Entry |
|
Name |
ADAMTS13 endopeptidase;
ADAMTS VWF cleaving metalloprotease;
ADAMTS-13;
ADAMTS13;
vWF-cleaving protease;
VWF-CP;
vWF-degrading protease;
Upshaw factor;
von Willebrand factor cleaving protease;
ADAMTS13 peptidase
|
Class |
Hydrolases;
Acting on peptide bonds (peptidases);
Metalloendopeptidases
|
Reaction(IUBMB) |
The enzyme cleaves the von Willebrand factor at bond Tyr842!Met843 within the A2 domain
|
Comment |
In peptidase family M12.
|
History |
EC 3.4.24.87 created 2009
|
Orthology |
K08627 | a disintegrin and metalloproteinase with thrombospondin motifs 13 |
|
Genes |
CSAB: | 103239684(ADAMTS13) |
CATY: | 105580513(ADAMTS13) |
PANU: | 101018650(ADAMTS13) |
MLEU: | 105528703(ADAMTS13) |
PTEH: | 111523982(ADAMTS13) |
CANG: | 105503983(ADAMTS13) |
CIMI: | 108292312(ADAMTS13) |
CSYR: | 103273391(ADAMTS13) |
MMUR: | 105880760(ADAMTS13) |
LCAT: | 123646680(ADAMTS13) |
PCOQ: | 105826699(ADAMTS13) |
MCAL: | 110312498(Adamts13) |
MPAH: | 110317485(Adamts13) |
MCOC: | 116091905(Adamts13) |
ANU: | 117701923 117703988(Adamts13) |
MAUA: | 101827371(Adamts13) |
PROB: | 127222654(Adamts13) |
PLEU: | 114684226(Adamts13) |
MORG: | 121462687(Adamts13) |
AAMP: | 119818562(Adamts13) |
CPOC: | 100727045(Adamts13) |
CCAN: | 109696127(Adamts13) |
DORD: | 105995613(Adamts13) |
PLOP: | 125353276(Adamts13) |
MMMA: | 107159168(Adamts13) |
CLUD: | 112677392(ADAMTS13) |
MPUF: | 101694125(ADAMTS13) |
PCOO: | 112860307(ADAMTS13) |
PVIV: | 125150198(ADAMTS13) |
PPAD: | 109258253(ADAMTS13) |
BBUB: | 102412616(ADAMTS13) |
BBIS: | 104987950(ADAMTS13) |
BTAX: | 128056485(ADAMTS13) |
CCAD: | 122442334(ADAMTS13) |
MBEZ: | 129539798(ADAMTS13) |
CBAI: | 105068608(ADAMTS13) |
BACU: | 102999611(ADAMTS13) |
BMUS: | 118897540(ADAMTS13) |
PCAD: | 102996576(ADAMTS13) |
PSIU: | 116755106(ADAMTS13) |
NASI: | 112411327(ADAMTS13) |
MMYO: | 118666904(ADAMTS13) |
EFUS: | 103296148(ADAMTS13) |
SHON: | 118980285(ADAMTS13) |
PDIC: | 114511173(ADAMTS13) |
PHAS: | 123823380(ADAMTS13) |
PPAM: | 129079464(ADAMTS13) |
PALE: | 102885523(ADAMTS13) |
PGIG: | 120599714(ADAMTS13) |
SARA: | 101548412(ADAMTS13) |
SETR: | 126009354(ADAMTS13) |
PCOC: | 116234434(ADAMTS13) |
TPAI: | 128073573(ADAMTS13) |
LMUT: | 125702505(ADAMTS13) |
NMEL: | 110406845(ADAMTS13) |
APLA: | 101800615(ADAMTS13) |
ACYG: | 106044108(ADAMTS13) |
CATA: | 118252273(ADAMTS13) |
AFUL: | 116496934(ADAMTS13) |
SCAN: | 103819131(ADAMTS13) |
PMOA: | 120512419(ADAMTS13) |
PRUF: | 121362425(ADAMTS13) |
PMAJ: | 107212053(ADAMTS13) |
CCAE: | 111937039(ADAMTS13) |
CBRC: | 103623248(ADAMTS13) |
ACHL: | 103809287(ADAMTS13) |
MMEA: | 130576694(ADAMTS13) |
PCRI: | 104028886(ADAMTS13) |
PLET: | 104624643(ADAMTS13) |
PCAO: | 104047343(ADAMTS13) |
ACUN: | 113486351(ADAMTS13) |
TALA: | 104363650(ADAMTS13) |
PADL: | 103915348(ADAMTS13) |
AFOR: | 103905329(ADAMTS13) |
ACHC: | 115335017(ADAMTS13) |
HALD: | 104323021(ADAMTS13) |
CCRI: | 104163978(ADAMTS13) |
CSTI: | 104561782(ADAMTS13) |
CMAC: | 104483793(ADAMTS13) |
BREG: | 104632222(ADAMTS13) |
GSTE: | 104261947(ADAMTS13) |
SHAB: | 115617127(ADAMTS13) |
DPUB: | 104296479(ADAMTS13) |
PGUU: | 104469452(ADAMTS13) |
ACAR: | 104527328(ADAMTS13) |
CPEA: | 104389819(ADAMTS13) |
AVIT: | 104278033(ADAMTS13) |
CUCA: | 104066938(ADAMTS13) |
BRHI: | 104489548(ADAMTS13) |
AROW: | 112964357(ADAMTS13) |
SCAM: | 104138242(ADAMTS13) |
CPOO: | 109313985(ADAMTS13) |
CCAY: | 125623621(ADAMTS13) |
CABI: | 116817469(ADAMTS13) |
PMUR: | 107300476 107302802(ADAMTS13) |
CTIG: | 120298847(ADAMTS13) |
APRI: | 131186207(ADAMTS13) |
PTEX: | 113443776(ADAMTS13) |
PMUA: | 114589118(ADAMTS13) |
PRAF: | 128406410(ADAMTS13) |
RTEM: | 120913870(ADAMTS13) |
BBUF: | 120977996(ADAMTS13) |
BGAR: | 122946443(ADAMTS13) |
SRX: | 107725310 107740991(adamts13) |
SANH: | 107691575(adamts13) 107702807 |
SGH: | 107548275 107565123(adamts13) |
CAUA: | 113070702(adamts13) |
PTET: | 122350338(adamts13) |
LROH: | 127169433(adamts13) |
PPRM: | 120473833(adamts13) |
MAMB: | 125279476(adamts13) |
TROS: | 130568092(adamts13) |
MANU: | 129415088(adamts13) |
PHYP: | 113533593(adamts13) |
SMEO: | 124399846(adamts13) |
AMEX: | 103029987(adamts13) |
CMAO: | 118813326(adamts13) |
CHAR: | 105894886(adamts13) |
TBEN: | 117472614(adamts13) |
CGOB: | 115013592(adamts13) |
PGEO: | 117452414(adamts13) |
GACU: | 117543933(adamts13) |
EMAC: | 134873591(adamts13) |
PLEP: | 121944087(adamts13) |
SLUC: | 116050540(adamts13) |
ECRA: | 117944827(adamts13) |
PFLV: | 114555418(adamts13) |
PPUG: | 119225063(adamts13) |
CLUM: | 117735888(adamts13) |
PSWI: | 130196825(adamts13) |
MSAM: | 119891655(adamts13) |
SCHU: | 122876145(adamts13) |
ALAT: | 119019795(adamts13) |
CSAI: | 133451247(adamts13) |
PRET: | 103470625(adamts13) |
PFOR: | 103147041(adamts13) |
PLAI: | 106939142(adamts13) |
PMEI: | 106917656(adamts13) |
PPRL: | 129372958(adamts13) |
CTUL: | 119785140(adamts13) |
ALIM: | 106516687(adamts13) |
AOCE: | 111586394(adamts13) |
MCEP: | 125012297(adamts13) |
SSEN: | 122769584(adamts13) |
HHIP: | 117767414(adamts13) |
SMAU: | 118313805(adamts13) |
SLAL: | 111644942(adamts13) |
SBIA: | 133499364(adamts13) |
PTAO: | 133475627(adamts13) |
BPEC: | 110169902(adamts13) |
MALB: | 109954821(adamts13) |
BSPL: | 114861250(adamts13) |
SASA: | 106579902(adamts13) |
STRU: | 115200048(adamts13) |
SALP: | 111957513(adamts13) |
CCLU: | 121551928(adamts13) |
AANG: | 118206510(adamts13) |
PSPA: | 121309677(adamts13) |
ARUT: | 117396819 117422042 |
PSEX: | 120536068(adamts13) |
CPLA: | 122564630(adamts13) |
LERI: | 129712093(adamts13) |
» show all
|
Reference |
|
Authors |
Fujikawa K, Suzuki H, McMullen B, Chung D |
Title |
Purification of human von Willebrand factor-cleaving protease and its identification as a new member of the metalloproteinase family. |
Journal |
|
Sequence |
|
Reference |
|
Authors |
Dong JF, Moake JL, Nolasco L, Bernardo A, Arceneaux W, Shrimpton CN, Schade AJ, McIntire LV, Fujikawa K, Lopez JA |
Title |
ADAMTS-13 rapidly cleaves newly secreted ultralarge von Willebrand factor multimers on the endothelial surface under flowing conditions. |
Journal |
|
Other DBs |
ExPASy - ENZYME nomenclature database: | 3.4.24.87 |
|