KEGG   ENZYME: 2.4.1.88
Entry
EC 2.4.1.88                 Enzyme                                 
Name
globoside alpha-N-acetylgalactosaminyltransferase;
uridine diphosphoacetylgalactosamine-globoside alpha-acetylgalactosaminyltransferase;
Forssman synthase;
globoside acetylgalactosaminyltransferase;
UDP-N-acetyl-D-galactosamine:N-acetyl-D-galactosaminyl-1,3-D-galactosyl-1,4-D-galactosyl-1,4-D-glucosylceramide alpha-N-acetyl-D-galactosaminyltransferase;
UDP-N-acetyl-D-galactosamine:N-acetyl-D-galactosaminyl-(1->3)-D-galactosyl-(1->4)-D-galactosyl-(1->4)-D-glucosyl-(1<->1)-ceramide alpha-N-acetyl-D-galactosaminyltransferase
Class
Transferases;
Glycosyltransferases;
Hexosyltransferases
Sysname
UDP-N-acetyl-alpha-D-galactosamine:N-acetyl-beta-D-galactosaminyl-(1->3)-alpha-D-galactosyl-(1->4)-beta-D-galactosyl-(1->4)-beta-D-glucosyl-(1<->1)-ceramide alpha-N-acetyl-D-galactosaminyltransferase
Reaction(IUBMB)
UDP-N-acetyl-alpha-D-galactosamine + N-acetyl-beta-D-galactosaminyl-(1->3)-alpha-D-galactosyl-(1->4)-beta-D-galactosyl-(1->4)-beta-D-glucosyl-(1<->1)-ceramide = UDP + N-acetyl-alpha-D-galactosaminyl-(1->3)-N-acetyl-beta-D-galactosaminyl-(1->3)-alpha-D-galactosyl-(1->4)-beta-D-galactosyl-(1->4)-beta-D-glucosyl-(1<->1)-ceramide [RN:R04182 R05965]
Reaction(KEGG)
R04182 R05965(G);
(other) R11322(G)
Substrate
UDP-N-acetyl-alpha-D-galactosamine [CPD:C00203];
N-acetyl-beta-D-galactosaminyl-(1->3)-alpha-D-galactosyl-(1->4)-beta-D-galactosyl-(1->4)-beta-D-glucosyl-(1<->1)-ceramide
Product
UDP [CPD:C00015];
N-acetyl-alpha-D-galactosaminyl-(1->3)-N-acetyl-beta-D-galactosaminyl-(1->3)-alpha-D-galactosyl-(1->4)-beta-D-galactosyl-(1->4)-beta-D-glucosyl-(1<->1)-ceramide
History
EC 2.4.1.88 created 1976
Pathway
ec00603  Glycosphingolipid biosynthesis - globo and isoglobo series
ec01100  Metabolic pathways
Orthology
K00722  globoside alpha-N-acetylgalactosaminyltransferase
Genes
HSA26301(GBGT1)
PTR464823(GBGT1)
PPS100978291(GBGT1)
GGO101145846(GBGT1)
PON100453106(GBGT1)
NLE100590023(GBGT1)
HMH116475812(GBGT1)
MCC106993582(GBGT1)
MCF102119767(GBGT1)
MTHB126937017
MNI105464077(GBGT1)
CSAB103239703(GBGT1)
PANU103881072(GBGT1)
TGE112607917(GBGT1)
MLEU105542947(GBGT1)
RRO104669732(GBGT1)
RBB108513510(GBGT1)
TFN117073852(GBGT1)
PTEH111524005(GBGT1)
CANG105503988(GBGT1)
CJC103795439(GBGT1)
SBQ104652637(GBGT1)
CIMI108295417(GBGT1)
CSYR103250924(GBGT1)
MMUR105859872(GBGT1)
LCAT123646556(GBGT1)
PCOQ105806630(GBGT1)
OGA105887449(GBGT1)
MMU227671(Gbgt1)
MCAL110290105(Gbgt1)
MPAH110319298(Gbgt1)
RNO499764(Gbgt1)
MCOC116089896(Gbgt1)
ANU117702057 117702485 117702823(Gbgt1)
MUN110549880(Gbgt1)
CGE100771256(Gbgt1)
MAUA101832682(Gbgt1)
PROB127222675(Gbgt1)
PLEU114702787(Gbgt1)
MORG121462826(Gbgt1)
MFOT126509254
AAMP119819957(Gbgt1)
HGL101726516(Gbgt1)
CPOC100736120(Gbgt1)
CCAN109690998(Gbgt1)
DORD105989368(Gbgt1)
DSP122109016(Gbgt1)
PLOP125353223(Gbgt1)
NCAR124964855
MMMA107151970(Gbgt1)
TUP102477690(GBGT1)
GVR103582072(GBGT1)
CFA403833(GBGT1)
CLUD112677377(GBGT1)
VVP112928011(GBGT1)
VLG121473804(GBGT1)
NPO129516418(GBGT1)
AML100479644 117800745
UMR103670247(GBGT1)
UAH113266556(GBGT1)
UAR123775725(GBGT1)
ELK111146249
LLV125083159
MPUF101672439(GBGT1)
MNP132024290(GBGT1)
MLK131813172(GBGT1)
NVS122917135(GBGT1)
ORO101386326(GBGT1)
EJU114198874(GBGT1)
ZCA113935141(GBGT1)
MLX118017554(GBGT1)
NSU110581602(GBGT1)
LWW102745627(GBGT1)
FCA101090810(GBGT1)
PYU121024025 121026244
PCOO112872266(GBGT1)
PBG122475454(GBGT1)
LRUF124525642
PTG102954717(GBGT1)
PPAD109249974(GBGT1)
PUC125922866
AJU106985321
HHV120230207(GBGT1)
BTA618517(GBGT1)
BOM102282202(GBGT1)
BIU109566575(GBGT1) 109566576
BBUB102405974(GBGT1)
BBIS105000764(GBGT1)
CHX102180325(GBGT1)
OAS101112039(GBGT1)
BTAX128055408(GBGT1)
ODA120852132(GBGT1)
CCAD122442307(GBGT1)
MBEZ129539432(GBGT1)
SSC110256486(GBGT1)
CFR102511010(GBGT1)
CBAI105069725(GBGT1)
CDK105085187(GBGT1)
VPC102544102(GBGT1)
BACU103008412
LVE103086807(GBGT1)
OOR105747968 125960274 125964891
DLE111177084(GBGT1)
PCAD102993265(GBGT1)
PSIU116755506(GBGT1)
NASI112411279(GBGT1)
ECB100069388(GBGT1)
EPZ103553672(GBGT1)
EAI106845361(GBGT1)
MYB102239613(GBGT1)
MYD102767739(GBGT1)
MMYO118666918(GBGT1)
MNA107524628(GBGT1)
PKL118708886(GBGT1)
EFUS103296001(GBGT1)
HAI109381005(GBGT1)
DRO112306338(GBGT1)
SHON118980198(GBGT1)
AJM119036120(GBGT1)
PDIC114503822(GBGT1)
PHAS123823587(GBGT1)
MMF118629656(GBGT1)
RFQ117032435(GBGT1)
PPAM129079185(GBGT1)
PALE102880609(GBGT1)
PGIG120602748(GBGT1)
PVP105298649(GBGT1) 105310501
RAY107504585(GBGT1)
MJV108388221(GBGT1)
TOD119231237(GBGT1)
LAV100665584(GBGT1)
TMU101349194
ETF101653910(GBGT1)
DNM101413632(GBGT1)
MDO100017839(GBGT1)
GAS123235206(GBGT1)
SHR100918940(GBGT1)
AFZ127550940
PCW110205392(GBGT1)
OAA100090987(GBGT1)
GGA417163(GBGT1)
PCOC116234290(GBGT1)
MGP116216187(GBGT1)
CJO107321913(GBGT1)
TPAI128074081(GBGT1)
NMEL110406850
APLA101799653(GBGT1)
ACYG106044126(GBGT1)
CATA118252209(GBGT1)
AFUL116496885(GBGT1)
TGU100225394(GBGT1)
LSR110477722(GBGT1)
SCAN103818975(GBGT1)
PMOA120512426
OTC121337072
PRUF121362457
GFR102040147(GBGT1)
FAB101806513(GBGT1)
PHI102103511(ABO)
PMAJ107212008(GBGT1)
CCAE111937029(GBGT1)
CCW104688481(GBGT1)
CBRC103623253(GBGT1)
ETL114059121
ZAB102073256(GBGT1)
ACHL103812068
SVG106851365
MMEA130576726(GBGT1)
HRT120761744(GBGT1)
FPG101921547(GBGT1)
FCH102050463(GBGT1)
CLV102095912(GBGT1)
EGZ104129328
NNI104023282(GBGT1)
PCRI104024593(GBGT1)
PLET104627305(GLT6D1)
EHS104507797
PCAO104049004(GBGT1)
ACUN113486511(GBGT1)
TALA104363600(GBGT1)
PADL103915270(GBGT1)
AFOR103905391(GBGT1)
ACHC115335226
HALD104311518(GBGT1)
HLE104833878(GBGT1)
AGEN126052297
GCL127023774
CCRI104156086(GBGT1)
CSTI104552838(GBGT1)
CMAC104486571(GBGT1)
MUI104547383(GBGT1)
BREG104634641(GBGT1)
FGA104079573(GBGT1)
GSTE104260891(GBGT1)
LDI104348261(GBGT1)
MNB103774500(GBGT1)
OHA104329589(GBGT1)
SHAB115617122
PGUU104457413(GBGT1)
ACAR114818962(GBGT1)
CPEA104389822(GBGT1)
AVIT104273399(GBGT1)
CVF104292818(GBGT1)
RTD128917441
CUCA104066934(GBGT1)
TEO104370774(GBGT1)
BRHI104492708(GBGT1)
AAM106483758(GBGT1)
AROW112964277
NPD112955910(GBGT1)
TGT104565735(GBGT1)
DNE112979913(GBGT1)
SCAM104138245(GBGT1)
ASN102388459(GBGT1)
AMJ102565956(GBGT1)
CPOO109313975(GBGT1)
GGN109292997(GBGT1)
PSS102455930(GBGT1)
CMY102938627
CCAY125623484(GBGT1)
DCC119844129(GBGT1)
CPIC101945380(GBGT1)
TST117889501
CABI116824002(GBGT1)
MRV120386791(GBGT1)
PVT110079644(GBGT1)
SUND121936036(GBGT1)
VKO123028392(GBGT1)
PMUA114589368(GBGT1)
PRAF128406620(GBGT1)
ZVI118083772(GBGT1)
HCG128339083(GBGT1)
GJA107124818(GBGT1)
EMC129341920(GBGT1)
DRE100005375(si:ch211-135f11.4) 100005565(gbgt1l8) 100005704(si:dkey-110k5.10) 387303(gbgt1l4) 447881(gbgt1l3) 563897(gbgt1l5) 566487(gbgt1l2)
SRX107726394 107732598 107732624 107747816 107747818 107747827
SANH107680407 107680408 107687663 107687696 107687702 107703160
SGH107554410 107592280 107592391 107597221 107597222 107599955 107599982
CCAR109066903 109073532 109084337 109084598 109090452 109096308 109099031 109099041
CAUA113048788 113048790 113070773 113091380 113091387 113093767 113093769 113093774 113093789 113093790 113093791 113106834 113107731
CGIB127957515 127957517 127957518 127964073 127964074 127988020 127988021 128011636 128011673 128018117 128018118 128018438
PTET122323501 122331250 122342346 122345519 122346179 122349911 122350290 122351022
LROH127157414 127161207 127161410 127166080 127166082 127169906 127170324 127170325
OMC131521882 131529717 131540759 131541257 131541414
PPRM120469831 120469855(gbgt1l1) 120469856 120492581 120492582 120492752
RKG130071210 130071223 130100362 130100371
MAMB125266605 125266608 125270868 125270877 125270898 125279747
CIDE127513534 127518848
MASI127417399 127420042 127427273 127432028
TROS130550131 130550258
TDW130414144 130418798 130439580
MANU129431154 129431207 129431215 129431223 129439437 129439438 129439439 129439978
IPU108260034 108261884 108262004 108262359 108279304 128628706 128628757 128629371 128629372
IFU128603269 128603373 128603461 128603462 128603601 128603602 128603788 128603940 128603941 128603942 128622788
PHYP113528687 113531017 113531111 113531290 113535471
SMEO124379102 124379514 124379517 124379518 124379519 124379520 124379521
TFD113642193 113643872 113645540 113645553 113646411 113662876 113662877 113662878 113662880 113662881 125138391 125138413
TVC132840826 132840948 132841095 132841368 132843550 132859580
AMEX103028363
CMAO118820652
EEE113567823 113567860 113569052 113569053 113569272 113583525 113591966(abo)
CHAR105902476
TRU101067861
TFS130524207
TNGGSTEN00020153G001
LCO104928926 104931896 104939769
NCC104957060 104960712
TBEN117469143 117475447
CGOB115004920 115008381
PGEO117439248 117446971
GACU117551431 117561882
ELY117252456 117256701 117268756
EFO125879223 125887409
PLEP121955086 121956892
SLUC116034799 116035209 116060445
ECRA117941309 117944096 117945063
ESP116688117 116692760
PFLV114552989 114553901 114570339
GAT120813179 120828061 120835006 120835856
PPUG119220178 119229407
AFB129098632 129101384 129106184
CLUM117731045 117735166
MSAM119886768 119895977
SCHU122864150 122868912
CUD121507191 121529122
ALAT119013560 119013945 119017792 119017794 119017795 119018539 119021038
MZE101467158 101480789
ONL100704949 100710225
OAU116319404 116326512
OLA101155669 101174260
OML112145421 112160595
XMA102220530(gbgt1) 102220535 102232496
XCO114135177 114142919 114160500(gbgt1)
XHE116710598 116718900 116736301(gbgt1)
PRET103462851 103464991 103469020(gbgt1)
PFOR103136522 103139590 103146879
PLAI106949161 106951144
PMEI106922789 106924471 106927187
GAF122821863 122834415 122842601
PPRL129352540 129364167
CVG107082024 107087987
CTUL119778562 119781763 119789605
GMU124856283 124862367 124863849 124866914
NFU107381862 107381863 107385470 107390254
KMR108228886 108239823 108251530
ALIM106511352 106523577 106528111
NWH119412206 119421205
AOCE111576205 111576206 111576208 111581210 111583435
MCEP124998197 124998341 125006869
CSEM103386423
POV109629071 109643274
SSEN122768523 122774639 122774640 122785122
HHIP117762003 117766136
HSP118104403 118124064
LCF108873243 108876865 108899640
SDU111220711 111225192 111225276 111239801(gbgt1)
SLAL111645940 111649580(gbgt1) 111659413 111659436 111670902
XGL120784939 120789858 120807357
HCQ109522118
SSCV125977842
SBIA133495215 133495486 133507454
PEE133409233 133409328
PTAO133484093 133487744
BPEC110164356 110166708
MALB109956078 109972655
BSPL114852344 114852345 114860876
SJO128356282 128357557 128378368
SASA100194757(gbgt1) 106563649 106565313 106591072 106592470 106592471 106592658 106593699 106594443 106603993 106607464 106609536
STRU115153855 115170972 115170975 115183185 115183188 115183191 115183198 115183200 115183201 115183714 115183718 115183724 115196558 115199057 115204591 115204592 115204593 115208260
OTW112225900 112230697 112233764 112238627 112241057 112258518 112264537
OMY110486140 110491256 110493996 110499918 110507938 110507939 110510239 110538060 110538061 118938868 118938904 118943004
OGO123995966 124000716 124004275 124014534 124015040 124015201
ONE115104034 115110144 115122935 115133691 115143597 115146862
OKI109873917 109887472 109893226 109897573 109899138
OKE118370396 118380367 118384403 118384900 118389556 118392532 127924859
SALP111962053 111980919 111981608 112069843
SNH120021890 120034500 120034688 120043974 120044497 120044499 120049126 120049185 120049430 120050483 120056744
CCLU121541271 121542007 121543467 121550650 121551456 121551555 121569699 121575997 121579098
ELS105008995 105009532 105009827 105009969 105016779 105027180 105028509 105031151 105031152 106024698 114828867 114828941
SFM108927512 108931896
PKI111839748 111846635 111846689 111846766
AANG118213113 118220398 118220551
LOC102685500 102693332 102696413(gbgt1) 102698054
PSPA121306702 121306711 121313236 121328687
ARUT117396906 117403512 117403809 117422695 117964649
PSEX120532902 120535046
LCM102355873 102356395
CMK103183073(gbgt1l5)
PMRN116950634
 » show all
Reference
1  [PMID:4823436]
  Authors
Kijimoto S, Ishibashi T, Makita A.
  Title
Biosynthesis of Forssman hapten from globoside by alpha-N-acetylgalactosaminyltransferase of guinea pig tissues.
  Journal
Biochem Biophys Res Commun 56:177-84 (1974)
DOI:10.1016/S0006-291X(74)80331-1
Other DBs
ExplorEnz - The Enzyme Database: 2.4.1.88
IUBMB Enzyme Nomenclature: 2.4.1.88
ExPASy - ENZYME nomenclature database: 2.4.1.88
BRENDA, the Enzyme Database: 2.4.1.88
CAS: 52037-97-5

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