Entry |
|
Name |
iduronate-2-sulfatase;
chondroitinsulfatase;
idurono-2-sulfatase;
iduronide-2-sulfate sulfatase;
L-iduronosulfatase;
L-idurono sulfate sulfatase;
iduronate sulfatase;
sulfo-L-iduronate sulfatase;
L-iduronate 2-sulfate sulfatase;
sulfoiduronate sulfohydrolase;
2-sulfo-L-iduronate 2-sulfatase;
iduronate-2-sulfate sulfatase;
iduronate sulfate sulfatase
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Class |
Hydrolases;
Acting on ester bonds;
Sulfuric-ester hydrolases
|
Sysname |
L-iduronate-2-sulfate 2-sulfohydrolase
|
Reaction(IUBMB) |
Hydrolysis of the 2-sulfate groups of the L-iduronate 2-sulfate units of dermatan sulfate, heparan sulfate and heparin [RN: R07812 R07821]
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Reaction(KEGG) |
|
History |
EC 3.1.6.13 created 1984
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Pathway |
ec00531 | Glycosaminoglycan degradation |
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Orthology |
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Genes |
MORG: | 121440220(Ids) 121440435 |
EJU: | 114199013(IDS) 114202770 |
RAY: | 107502397 107502399(IDS) 107506382 107507519 107507961 |
SSEN: | 122761367 122778945(ids) |
SALP: | 111965339 112070437(ids) |
CCLU: | 121545498 123492866(ids) |
SPU: | 100892602 100892667 115918435 115922305 579992 584730 587680 588607 588631 |
LPIC: | 129261086 129261216 129262001 |
APLC: | 110983712 110983804 |
DSI: | Dsimw501_GD13763(Dsim_GD13763) |
TDA: | 119673156 119673434 119673475 |
NLU: | 111046525 111061142 120355108 120355801 120356024 |
TCF: | 131884735 131885872 131886338 131886774 |
PTEP: | 107436780 107441331 |
LGI: | LOTGIDRAFT_104488 LOTGIDRAFT_123341 LOTGIDRAFT_153520 LOTGIDRAFT_165917 LOTGIDRAFT_182753 |
PVUL: | 126814320 126814405 126815082 126830115 130014136 |
PCAN: | 112559502 112559503 112559504 112559583 112559713 |
GAE: | 121374686 121377054 121378631 121378632 121378634 121378635 |
HRF: | 124112807 124112980 124113001 124118457 124118983 124118984 124122656 124122661 124132900 124149615 124152520 124152521 124152523 124152524 124152526 124152528 124152530 124152531 124152532 124152533 124152534 124152535 124152538 |
HRJ: | 124253119 124262409 124265030 124269853 124269854 124269855 124270479 124270480 124270816 124272583 124274728 124286941 124286945 124287446 124287447 124287449 124287451 124287452 124287453 124287454 124287455 124287457 124287483 124287488 124287489 124290992 124292414 124292415 124292417 124292418 |
MMER: | 123541840 123542263 123545463 123546109 123556889 123562141 123562143 128549368 |
RPHI: | 132721451 132738419 132738430 132738714 132744324 132755302 132755420 132757676 |
DPOL: | 127835673 127842995 127845876 127859789 127859800 127860871 127860873 127860910 127875992 127877713 127878101 127879459 |
PDAM: | 113686490 113686493 |
AQU: | 100632261 100634409 100635941 100636070 100637425 100637941 100638175 100638304 105312205 109584014 109584015 109587233 |
MBR: | MONBRDRAFT_22994 MONBRDRAFT_25248 MONBRDRAFT_27026 MONBRDRAFT_27633 MONBRDRAFT_28811 MONBRDRAFT_30487 MONBRDRAFT_32660 |
SRE: | PTSG_08138 PTSG_08989 |
AAF: | AURANDRAFT_24889(ITS3) AURANDRAFT_63017(ITS1) AURANDRAFT_67199(ITS2) |
EHX: | EMIHUDRAFT_103111 EMIHUDRAFT_103855 EMIHUDRAFT_112105 EMIHUDRAFT_122517 EMIHUDRAFT_194249 EMIHUDRAFT_209682 EMIHUDRAFT_212280 EMIHUDRAFT_217387 EMIHUDRAFT_219397 EMIHUDRAFT_224019 EMIHUDRAFT_226946 EMIHUDRAFT_236119 EMIHUDRAFT_241437 EMIHUDRAFT_251085 EMIHUDRAFT_254050 EMIHUDRAFT_449285 EMIHUDRAFT_462481 EMIHUDRAFT_98819 |
CPS: | CPS_2358 CPS_2375 CPS_2381 |
CATE: | C2869_03515 C2869_06890 C2869_07510 C2869_07615 |
ADO: | A6F68_00793(betC_2) A6F68_01095(betC_7) |
ROO: | G5S37_04965 G5S37_05100 G5S37_06235 G5S37_09990 G5S37_28180 |
LUO: | HHL09_01145 HHL09_01155 HHL09_08160 |
VBA: | IMCC26134_05065 IMCC26134_14340 IMCC26134_14360 |
VBS: | EGM51_05040 EGM51_06095 EGM51_06440 |
RBA: | RB10612 RB110 RB11127(ids) RB12089 RB2085(betC) RB2254 RB2707 RB5424 RB763 |
PSL: | Psta_0190 Psta_1325 Psta_4390 |
PIR: | VN12_09385 VN12_21255(betC_6) VN12_22170(betC_7) |
RUL: | UC8_11930 UC8_17290(betC_4) UC8_25850 UC8_36630(betC_8) UC8_53680(betC_12) |
MFF: | MFFC18_08440(betC_1) MFFC18_24440(betC_5) MFFC18_27880(betC_6) MFFC18_28310 MFFC18_48110 |
ROL: | CA51_00570(betC_1) CA51_05180 CA51_09680 CA51_13020(betC_3) CA51_15580(betC_4) CA51_27610 CA51_27790(betC_7) |
AHEL: | Q31a_06790(betC_2) Q31a_18220 Q31a_38050 Q31a_39670 Q31a_40250(betC_12) Q31a_49120 Q31a_52450 Q31a_62100(betC_14) |
LCRE: | Pla8534_31970(betC_9) Pla8534_37420 Pla8534_62290(betC_14) |
AAGG: | ETAA8_12620 ETAA8_19150(betC_4) ETAA8_29880 ETAA8_34290(betC_7) ETAA8_40770 |
BVO: | Pan97_01350(betC_1) Pan97_04460(betC_3) Pan97_04520 Pan97_05370 Pan97_10250(betC_7) Pan97_11360 Pan97_28910 |
RLC: | K227x_60000(betC_18) |
TTF: | THTE_1564 THTE_3218 THTE_3574 |
AMUC: | Pan181_24280(betC_2) Pan181_35480 |
PND: | Pla175_08790(betC_3) Pla175_16280(betC_7) Pla175_17960 Pla175_22610(betC_9) Pla175_23090 Pla175_29660(betC_16) Pla175_30230(betC_17) Pla175_30620(betC_18) Pla175_34340(betC_19) Pla175_43580(betC_21) Pla175_44060 |
PLM: | Plim_0651 Plim_3206 Plim_3468 |
PEH: | Spb1_00530(betC_1) Spb1_14370(betC_2) Spb1_39310(betC_6) |
PBS: | Plabr_1704 Plabr_1705 Plabr_2092 Plabr_3173 Plabr_3214 Plabr_3306 Plabr_3888 Plabr_3983 |
PLS: | VT03_16380(betC_4) VT03_26185(betC_5) |
FMR: | Fuma_00103 Fuma_00319 Fuma_00869(betC_3) Fuma_03662(betC_8) Fuma_05561 Fuma_05572 |
GMR: | GmarT_16040(betC_3) GmarT_33550(betC_6) GmarT_39170(betC_9) GmarT_51320(betC_11) GmarT_52750(betC_12) GmarT_56780(betC_15) GmarT_56970(betC_16) |
GIM: | F1728_16070 F1728_16135 F1728_17540 F1728_18375 F1728_20155 F1728_26680 F1728_28935 F1728_29645 |
GPN: | Pan110_26060 Pan110_31690(betC_5) Pan110_33350(betC_6) Pan110_37530 Pan110_50420(betC_9) Pan110_52270(betC_11) Pan110_54560(betC_12) Pan110_57880(betC_13) Pan110_58100(betC_14) |
MRI: | Mal4_02780(betC_2) Mal4_02830 Mal4_11450(betC_3) Mal4_23560 Mal4_25490(betC_10) Mal4_25920 Mal4_38510 Mal4_38980(betC_16) Mal4_43080(betC_18) Mal4_52730 |
SDYN: | Mal52_09100(betC_4) Mal52_09280 Mal52_20470(betC_5) Mal52_23390 |
PLON: | Pla110_26770(betC_3) Pla110_45380(betC_7) |
LRS: | PX52LOC_01054 PX52LOC_03291 |
ULI: | ETAA1_29150 ETAA1_30410(betC_3) ETAA1_30420 ETAA1_48310(betC_4) |
SACI: | Sinac_2390 Sinac_5994 |
PBAS: | SMSP2_00670 SMSP2_00786 |
ALUS: | STSP2_00836(betC_2) |
HBS: | IPV69_00480 IPV69_05370 IPV69_05465 IPV69_06155 IPV69_07740 IPV69_17595 |
VBL: | L21SP4_00397(betC_1) L21SP4_01487 L21SP4_01919(betC_8) |
ABAC: | LuPra_00139(betC_1) |
MCOS: | GM418_07545 GM418_10580 GM418_11520 GM418_11530 GM418_15485 GM418_18720 GM418_22600 GM418_24840 GM418_25460 |
MBAS: | ALGA_0045 ALGA_2234 |
CHIT: | FW415_14010 FW415_21965 |
PGIN: | FRZ67_01245 FRZ67_01250 |
SHG: | Sph21_4218 Sph21_5173 |
SDJ: | NCTC13534_02722(betC_2) |
AGD: | FRZ59_08605 FRZ59_09485 |
OLI: | FKG96_18495 FKG96_21210 FKG96_23435 |
CMR: | Cycma_0852 Cycma_3754 Cycma_3797 Cycma_3901 |
CAMU: | CA2015_0736 CA2015_3688 CA2015_3725 |
EVI: | Echvi_0936 Echvi_3776 |
EST: | DN752_02210 DN752_10940 DN752_23000 DN752_23410 |
ECHI: | FKX85_04685 FKX85_17770 |
ALS: | DJ013_02320 DJ013_04270 DJ013_06750 |
FLM: | MY04_5044 MY04_5052 MY04_5157 MY04_5164 |
FLL: | EI427_16845 EI427_21685 EI427_21720 |
FYA: | KMW28_27690 KMW28_27725 KMW28_28200 |
FKA: | KM029_23090 KM029_26055 |
FFA: | FFWV33_10655 FFWV33_14845 FFWV33_15050 FFWV33_17845 |
FNK: | E1750_01020 E1750_01035 E1750_17170 E1750_17200 |
FBC: | FB2170_01941 FB2170_06815 |
MARE: | EJ994_10160 EJ994_10220 EJ994_10435 |
CAO: | Celal_0430 Celal_0431 |
CLY: | Celly_1791 Celly_1796 |
CLH: | IX49_08840 IX49_08865 |
CBAL: | M667_18145 M667_19620 |
CBAT: | M666_18145 M666_19535 |
COMN: | PBN93_08865 PBN93_08890 |
ZGA: | ZOBELLIA_181(idsA1) ZOBELLIA_2730(idsA2) ZOBELLIA_3146(idsA3) ZOBELLIA_3526(idsA4) |
POLA: | BXQ17_09695 BXQ17_09710 BXQ17_09750 BXQ17_09845 |
PHAL: | H9I45_05880 H9I45_05905 H9I45_05950 H9I45_05955 |
SZE: | AW14_08895 AW14_08920 AW14_08960 AW14_13205 AW14_13220 AW14_13235 AW14_13405 AW14_13435 |
AHZ: | APS56_04555 APS56_05910 APS56_09900 |
WFU: | AXE80_00055 AXE80_06065 AXE80_06125 AXE80_06140 AXE80_07595 AXE80_10200 AXE80_10210 AXE80_10620 AXE80_12690 AXE80_12995 |
FOH: | FORMA_02030 FORMA_02150 FORMA_02410 FORMA_02490 FORMA_02510 FORMA_07140 FORMA_07310 |
FOP: | FNB79_04820 FNB79_14610 |
SEON: | BWZ22_10495 BWZ22_10535 BWZ22_10550 BWZ22_11745 |
AALG: | AREALGSMS7_01173 AREALGSMS7_01304 |
TAJ: | C1A40_08420 C1A40_08455 C1A40_13045 C1A40_13085 C1A40_13100 |
KAN: | IMCC3317_46410 IMCC3317_46440 |
GAA: | HX109_03365 HX109_13995 |
FBE: | FF125_02310 FF125_03865 FF125_12590 FF125_15540 |
FBU: | UJ101_00816 UJ101_00822(GNS) |
» show all
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Reference |
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Authors |
Archer IM, Harper PS, Wusteman FS. |
Title |
Multiple forms of iduronate 2-sulphate sulphatase in human tissues and body fluids. |
Journal |
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Reference |
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Authors |
Bach G, Eisenberg F Jr, Cantz M, Neufeld EF. |
Title |
The defect in the Hunter syndrome: deficiency of sulfoiduronate sulfatase. |
Journal |
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Reference |
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Authors |
Di Natale P, Ronsisvalle L. |
Title |
Identification and partial characterization of two enzyme forms of iduronate sulfatase from human placenta. |
Journal |
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Reference |
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Authors |
Yutaka T, Fluharty AL, Stevens RL, Kihara H. |
Title |
Purification and some properties of human liver iduronate sulfatase. |
Journal |
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Other DBs |
ExplorEnz - The Enzyme Database: | 3.1.6.13 |
ExPASy - ENZYME nomenclature database: | 3.1.6.13 |
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