltransferases;
Hexosyltransferases
Sysname
UDP-alpha-D-galactose:N-acetyl-beta-D-glucosaminyl-(1->3)-beta-D-galactosyl-(1->4)-beta-D-glucosyl-(1<->1)-ceramide 4-beta-D-galactosyltransferase
Reaction(IUBMB)
UDP-alpha-D-galactose + N-acetyl-beta-D-glucosaminyl-(1->3)-beta-D-galactosyl-(1->4)-beta-D-glucosyl-(1<->1)-ceramide = UDP + beta-D-galactosyl-(1->4)-N-acetyl-beta-D-glucosaminyl-(1->3)-beta-D-galactosyl-(1->4)-beta-D-glucosyl-(1<->1)-ceramide [RN:R05977 R09755]
Reaction(KEGG)
R05977(G) R09755
Substrate
UDP-alpha-D-galactose [CPD:C00052];
N-acetyl-beta-D-glucosaminyl-(1->3)-beta-D-galactosyl-(1->4)-beta-D-glucosyl-(1<->1)-ceramide [CPD:C04845]
Product
UDP [CPD:C00015];
beta-D-galactosyl-(1->4)-N-acetyl-beta-D-glucosaminyl-(1->3)-beta-D-galactosyl-(1->4)-beta-D-glucosyl-(1<->1)-ceramide [CPD:C04922]
History
EC 2.4.1.275 created 2011, modified 2013
Pathway
ec00601  Glycosphingolipid biosynthesis - lacto and neolacto series
ec01100  Metabolic pathways
Orthology
K07969  beta-1,4-galactosyltransferase 4
Genes
HSA8702(B4GALT4)
PTR100608173(B4GALT4)
PPS100994562(B4GALT4)
GGO101146705(B4GALT4)
PON100443591(B4GALT4)
NLE100600025(B4GALT4)
HMH116466914(B4GALT4)
MCC711983(B4GALT4)
MCF102142820(B4GALT4)
MTHB126947755
MNI105470345(B4GALT4)
CSAB103228234(B4GALT4)
CATY105589723(B4GALT4)
PANU101019227(B4GALT4)
TGE112618410(B4GALT4)
MLEU105544630(B4GALT4)
RRO104657610(B4GALT4)
RBB108531771(B4GALT4)
TFN117083477(B4GALT4)
PTEH111543736(B4GALT4)
CANG105510722(B4GALT4)
CJC100402903(B4GALT4)
SBQ101029385(B4GALT4)
CIMI108296461(B4GALT4)
CSYR103257478(B4GALT4)
MMUR105879930(B4GALT4)
LCAT123630518(B4GALT4)
PCOQ105808837(B4GALT4)
OGA100965108(B4GALT4)
MMU56375(B4galt4)
MCAL110311536(B4galt4)
MPAH110329539(B4galt4)
RNO303923(B4galt4)
MCOC116085906(B4galt4)
ANU117718186(B4galt4)
MUN110555392(B4galt4)
CGE100689435(B4galt4)
MAUA101840266(B4galt4)
PROB127227166(B4galt4)
PLEU114701494(B4galt4)
MORG121461767(B4galt4)
MFOT126505726
AAMP119824226(B4galt4)
NGI103741937(B4galt4)
HGL101723638(B4galt4)
CPOC100735550(B4galt4)
CCAN109694543(B4galt4)
DORD105987926(B4galt4)
DSP122097753(B4galt4)
PLOP125351722(B4galt4)
NCAR124993410
MMMA107136294(B4galt4)
OCU100357504
OPI101535740(B4GALT4)
TUP102470291(B4GALT4)
GVR103598136(B4GALT4)
CFA608143(B4GALT4)
CLUD112677857(B4GALT4)
VVP112913456(B4GALT4)
VLG121471564(B4GALT4)
NPO129503953(B4GALT4)
AML100481658(B4GALT4)
UMR103678795(B4GALT4)
UAH113251830(B4GALT4)
UAR123784036(B4GALT4)
ELK111150160
LLV125097716
MPUF101682220(B4GALT4)
MNP132012207(B4GALT4)
MLK131825095(B4GALT4)
NVS122908528(B4GALT4)
ORO101385802(B4GALT4)
EJU114214700(B4GALT4)
ZCA113917141(B4GALT4)
MLX118007075(B4GALT4)
NSU110582414(B4GALT4)
LWW102743563(B4GALT4)
FCA101100325(B4GALT4)
PYU121026811 121026814
PCOO112850255(B4GALT4)
PBG122491467(B4GALT4)
LRUF124526974
PTG102966539(B4GALT4)
PPAD109266428(B4GALT4)
PUC125920984
AJU106980243
HHV120223122(B4GALT4)
BTA511328(B4GALT4)
BOM102279871(B4GALT4)
BIU109576562(B4GALT4)
BBUB102407421(B4GALT4)
BBIS104992470(B4GALT4)
CHX102190262(B4GALT4)
OAS101104949(B4GALT4)
BTAX128050393(B4GALT4)
ODA120871334(B4GALT4)
CCAD122445575(B4GALT4)
MBEZ129560034(B4GALT4)
CFR102522848(B4GALT4)
CBAI105081587(B4GALT4)
CDK105090333(B4GALT4)
VPC102543992(B4GALT4)
BACU103005928(B4GALT4)
LVE103084555(B4GALT4)
OOR101278923(B4GALT4)
DLE111166843(B4GALT4)
PCAD102977710(B4GALT4)
PSIU116753398(B4GALT4)
NASI112414210(B4GALT4)
ECB100071082(B4GALT4)
EPZ103547412(B4GALT4)
EAI106823399(B4GALT4) 106840352
MYB102243483(B4GALT4)
MYD102775104(B4GALT4)
MMYO118677233(B4GALT4)
MLF102424615(B4GALT4)
MNA107527210(B4GALT4)
PKL118723891(B4GALT4)
EFUS103290708(B4GALT4)
HAI109386911(B4GALT4)
DRO112320685(B4GALT4)
SHON118986581(B4GALT4)
AJM119059204(B4GALT4)
PDIC114491006(B4GALT4)
PHAS123826745(B4GALT4)
MMF118617345(B4GALT4)
RFQ117012959(B4GALT4)
PPAM129069631(B4GALT4)
PALE102879802(B4GALT4)
PGIG120586651(B4GALT4)
PVP105302719(B4GALT4)
RAY107508361(B4GALT4)
MJV108408457(B4GALT4)
TOD119257499(B4GALT4)
SARA101538619(B4GALT4)
LAV100662008(B4GALT4)
TMU101352100
ETF101662346(B4GALT4)
DNM101427468(B4GALT4)
MDO100015888(B4GALT4)
GAS123239480(B4GALT4)
SHR100933479(B4GALT4)
AFZ127554104
PCW110208058(B4GALT4)
OAA114817430(B4GALT4)
GGA418341(B4GALT4)
PCOC116242431(B4GALT4)
MGP100547867(B4GALT4)
CJO107320407(B4GALT4)
TPAI128091583(B4GALT4)
LMUT125688131(B4GALT4)
NMEL110399397(B4GALT4)
APLA101792176(B4GALT4)
ACYG106037583(B4GALT4)
CATA118245195(B4GALT4)
AFUL116496664(B4GALT4)
TGU100230291(B4GALT4)
LSR110480885(B4GALT4)
SCAN103827100(B4GALT4)
PMOA120506431(B4GALT4)
OTC121339348(B4GALT4)
PRUF121351674(B4GALT4)
GFR102034782(B4GALT4)
FAB101809954(B4GALT4)
OMA130248786(B4GALT4)
PHI102108146(B4GALT4)
PMAJ107205999(B4GALT4)
CCAE111939072(B4GALT4)
CCW104687053(B4GALT4)
CBRC103613891(B4GALT4)
ETL114055096(B4GALT4)
ZAB102070358(B4GALT4)
ACHL103806959(B4GALT4)
SVG106861701(B4GALT4)
MMEA130582236(B4GALT4)
HRT120749274(B4GALT4)
FPG101915659(B4GALT4)
FCH102051115(B4GALT4)
CLV102093764(B4GALT4)
EGZ104126497(B4GALT4)
NNI104008639(B4GALT4)
PCRI104027586(B4GALT4)
PLET104616698(B4GALT4)
EHS104515315(B4GALT4)
PCAO104053136(B4GALT4)
ACUN113483816(B4GALT4)
TALA104365156(B4GALT4)
PADL103921433(B4GALT4)
AFOR103894987(B4GALT4)
ACHC115343602(B4GALT4)
HALD104325247(B4GALT4)
HLE104831696(B4GALT4)
AGEN126048934
GCL127016354
CCRI104165245(B4GALT4)
CSTI104557932(B4GALT4)
CMAC104485873(B4GALT4)
MUI104545693(B4GALT4)
BREG104634611(B4GALT4)
FGA104074553(B4GALT4)
GSTE104259789(B4GALT4)
LDI104344499(B4GALT4)
MNB103777280
OHA104328249(B4GALT4)
NNT104412010(B4GALT4)
SHAB115601472(B4GALT4)
DPUB104298665(B4GALT4)
PGUU104458150(B4GALT4)
ACAR104528881(B4GALT4)
CPEA104389259(B4GALT4)
AVIT104278920(B4GALT4)
CVF104281854(B4GALT4)
RTD128908089(B4GALT4)
CUCA104055805(B4GALT4)
TEO104370239(B4GALT4)
BRHI104497986(B4GALT4)
AAM106490705(B4GALT4)
AROW112960462(B4GALT4)
NPD112951788(B4GALT4)
TGT104566934(B4GALT4)
DNE112989408(B4GALT4)
SCAM104144280(B4GALT4)
ASN102370808(B4GALT4)
AMJ102569919(B4GALT4)
CPOO109319251(B4GALT4)
GGN109304505(B4GALT4)
PSS102453780(B4GALT4)
CMY102946330(B4GALT4)
CCAY125621393(B4GALT4)
DCC119852571(B4GALT4)
CPIC101953425(B4GALT4)
TST117886849(B4GALT4)
CABI116825981
MRV120400130(B4GALT4)
ACS100553568(b4galt4)
ASAO132772081(B4GALT4)
PVT110074021(B4GALT4)
SUND121925377(B4GALT4)
PBI103068176(B4GALT4)
PMUR107287653(B4GALT4)
CTIG120300789(B4GALT4)
TSR106549008(B4GALT4)
PGUT117662153(B4GALT4)
APRI131199571(B4GALT4)
PTEX113441668(B4GALT4)
NSS113421481(B4GALT4)
VKO123029121(B4GALT4)
PMUA114595809(B4GALT4)
PRAF128412744(B4GALT4)
ZVI118085493(B4GALT4)
HCG128352179(B4GALT4)
GJA107106045(B4GALT4)
STOW125430629(B4GALT4)
EMC129325976(B4GALT4)
XLA108707823(b4galt4.L) 444709(b4galt4.S)
XTR100488464(b4galt4)
NPR108797173(B4GALT4)
RTEM120928030(B4GALT4)
BBUF120994392(B4GALT4)
BGAR122930604(B4GALT4)
MUO115470620(B4GALT4)
GSH117359951(B4GALT4)
DRE492760(b4galt4)
SRX107719754 107752248(b4galt4)
SANH107662077 107702948
SGH107557767(b4galt4) 107576632
CCAR109059855 109105806
CAUA113086208 113094244
CGIB127958879 127991291
PTET122324890(b4galt4)
LROH127165952(b4galt4)
OMC131540386(b4galt4)
PPRM120472161(b4galt4)
RKG130082523(b4galt4)
MAMB125267779(b4galt4)
CIDE127512966
MASI127426252 127435954
TROS130550097(b4galt4) 130568376
TDW130420135(b4galt4)
MANU129441095(b4galt4)
IPU108260163
IFU128603803(b4galt4)
PHYP113531354(b4galt4)
SMEO124378852(b4galt4)
TFD113650901(b4galt4)
TVC132841028(b4galt4)
AMEX103042661(b4galt4)
CMAO118814829(b4galt4)
EEE113587379(b4galt4)
CHAR105904396(b4galt4)
TRU101061200(b4galt4)
TFS130537421(b4galt4)
TNGGSTEN00019044G001
LCO104935626(b4galt4)
NCC104965999(b4galt4)
TBEN117490772(b4galt4)
CGOB115018943
PGEO117458582(b4galt4)
GACU117536977(b4galt4)
ELY117271675(b4galt4)
EFO125897803(b4galt4)
PLEP121953054(b4galt4)
SLUC116064910(b4galt4)
ECRA117956097(b4galt4)
ESP116700058(b4galt4)
PFLV114566193(b4galt4)
GAT120822075(b4galt4)
PPUG119215836(b4galt4)
AFB129113568(b4galt4)
CLUM117743181(b4galt4)
MSAM119895361(b4galt4)
SCHU122887908(b4galt4)
CUD121518801(b4galt4)
ALAT119031748(b4galt4)
MZE101466383(b4galt4)
ONL100692349(b4galt4)
OAU116336153(b4galt4)
OLA101164915(b4galt4)
OML112142420(b4galt4)
XMA102221477(b4galt4)
XCO114152935(b4galt4)
XHE116728667(b4galt4)
PRET103475412(b4galt4)
PFOR103141626(b4galt4)
PLAI106959946(b4galt4)
PMEI106911344(b4galt4)
GAF122844987(b4galt4)
PPRL129368814(b4galt4)
CVG107096681(b4galt4)
CTUL119778358(b4galt4)
GMU124876934(b4galt4)
NFU107386424(b4galt4)
KMR108237029(b4galt4)
ALIM106526137(b4galt4)
NWH119420190(b4galt4)
AOCE111587187(b4galt4)
MCEP125020865(b4galt4)
CSEM103395579
POV109628818(b4galt4)
SSEN122780202(b4galt4)
HHIP117774906(b4galt4)
HSP118122401(b4galt4)
LCF108893526
SDU111234517(b4galt4)
SLAL111666268(b4galt4)
XGL120802943(b4galt4)
HCQ109517999(b4galt4)
SSCV125982003
SBIA133491369 133491770(b4galt4) 133492114 133492193
PEE133416413(b4galt4)
PTAO133467356(b4galt4)
BPEC110158487(b4galt4)
MALB109959384(b4galt4)
BSPL114869417(b4galt4)
SJO128371518(b4galt4)
SASA106563608(b4galt4) 106603047
STRU115154807 115204411
OTW112228922 112231206
OMY110510090(b4galt4) 110534104
OGO124006477 124007296(b4galt4)
ONE115116498 115135528
OKI109873181 109874262(b4galt4)
OKE118385022(b4galt4) 118390473
SALP111950662 111964307(b4galt4)
SNH120021475 120057301
CCLU121541939(b4galt4) 121579577
ELS105010876(b4galt4)
SFM108924680(b4galt4)
PKI111838050(b4galt4)
AANG118235907(b4galt4)
LOC102693001(b4galt4)
PSPA121302655 121321209
ARUT117405908 117972656
PSEX120523099(b4galt4)
LCM102355454 102358769
CMK103185094(b4galt4)
RTP109921819(b4galt4)
CPLA122555032(b4galt4)
HOC132821014(b4galt4)
LERI129702618(b4galt4)
PMRN116955899
CIN100182391
NLU120350325
PCLA123755135
CQD128701344
TCF131888569
GAE121388902
HRF124121890
HRJ124258766 124269138 124269671
CANU128159955 128173497 128180866 128180868
MMER123562190
RPHI132731522
 » show all
Reference
1  [PMID:9792633]
  Authors
Schwientek T, Almeida R, Levery SB, Holmes EH, Bennett E, Clausen H
  Title
Cloning of a novel member of the UDP-galactose:beta-N-acetylglucosamine beta1,4-galactosyltransferase family, beta4Gal-T4, involved in glycosphingolipid biosynthesis.
  Journal
J Biol Chem 273:29331-40 (1998)
DOI:10.1074/jbc.273.45.29331
  Sequence
[hsa:8702]
Other DBs
ExplorEnz - The Enzyme Database: 2.4.1.275
IUBMB Enzyme Nomenclature: 2.4.1.275
ExPASy - ENZYME nomenclature database: 2.4.1.275
BRENDA, the Enzyme Database: 2.4.1.275

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