KEGG   Mus musculus (house mouse): 12040
Entry
12040             CDS       T01002                                 
Symbol
Bckdhb, BCKDE1B, BCKDH_E1-beta
Name
(RefSeq) branched chain ketoacid dehydrogenase E1, beta polypeptide
  KO
K00167  2-oxoisovalerate dehydrogenase E1 component subunit beta [EC:1.2.4.4]
Organism
mmu  Mus musculus (house mouse)
Pathway
mmu00280  Valine, leucine and isoleucine degradation
mmu00640  Propanoate metabolism
mmu00785  Lipoic acid metabolism
mmu01100  Metabolic pathways
mmu01210  2-Oxocarboxylic acid metabolism
Module
mmu_M00036  Leucine degradation, leucine => acetoacetate + acetyl-CoA
Brite
KEGG Orthology (KO) [BR:mmu00001]
 09100 Metabolism
  09101 Carbohydrate metabolism
   00640 Propanoate metabolism
    12040 (Bckdhb)
  09105 Amino acid metabolism
   00280 Valine, leucine and isoleucine degradation
    12040 (Bckdhb)
  09108 Metabolism of cofactors and vitamins
   00785 Lipoic acid metabolism
    12040 (Bckdhb)
Enzymes [BR:mmu01000]
 1. Oxidoreductases
  1.2  Acting on the aldehyde or oxo group of donors
   1.2.4  With a disulfide as acceptor
    1.2.4.4  3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)
     12040 (Bckdhb)
SSDB
Motif
Pfam: Transket_pyr Transketolase_C
Other DBs
NCBI-GeneID: 12040
NCBI-ProteinID: NP_001292864
MGI: 88137
Ensembl: ENSMUSG00000032263
UniProt: Q6P3A8
Position
9:83807190..84006293
AA seq 390 aa
MAAVAARAGGLLWLRAAGAERRRCGLRCAALVQGFLQPGGEDTAQKRRVAHFTFHPDPES
LQYGQTQKMNLFQSITSALDNSLAKDPTAVIFGEDVAFGGVFRCTVGLRDKYGKDRVFNT
PLCEQGIVGFGIGIAVTGATAIAEIQFADYIFPAFDQIVNEAAKYRYRSGDLFNCGSLTI
RAPWGCVGHGALYHSQSPEAFFAHCPGIKVVIPRSPFQAKGLLLSCIEDKNPCIFFEPKI
LYRAAVEQVPVEPYKIPLSQAEVIQEGSDVTLVAWGTQVHVIREVASMAQEKLGVSCEVI
DLRTIVPWDVDTVCKSVIKTGRLLISHEAPLTGGFASEISSTVQEECFLNLEAPISRVCG
YDTPFPHIFEPFYIPDKWKCYDALRKMINY
NT seq 1173 nt   +upstreamnt  +downstreamnt
atggcggcggtggctgcgcgcgcgggtgggctgctgtggctccgggctgcgggagcagag
cggcggcggtgcggactgcgctgcgctgcgctggtgcaaggcttcctgcaacccgggggc
gaggacacggcccagaagcggcgggtggcccacttcactttccatccggacccagagtcc
ctgcagtatgggcaaactcagaagatgaacctcttccagtcaataacaagtgccctggat
aactcattagccaaagaccccactgcagtaatatttggtgaagatgttgcctttggtgga
gtcttccgatgcactgttggtttacgagacaaatacggaaaagatagagtgtttaacacc
ccgttgtgtgaacaaggaatagttggatttggcattggaatcgcggtcaccggtgctaca
gctattgcggaaatccagtttgccgactatattttccctgcctttgatcagattgtcaac
gaagctgccaagtatcgctaccgctcaggtgatcttttcaactgtgggagcctcaccatc
cgggccccgtggggttgtgtgggccatggggctctctaccattctcagagtcctgaagcc
ttttttgcccattgcccagggatcaaggtggtaataccccgaagccctttccaggccaag
ggacttctgttgtcatgcatagaagataaaaatccatgtatattttttgaacctaaaata
ctttaccgggcagcagtggaacaggtcccagtagaaccctacaagatccccttgtctcag
gctgaagtcatccaggagggcagcgatgtgactctggttgcctggggcactcaggttcat
gtcatccgggaggtggcttccatggcccaagaaaagcttggagtatcttgtgaagtcatc
gatctgcggacaattgtgccttgggatgtggatacagtttgcaagtctgtgatcaaaacc
gggcgactgttgatcagccacgaggctcccttaacaggcggctttgcctctgagatcagc
tccacggtccaggaagaatgtttcttgaacctagaggctccaatatctcgagtttgcgga
tatgacaccccgtttcctcacatctttgagcccttttatatcccagacaaatggaagtgc
tacgatgcccttcgcaagatgatcaactattga

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