KEGG   Homo sapiens (human): 722
Entry
722               CDS       T01001                                 
Symbol
C4BPA, C4BP, PRP
Name
(RefSeq) complement component 4 binding protein alpha
  KO
K04002  complement component 4 binding protein alpha
Organism
hsa  Homo sapiens (human)
Pathway
hsa04610  Complement and coagulation cascades
hsa05133  Pertussis
Network
nt06513  Complement cascade
  Element
N01495  Classical/Lectin pathway of complement cascade, C4b breakdown
Disease
H00106  Complement regulatory protein defects
Brite
KEGG Orthology (KO) [BR:hsa00001]
 09150 Organismal Systems
  09151 Immune system
   04610 Complement and coagulation cascades
    722 (C4BPA)
 09160 Human Diseases
  09171 Infectious disease: bacterial
   05133 Pertussis
    722 (C4BPA)
SSDB
Motif
Pfam: Sushi C4bp_oligo C6
Other DBs
NCBI-GeneID: 722
NCBI-ProteinID: NP_000706
OMIM: 120830
HGNC: 1325
Ensembl: ENSG00000123838
UniProt: P04003
Structure
Position
1:207104233..207144972
AA seq 597 aa
MHPPKTPSGALHRKRKMAAWPFSRLWKVSDPILFQMTLIAALLPAVLGNCGPPPTLSFAA
PMDITLTETRFKTGTTLKYTCLPGYVRSHSTQTLTCNSDGEWVYNTFCIYKRCRHPGELR
NGQVEIKTDLSFGSQIEFSCSEGFFLIGSTTSRCEVQDRGVGWSHPLPQCEIVKCKPPPD
IRNGRHSGEENFYAYGFSVTYSCDPRFSLLGHASISCTVENETIGVWRPSPPTCEKITCR
KPDVSHGEMVSGFGPIYNYKDTIVFKCQKGFVLRGSSVIHCDADSKWNPSPPACEPNSCI
NLPDIPHASWETYPRPTKEDVYVVGTVLRYRCHPGYKPTTDEPTTVICQKNLRWTPYQGC
EALCCPEPKLNNGEITQHRKSRPANHCVYFYGDEISFSCHETSRFSAICQGDGTWSPRTP
SCGDICNFPPKIAHGHYKQSSSYSFFKEEIIYECDKGYILVGQAKLSCSYSHWSAPAPQC
KALCRKPELVNGRLSVDKDQYVEPENVTIQCDSGYGVVGPQSITCSGNRTWYPEVPKCEW
ETPEGCEQVLTGKRLMQCLPNPEDVKMALEVYKLSLEIEQLELQRDSARQSTLDKEL
NT seq 1794 nt   +upstreamnt  +downstreamnt
atgcaccccccaaaaactccatctggggctcttcatagaaaaaggaaaatggcagcctgg
cccttctccaggctgtggaaagtctctgatccaattctcttccaaatgaccttgatcgct
gctctgttgcctgctgttcttggcaattgtggtcctccacccactttatcatttgctgcc
ccgatggatattacgttgactgagacacgcttcaaaactggaactactctgaaatacacc
tgcctccctggctacgtcagatcccattcaactcagacgcttacctgtaattctgatggc
gaatgggtgtataacaccttctgtatctacaaacgatgcagacacccaggagagttacgt
aatgggcaagtagagattaagacagatttatcttttggatcacaaatagaattcagctgt
tcagaaggatttttcttaattggctcaaccactagtcgttgtgaagtccaagatagagga
gttggctggagtcatcctctcccacaatgtgaaattgtcaagtgtaagcctcctccagac
atcaggaatggaaggcacagcggtgaagaaaatttctacgcatacggcttttctgtcacc
tacagctgtgacccccgcttctcactcttgggccatgcctccatttcttgcactgtggag
aatgaaacaataggtgtttggagaccaagccctcctacctgtgaaaaaatcacctgtcgc
aagccagatgtttcacatggggaaatggtctctggatttggacccatctataattacaaa
gacactattgtgtttaagtgccaaaaaggttttgttctcagaggcagcagtgtaattcat
tgtgatgctgatagcaaatggaatccttctcctcctgcttgtgagcccaatagttgtatt
aatttaccagacattccacatgcttcctgggaaacatatcctaggccgacaaaagaggat
gtgtatgttgttgggactgtgttaaggtaccgctgtcatcctggctacaaacccactaca
gatgagcctacgactgtgatttgtcagaaaaatttgagatggaccccataccaaggatgt
gaggcgttatgttgccctgaaccaaagctaaataatggtgaaatcactcaacacaggaaa
agtcgtcctgccaatcactgtgtttatttctatggagatgagatttcattttcatgtcat
gagaccagtaggttttcagctatatgccaaggagatggcacgtggagtccccgaacacca
tcatgtggagacatttgcaattttcctcctaaaattgcccatgggcattataaacaatct
agttcatacagctttttcaaagaagagattatatatgaatgtgataaaggctacattctg
gtcggacaggcgaaactctcctgcagttattcacactggtcagctccagcccctcaatgt
aaagctctgtgtcggaaaccagaattagtgaatggaaggttgtctgtggataaggatcag
tatgttgagcctgaaaatgtcaccatccaatgtgattctggctatggtgtggttggtccc
caaagtatcacttgctctgggaacagaacctggtacccagaggtgcccaagtgtgagtgg
gagacccccgaaggctgtgaacaagtgctcacaggcaaaagactcatgcagtgtctccca
aacccagaggatgtgaaaatggccctggaggtatataagctgtctctggaaattgaacaa
ctggaactacagagagacagcgcaagacaatccactttggataaagaactataa

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