KEGG   Mus musculus (house mouse): 72039
Entry
72039             CDS       T01002                                 
Symbol
Mccc1, 1810045E08Rik, 2310058B18Rik, MCCalpha, Mcca
Name
(RefSeq) methylcrotonoyl-Coenzyme A carboxylase 1 (alpha)
  KO
K01968  3-methylcrotonyl-CoA carboxylase alpha subunit [EC:6.4.1.4]
Organism
mmu  Mus musculus (house mouse)
Pathway
mmu00280  Valine, leucine and isoleucine degradation
mmu01100  Metabolic pathways
Module
mmu_M00036  Leucine degradation, leucine => acetoacetate + acetyl-CoA
Brite
KEGG Orthology (KO) [BR:mmu00001]
 09100 Metabolism
  09105 Amino acid metabolism
   00280 Valine, leucine and isoleucine degradation
    72039 (Mccc1)
Enzymes [BR:mmu01000]
 6. Ligases
  6.4  Forming carbon-carbon bonds
   6.4.1  Ligases that form carbon-carbon bonds (only sub-subclass identified to date)
    6.4.1.4  methylcrotonoyl-CoA carboxylase
     72039 (Mccc1)
SSDB
Motif
Pfam: CPSase_L_D2 Biotin_carb_N Biotin_carb_C Biotin_lipoyl Dala_Dala_lig_C ATP-grasp Biotin_lipoyl_2 ATP-grasp_3 ATPgrasp_ST RimK ATP-grasp_4 HlyD_3 GARS_A HlyD_D23
Other DBs
NCBI-GeneID: 72039
NCBI-ProteinID: NP_076133
MGI: 1919289
Ensembl: ENSMUSG00000027709
UniProt: Q99MR8
Position
3:complement(36009584..36054843)
AA seq 717 aa
MAAAALLAAVDRNQLRRVPILLLQPREWAWKLRTMKYGTTPGGSITKVLIANRGEIACRV
IRTAKKMGVQSVAVYSEADRNSMHVDMADEAYSIGPAPSQQSYLAMEKIIQVAKSSAAQA
IHPGYGFLSENMEFAELCKQEGIIFIGPPSSAIRDMGIKSTSKSIMAAAGVPVVEGYHGK
DQSDQCLREHAGKIGYPVMIKAVRGGGGKGMRIVRSEREFQEQLESARREAKKSFNDDAM
LIEKFVDTPRHVEVQVFGDHHGNAVYLFERDCSVQRRHQKIIEEAPAPGINPEVRRKLGE
AAVRAAKAVKYVGAGTVEFIMDSRHNFYFMEMNTRLQVEHPVTEMITGTDLVEWQLRIAA
GEKIPLSQEEIPLQGHAFEARIYAEDPDNNFMPGAGPLVHLSTPSADMSTRIETGVRQGD
EVSVHYDPMIAKLVVWASDRQSALSKLRYCLHQYNIVGLRSNVDFLLRLSGHPEFEAGNV
HTDFIPQHHKDLLPSHSTIAKESVCQAALGLILKEKEMTSAFKLHTQDQFSPFSFSSGRR
LNISYTRNMTLRSGKSDIVIAVTYNRDGSYDMQIDNKSFRVLGDLSSEDGCTYLKSSING
VARKSKFILLDNTVHLFSMEGSIEVGIPVPKYLSPVSAEGAQGGTIAPMTGTIEKVFVKA
GDRVKAGDSLMVMIAMKMEHTIKAPKDGRIKKVFFSEGAQANRHAPLVEFEEEESDK
NT seq 2154 nt   +upstreamnt  +downstreamnt
atggcggcggcggcgttgttggctgcggtggacaggaaccagttgcgacgggtcccgatc
ctgctgctgcagccgagggaatgggcttggaagttgagaaccatgaagtatggaacaacc
ccaggaggaagtattaccaaggtcctcattgcaaacagaggagaaattgcctgcagggtg
atacgaacagccaaaaagatgggtgtgcagtcggtggctgtgtacagtgaggccgaccgg
aattccatgcatgtagatatggcagacgaggcatattccattggccctgctccatctcag
cagagctacctcgcaatggagaaaatcattcaagtggccaagagctctgcagcacaggcc
atccatccaggctacggttttctttcggaaaacatggagtttgctgaactttgtaagcaa
gagggaatcatttttataggtcctccttcgtctgcaattagagacatgggtataaagagc
acgtccaagtccatcatggctgctgctggagttcctgttgtggaaggttaccatggcaag
gaccagtctgatcagtgcctgagagagcatgctgggaaaatcgggtatcctgttatgatc
aaagcagtccgtggtggaggaggaaaaggcatgaggatcgttagatcagagagagaattc
caagagcagttagagtcagcccggagggaggcgaagaagtctttcaatgatgatgcaatg
ttgatcgagaagttcgtggacactccaaggcatgtagaagtccaggtgtttggtgatcac
catggcaacgcagtgtacttgtttgaaagagactgtagtgtgcagaggcgacatcagaag
atcattgaggaggccccagcgcctggtattaatcctgaagtaagaagaaagctgggagag
gctgcagtcagagctgcgaaggctgtcaagtacgtgggagcaggaactgtggaattcatt
atggactcaaggcacaatttttatttcatggagatgaacaccaggctacaagtggaacat
cctgtcactgaaatgatcacagggactgacttggtggagtggcaactcaggattgcagca
ggagagaagattcctttgagccaggaagaaatccctctgcagggccatgcctttgaggct
agaatctatgcagaagaccctgacaataacttcatgccaggggctggaccgttggttcat
ctctctaccccttcggcagacatgtctacgaggattgaaactggagtccggcaaggagat
gaagtctcggtgcattacgatcccatgatcgcaaagctcgttgtgtgggcctcagaccgc
cagtcagccctgtcgaagctgaggtactgccttcatcagtacaacattgtcggcttgcgc
agcaacgtggacttcctgctccggctctccggccacccagagtttgaggctgggaacgtg
cacacggacttcatccctcagcaccacaaggacctgctgccgagtcacagcactatagcc
aaagagtctgtgtgccaggcagctctggggctcatcctcaaagagaaagaaatgaccagc
gcttttaaactccacactcaagatcaattctctccgttttcattcagcagtgggagaaga
ctgaatatctcttacaccaggaacatgactctgagaagtggtaaaagtgatatagtcata
gctgtgacgtataaccgcgatgggtcatatgatatgcagattgacaacaagtccttccga
gtcctgggcgatctttccagtgaagatggctgtacctacctgaagtcttctattaatggg
gtagcccgtaaatccaagttcatcctcctggacaacactgtccacctgttttctatggaa
ggcagtattgaagttggcattccagtgcccaagtacttgtctccagtgagtgcagaagga
gctcaggggggcaccatcgcgcccatgactggaaccattgaaaaggtgtttgtgaaagct
ggagacagagtaaaagctggagactctctgatggttatgattgccatgaagatggagcat
accataaaggctccaaaggatggcaggataaagaaggtattcttcagtgaaggagcccaa
gccaacagacatgcacctttagtggaatttgaggaggaggagtctgacaaatga

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