KEGG   Rattus norvegicus (rat): 25244
Entry
25244             CDS       T01003                                 
Symbol
Bckdha
Name
(RefSeq) 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial
  KO
K00166  2-oxoisovalerate dehydrogenase E1 component subunit alpha [EC:1.2.4.4]
Organism
rno  Rattus norvegicus (rat)
Pathway
rno00280  Valine, leucine and isoleucine degradation
rno00640  Propanoate metabolism
rno00785  Lipoic acid metabolism
rno01100  Metabolic pathways
rno01210  2-Oxocarboxylic acid metabolism
Brite
KEGG Orthology (KO) [BR:rno00001]
 09100 Metabolism
  09101 Carbohydrate metabolism
   00640 Propanoate metabolism
    25244 (Bckdha)
  09105 Amino acid metabolism
   00280 Valine, leucine and isoleucine degradation
    25244 (Bckdha)
  09108 Metabolism of cofactors and vitamins
   00785 Lipoic acid metabolism
    25244 (Bckdha)
Enzymes [BR:rno01000]
 1. Oxidoreductases
  1.2  Acting on the aldehyde or oxo group of donors
   1.2.4  With a disulfide as acceptor
    1.2.4.4  3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)
     25244 (Bckdha)
SSDB
Motif
Pfam: E1_dh TPP_enzyme_C DXP_synthase_N
Other DBs
NCBI-GeneID: 25244
NCBI-ProteinID: NP_036914
RGD: 2196
Ensembl: ENSRNOG00000020607
UniProt: P11960 Q5EB89 B1WBN3
Position
1:complement(90266731..90295521)
AA seq 446 aa
MAVAMSAAKIWRPSRGLRQAALLLLGRPGARGLARFHPSRQQQQQFPSLDDKPQFPGASA
EFVDKLEFIQPNVISGIPIYRVMDRQGQIINPSEDPHLPQEEVLKLYRSMTLLNTMDRIL
YESQRQGRISFYMTNYGEEGTHVGSAAALERTDLVFGQYREAGVLMYRDYPLELFMAQCY
GNVSDPGKGRQMPVHYGCKERHFVTISSPLATQIPQAVGAAYAAKRANANQIVICYFGEG
AASEGDAHAGFNFAATLECPIIFFCRNNGYAISTPTSEQYRGDGIAARGPGYGIMSIRVD
GNDVFAVYNATKEARRRAVAENQPFLIEAMTYRIGHHSTSDDSSAYRSVDEVNYWDKQDH
PISRLRQYLLNQGWWDEEQEKAWRKQSRKKVMEAFEQAERKLKPNPSLLFSDVYQEMPAQ
LRRQQESLARHLQTYGEHYPLDHFDK
NT seq 1341 nt   +upstreamnt  +downstreamnt
atggcggtagcgatgtccgcggccaagatctggaggccgagccgtggcctgcgccaggct
gccctcttgctgttggggcgacctggggctcggggcttggctagattccaccccagcagg
cagcagcaacagcagttcccatccctggatgacaagccccagttcccaggggcctctgca
gagtttgtagacaagcttgagttcatccagcccaatgtcatctccggcatccccatctac
cgcgtcatggaccgacagggccagatcatcaaccccagtgaagatccccacctgccccag
gaggaggtcctgaagttgtacaggagcatgacgctgctcaacaccatggaccgcattctc
tatgagtcccagcgacagggccggatctccttctacatgaccaactatggcgaggagggg
acacatgtggggagtgccgctgccctggagcgaacggacctggtgtttggccagtaccgg
gaggcaggtgtgctcatgtaccgggactacccgctggagctgttcatggcccagtgctac
ggcaacgtgagtgacccaggcaagggacgccagatgcccgttcactacggctgcaaggag
cgtcacttcgtcaccatttcctctccactggctacgcagatccctcaggcggtaggggca
gcctatgctgccaagcgggccaatgccaatcagatcgtgatctgttactttggcgagggg
gcagccagtgaaggggatgcccacgccggtttcaattttgctgccaccttggagtgtcct
atcatcttcttctgccggaacaatggctatgccatctccacaccaacctctgagcagtac
cgtggggatggcatagcggctcggggccctgggtatggcatcatgtcaatccgtgtggac
ggcaacgatgtgtttgcggtgtacaatgccactaaggaggcccgacggcgggctgtggct
gagaaccagcccttcctcattgaggccatgacctacaggatcgggcaccacagcaccagt
gacgacagctctgcgtaccgttcggtggatgaggtcaattactgggacaagcaggaccac
ccgatctcgagactgaggcagtacctgctgaaccagggttggtgggatgaggaacaggag
aaggcctggcggaagcagtcacgaaagaaggtgatggaggcctttgaacaggctgagcgg
aagctaaagcccaacccaagcctcctcttctccgatgtgtaccaggagatgcctgcccag
ctgcgcaggcagcaggagtccctggctcggcacctgcagacctacggggagcactacccc
ctggaccactttgacaagtga

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