KEGG   Homo sapiens (human): 8802
Entry
8802              CDS       T01001                                 
Symbol
SUCLG1, GALPHA, MTDPS9, SUCLA1
Name
(RefSeq) succinate-CoA ligase GDP/ADP-forming subunit alpha
  KO
K01899  succinyl-CoA synthetase alpha subunit [EC:6.2.1.4 6.2.1.5]
Organism
hsa  Homo sapiens (human)
Pathway
hsa00020  Citrate cycle (TCA cycle)
hsa00640  Propanoate metabolism
hsa01100  Metabolic pathways
hsa01200  Carbon metabolism
Module
hsa_M00009  Citrate cycle (TCA cycle, Krebs cycle)
hsa_M00011  Citrate cycle, second carbon oxidation, 2-oxoglutarate => oxaloacetate
Network
nt06031  Citrate cycle and pyruvate metabolism
  Element
N01617  Citrate cycle, second carbon oxidation 2
Disease
H00469  Mitochondrial DNA depletion syndrome
Brite
KEGG Orthology (KO) [BR:hsa00001]
 09100 Metabolism
  09101 Carbohydrate metabolism
   00020 Citrate cycle (TCA cycle)
    8802 (SUCLG1)
   00640 Propanoate metabolism
    8802 (SUCLG1)
Enzymes [BR:hsa01000]
 6. Ligases
  6.2  Forming carbon-sulfur bonds
   6.2.1  Acid-thiol ligases
    6.2.1.4  succinate---CoA ligase (GDP-forming)
     8802 (SUCLG1)
    6.2.1.5  succinate---CoA ligase (ADP-forming)
     8802 (SUCLG1)
SSDB
Motif
Pfam: CoA_binding Ligase_CoA Succ_CoA_lig CoA_binding_2
Other DBs
NCBI-GeneID: 8802
NCBI-ProteinID: NP_003840
OMIM: 611224
HGNC: 11449
Ensembl: ENSG00000163541
UniProt: P53597
Structure
Position
2:complement(84423528..84459280)
AA seq 346 aa
MTATLAAAADIATMVSGSSGLAAARLLSRSFLLPQNGIRHCSYTASRQHLYVDKNTKIIC
QGFTGKQGTFHSQQALEYGTKLVGGTTPGKGGQTHLGLPVFNTVKEAKEQTGATASVIYV
PPPFAAAAINEAIEAEIPLVVCITEGIPQQDMVRVKHKLLRQEKTRLIGPNCPGVINPGE
CKIGIMPGHIHKKGRIGIVSRSGTLTYEAVHQTTQVGLGQSLCVGIGGDPFNGTDFIDCL
EIFLNDSATEGIILIGEIGGNAEENAAEFLKQHNSGPNSKPVVSFIAGLTAPPGRRMGHA
GAIIAGGKGGAKEKISALQSAGVVVSMSPAQLGTTIYKEFEKRKML
NT seq 1041 nt   +upstreamnt  +downstreamnt
atgaccgcaacccttgccgctgccgctgacatcgctaccatggtctccggcagcagcggc
ctcgccgccgcccgtctcctgtcgcgcagcttcctcctgccgcagaatggaattcggcat
tgttcctacacagcttctcggcaacatctctatgttgataaaaatacaaagattatttgc
cagggtttcactggcaaacagggcacctttcacagccagcaggcattggaatatggcacc
aaactcgttggaggaaccactccagggaaaggaggccagacacatctgggcttacctgtc
tttaatactgtgaaggaggccaaagaacagacaggagcaacggcttctgtcatttatgtt
cctccgccttttgctgctgctgccattaatgaagctattgaggcagaaattcccttggtt
gtgtgtatcactgaaggaattccccagcaggacatggtacgagtcaagcacaaactgctg
cgccaggaaaagacaaggctaattgggcccaactgccctggagtcatcaatcctggagaa
tgtaaaattggcatcatgcctggccatattcacaaaaaaggaaggattggcattgtgtcc
agatctggcaccctgacttatgaagcagttcaccaaacaacgcaagttggattggggcag
tctttgtgcgttggcattggaggtgatccttttaatggaacagattttattgactgcctc
gaaatctttttgaacgattctgccacagaaggcatcatattgattggtgaaattggtggt
aatgcagaagagaatgctgcagaatttttgaagcaacataattcaggtccaaattccaag
cctgtagtgtccttcattgctggtttaactgctcctcctgggagaagaatgggtcatgcc
ggggcaattattgctggaggaaaaggtggagctaaagagaagatctctgcccttcagagt
gcaggagttgtggtcagtatgtctcctgcacagctgggaaccacgatctacaaggaattt
gaaaagaggaagatgctatga

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