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Mitochondrial Biogenesis - Danio rerio (zebrafish)
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AMitochondrial DNA transcription, translation, and replication factors
B Mitochondrial DNA-encoded proteins
C Mitochondrial respiratory chain complex I
D 140531 ND1; NADH dehydrogenase subunit 1 K03878 ND1; NADH-ubiquinone oxidoreductase chain 1 [EC:7.1.1.2]
D 140532 ND2; NADH dehydrogenase subunit 2 K03879 ND2; NADH-ubiquinone oxidoreductase chain 2 [EC:7.1.1.2]
D 140533 ND3; NADH dehydrogenase subunit 3 K03880 ND3; NADH-ubiquinone oxidoreductase chain 3 [EC:7.1.1.2]
D 140534 ND4; NADH dehydrogenase subunit 4 K03881 ND4; NADH-ubiquinone oxidoreductase chain 4 [EC:7.1.1.2]
D 140538 ND4L; NADH dehydrogenase subunit 4L K03882 ND4L; NADH-ubiquinone oxidoreductase chain 4L [EC:7.1.1.2]
D 140535 ND5; NADH dehydrogenase subunit 5 K03883 ND5; NADH-ubiquinone oxidoreductase chain 5 [EC:7.1.1.2]
D 140536 ND6; NADH dehydrogenase subunit 6 K03884 ND6; NADH-ubiquinone oxidoreductase chain 6 [EC:7.1.1.2]
C Mitochondrial respiratory chain complex III
D 140512 CYTB; cytochrome b K00412 CYTB; ubiquinol-cytochrome c reductase cytochrome b subunit
C Cytochrome c oxidase
D 140539 COX1; cytochrome c oxidase subunit I K02256 COX1; cytochrome c oxidase subunit 1 [EC:7.1.1.9]
D 140540 COX2; cytochrome c oxidase subunit II K02261 COX2; cytochrome c oxidase subunit 2
D 140541 COX3; cytochrome c oxidase subunit III K02262 COX3; cytochrome c oxidase subunit 3
C F-type ATPase
D 140520 ATP8; ATP synthase F0 subunit 8 K02125 ATPeF08; F-type H+-transporting ATPase subunit 8
D 140519 ATP6; ATP synthase F0 subunit 6 K02126 ATPeF0A; F-type H+-transporting ATPase subunit a
B Mitochondrial transcription and translation factors
C Mitochondrial RNA polymerase
D 100034434 polrmt; DNA-directed RNA polymerase, mitochondrial isoform X1 K10908 POLRMT; DNA-directed RNA polymerase, mitochondrial [EC:2.7.7.6]
C Mitochondrial transcription factors
D 571106 tfam; transcription factor A, mitochondrial K11830 TFAM; transcription factor A, mitochondrial
D 767802 tfb1m; dimethyladenosine transferase 1, mitochondrial K15266 TFB1M; dimethyladenosine transferase 1, mitochondrial [EC:2.1.1.-]
D 569468 tfb2m; dimethyladenosine transferase 2, mitochondrial precursor K17653 TFB2M; dimethyladenosine transferase 2, mitochondrial [EC:2.1.1.-]
C Mitochondrial translation factors
D 556465 mtif2; translation initiation factor IF-2, mitochondrial K02519 infB; translation initiation factor IF-2
D 325802 mtif3; translation initiation factor IF-3, mitochondrial K02520 infC; translation initiation factor IF-3
D 567785 tsfm; elongation factor Ts, mitochondrial K02357 tsf; elongation factor Ts
D 541378 tufm; elongation factor Tu, mitochondrial K02358 tuf; elongation factor Tu
D 558184 gfm2; ribosome-releasing factor 2, mitochondrial K02355 fusA; elongation factor G
D 561840 gfm1; elongation factor G, mitochondrial K02355 fusA; elongation factor G
D 557469 mterf2; transcription termination factor 2, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein
D 100536997 mterf1; transcription termination factor 1, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein
D 100000849 mterf4; transcription termination factor 4, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein
D 436888 mterf3; transcription termination factor 3, mitochondrial precursor K15031 MTERF; mitochondrial transcription termination factor family protein
D 553030 guf1; translation factor GUF1, mitochondrial isoform X1 K21594 GUF1; translation factor GUF1, mitochondrial [EC:3.6.5.-]
C RNase MRP
D 799016 pop1; ribonucleases P/MRP protein subunit POP1 K01164 POP1; ribonuclease P/MRP protein subunit POP1 [EC:3.1.26.5]
D 553787 pop4; ribonuclease P protein subunit p29 K03538 POP4; ribonuclease P protein subunit POP4 [EC:3.1.26.5]
D 541421 pop5; ribonuclease P/MRP protein subunit POP5 K03537 POP5; ribonuclease P/MRP protein subunit POP5 [EC:3.1.26.5]
D 541352 rpp30; ribonuclease P protein subunit p30 K03539 RPP1; ribonuclease P/MRP protein subunit RPP1 [EC:3.1.26.5]
D 100004610 pop7; ribonuclease P protein subunit p20 K14527 RPP20; ribonuclease P/MRP protein subunit RPP20 [EC:3.1.26.5]
D 100000532 rpp25a; ribonuclease P protein subunit p25a K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5]
D 436813 rpp25l; ribonuclease P protein subunit p25-like protein K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5]
D 101885168 rpp25b; ribonuclease P protein subunit p25b K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5]
D 436798 rpp38; ribonuclease P protein subunit p38 K14523 RPP38; ribonucleases P/MRP protein subunit RPP38 [EC:3.1.26.5]
D 415238 rpp40; ribonuclease P protein subunit p40 K14530 RPP40; ribonucleases P/MRP protein subunit RPP40 [EC:3.1.26.5]
C Mitochondrial ribonuclease P
D 492460 trmt10c; tRNA methyltransferase 10 homolog C K17654 TRMT10C; mitochondrial ribonuclease P protein 1 [EC:2.1.1.-]
D 450078 hsd17b10; 3-hydroxyacyl-CoA dehydrogenase type-2 K08683 HSD17B10; 3-hydroxyacyl-CoA dehydrogenase / 3-hydroxy-2-methylbutyryl-CoA dehydrogenase [EC:1.1.1.35 1.1.1.178]
D 555630 si:dkeyp-33b5.4; mitochondrial ribonuclease P protein 3 K17655 MRPP3; mitochondrial ribonuclease P protein 3
C Other mitochondrial DNA transcription and translation factors
D 100330275 mss51; putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51
D 103908684 putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51
D 566236 tefm; transcription elongation factor, mitochondrial K17658 TEFM; transcription elongation factor, mitochondrial
D 570247 ptcd1; pentatricopeptide repeat-containing protein 1, mitochondrial isoform X1 K17710 PTCD1; pentatricopeptide repeat domain-containing protein 1
D 550275 ptcd2; pentatricopeptide repeat-containing protein 2, mitochondrial K17711 PTCD2; pentatricopeptide repeat domain-containing protein 2
D 553325 ptcd3; small ribosomal subunit protein mS39 precursor K17659 PTCD3; pentatricopeptide repeat domain-containing protein 3
D 570735 dhx30; putative ATP-dependent RNA helicase DHX30 isoform X2 K13185 DHX30; ATP-dependent RNA helicase DHX30 [EC:5.6.2.6]
D 767788 uqcc1; ubiquinol-cytochrome-c reductase complex assembly factor 1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3
D 555926 afg1lb; lactation elevated protein 1 homolog B K18798 AFG1; peroxisome-assembly ATPase [EC:3.6.4.7]
D 561238 afg1la; AFG1 like ATPase a K18798 AFG1; peroxisome-assembly ATPase [EC:3.6.4.7]
D 100004177 atp23; mitochondrial inner membrane protease ATP23 homolog K18156 ATP23; mitochondrial inner membrane protease ATP23 [EC:3.4.24.-]
D 570852 supv3l1; ATP-dependent RNA helicase SUPV3L1, mitochondrial precursor K17675 SUPV3L1; ATP-dependent RNA helicase SUPV3L1/SUV3 [EC:5.6.2.6]
D 405820 lactb2; endoribonuclease LACTB2 K16639 LACTB2; endoribonuclease LACTB2 [EC:3.1.27.-]
D 192321 slc25a5; ADP/ATP translocase 2 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 327067 slc25a4; ADP/ATP translocase 1 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 566370 slc25a6; ADP/ATP translocase 3 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 100038774 si:dkey-251i10.1; uncharacterized protein LOC100038774 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31
D 100535877 slc25a28; mitoferrin-2 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37
D 387000 slc25a37; mitoferrin-1 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37
D 796868 malsu1; mitochondrial assembly of ribosomal large subunit protein 1 K25803 MALSU1; mitochondrial assembly of ribosomal large subunit protein 1
D 569087 eral1; GTPase Era, mitochondrial K03595 era; GTPase
D 368235 yars1; tyrosine--tRNA ligase, cytoplasmic K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1]
D 556702 yars2; tyrosine--tRNA ligase, mitochondrial K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1]
D 100126021 lars2; probable leucine--tRNA ligase, mitochondrial K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4]
D 569778 larsb; leucine--tRNA ligase, cytoplasmic K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4]
D 571144 dars2; aspartate--tRNA ligase, mitochondrial K01876 DARS2; aspartyl-tRNA synthetase [EC:6.1.1.12]
D 337230 gars1; glycine--tRNA ligase K01880 GARS; glycyl-tRNA synthetase [EC:6.1.1.14]
D 337070 rars1; arginine--tRNA ligase, cytoplasmic K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19]
D 393589 rars2; probable arginine--tRNA ligase, mitochondrial K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19]
D 327329 qrsl1; glutamyl-tRNA(Gln) amidotransferase subunit A, mitochondrial K02433 gatA; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit A [EC:6.3.5.6 6.3.5.7]
D 541317 gatb; glutamyl-tRNA(Gln) amidotransferase subunit B, mitochondrial K02434 gatB; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit B [EC:6.3.5.6 6.3.5.7]
D 558898 gatc; glutamyl-tRNA(Gln) amidotransferase subunit C, mitochondrial K02435 gatC; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit C [EC:6.3.5.6 6.3.5.7]
D 563801 mtpap; poly(A) RNA polymerase, mitochondrial K18060 MTPAP; poly(A) RNA polymerase, mitochondrial [EC:2.7.7.19]
D 692319 pde12; 2',5'-phosphodiesterase 12 K19612 PDE12; 2',5'-phosphodiesterase [EC:3.1.13.4 3.1.4.-]
D 100150980 mtg1; mitochondrial ribosome-associated GTPase 1 isoform 1 K19828 MTG1; mitochondrial GTPase 1
D 564706 noa1; nitric oxide-associated protein 1 K19832 NOA1; nitric oxide-associated protein 1
D 101883563 nitric oxide-associated protein 1-like K19832 NOA1; nitric oxide-associated protein 1
D 553534 nsun3; tRNA (cytosine(34)-C(5))-methyltransferase, mitochondrial K21969 NSUN3; tRNA (cytosine34-C5)-methyltransferase [EC:2.1.1.-]
D 494106 nsun4; 5-methylcytosine rRNA methyltransferase NSUN4 K21970 NSUN4; 5-methylcytosine rRNA methyltransferase NSUN4 [EC:2.1.1.-]
D 445101 rpusd4; pseudouridylate synthase RPUSD4, mitochondrial K22538 RPUSD4; mitochondrial RNA pseudouridine synthase RPUSD4 [EC:5.4.99.-]
D 555972 rcc1l; RCC1-like G exchanging factor-like protein K23495 RCC1L; RCC1-like G exchanging factor-like protein
D 569275 ngrn; neugrin K23496 NGRN; neugrin
D 431747 trub2; mitochondrial mRNA pseudouridine synthase TRUB2 K23497 TRUB2; mitochondrial mRNA pseudouridine synthase TRUB2 [EC:5.4.99.-]
D 564382 fastkd2; FAST kinase domain-containing protein 2, mitochondrial K18190 FASTKD2; FAST kinase domain-containing protein 2
D 100004874 mtrfr; mitochondrial translation release factor in rescue K23498 COXPD7; peptide chain release factor
D 553810 rmnd1; required for meiotic nuclear division protein 1 homolog K23499 RMND1; required for meiotic nuclear division protein 1
D 563249 grsf1; G-rich sequence factor 1 K24984 GRSF1; G-rich sequence factor 1
D 560573 mettl15; probable methyltransferase-like protein 15 K25876 METTL15; 12S rRNA N4-methylcytidine (m4C) methyltransferase [EC:2.1.1.-]
D 664752 myg1; UPF0160 protein MYG1, mitochondrial K25877 MYG1; MYG1 exonuclease [EC:3.1.-.-]
D 565648 mtres1; mitochondrial transcription rescue factor 1 K26186 MTRES1; mitochondrial transcription rescue factor 1
B Mitochondrial DNA replication factors
C Mitochondrial DNA polymerase
D 100150924 polg; DNA polymerase subunit gamma-1 K02332 POLG; DNA polymerase gamma 1 [EC:2.7.7.7]
D 100150674 polg2; DNA polymerase subunit gamma-2, mitochondrial K02333 POLG2; DNA polymerase gamma 2
D 556571 primpol; DNA-directed primase/polymerase protein K22761 PRIMPOL; DNA-directed primase/polymerase protein [EC:2.7.7.102 2.7.7.7]
C Mitochondrial DNA maintenance factors
D 100002293 endog; endonuclease G, mitochondrial K01173 ENDOG; endonuclease G, mitochondrial
D 101885345 uncharacterized protein LOC101885345 K01173 ENDOG; endonuclease G, mitochondrial
D 101886621 endonuclease G, mitochondrial-like K01173 ENDOG; endonuclease G, mitochondrial
D 494097 mgme1; mitochondrial genome maintenance exonuclease 1 K19465 MGME1; mitochondrial genome maintenance exonuclease 1 [EC:3.1.-.-]
D 100330448 twnk; twinkle protein, mitochondrial K17680 PEO1; twinkle protein [EC:5.6.2.3]
D 326729 pif1; ATP-dependent DNA helicase PIF1 K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3]
C Other Mitochondrial DNA replication factors
D 550504 ssbp1; single-stranded DNA-binding protein, mitochondrial K03111 ssb; single-strand DNA-binding protein
D 403004 atad3; ATPase family AAA domain containing 3 K17681 ATAD3A_B; ATPase family AAA domain-containing protein 3A/B
D 393731 uqcc2; ubiquinol-cytochrome-c reductase complex assembly factor 2 K17682 MNF1; mitochondrial nucleoid factor 1
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AMitochondrial protein import machinery
B Endoplasmic reticulum membrane and cytosol
C ER-mitochondria encounter structure (ERMES) complex
C Other ER-memrane and cytosol factors
D 406814 dnaja2a; dnaJ homolog subfamily A member 2a K09503 DNAJA2; DnaJ homolog subfamily A member 2
D 324164 dnaja2b; dnaJ homolog subfamily A member 2b K09503 DNAJA2; DnaJ homolog subfamily A member 2
D 323361 tomm34; mitochondrial import receptor subunit TOM34 K17766 TOM34; mitochondrial import receptor subunit TOM34
D 327143 rhot1a; mitochondrial Rho GTPase 1-A K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 561933 rhot1b; mitochondrial Rho GTPase 1b K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 30671 hsp70.3; heat shock cognate 70-kd protein, tandem duplicate 3 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 393586 hsc70; uncharacterized protein LOC393586 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 573376 hspa8; heat shock cognate 71 kDa protein K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 560210 hsp70l; heat shock cognate 70-kd protein, like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 798846 hspa1b; Heat shock 70 kDa protein-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 100535101 hsp70.2; heat shock cognate 70-kd protein, tandem duplicate 2 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 100126123 hsp70.1; heat shock cognate 70-kd protein, tandem duplicate 1 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 562935 hspa8b; heat shock protein family A (Hsp70) member 8b K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8
D 100534741 uncharacterized protein LOC100534741 K17767 AIP; AH receptor-interacting protein
D 100537095 aipl1; aryl-hydrocarbon-interacting protein-like 1 K17767 AIP; AH receptor-interacting protein
D 334795 aip; AH receptor-interacting protein K17767 AIP; AH receptor-interacting protein
B Outer membrane
C Transporter outer membrane (TOM) complex
D 322645 tomm40; mitochondrial import receptor subunit TOM40 homolog K11518 TOM40; mitochondrial import receptor subunit TOM40
D 405895 tomm40l; mitochondrial import receptor subunit TOM40B K11518 TOM40; mitochondrial import receptor subunit TOM40
D 569883 si:dkey-71l1.1; uncharacterized protein LOC569883 K11518 TOM40; mitochondrial import receptor subunit TOM40
D 572969 tomm70a; mitochondrial import receptor subunit TOM70 K17768 TOM70; mitochondrial import receptor subunit TOM70
D 321232 tomm22; mitochondrial import receptor subunit TOM22 homolog K17769 TOM22; mitochondrial import receptor subunit TOM22
D 406309 tomm20a; translocase of outer mitochondrial membrane 20 K17770 TOM20; mitochondrial import receptor subunit TOM20
D 436971 tomm20b; mitochondrial import receptor subunit TOM20 homolog B K17770 TOM20; mitochondrial import receptor subunit TOM20
D 751649 tomm7; mitochondrial import receptor subunit TOM7 homolog K17771 TOM7; mitochondrial import receptor subunit TOM7
D 100001229 tomm6; mitochondrial import receptor subunit TOM6 homolog K17772 TOM6; mitochondrial import receptor subunit TOM6
D 497181 tomm5; mitochondrial import receptor subunit TOM5 homolog K17773 TOM5; mitochondrial import receptor subunit TOM5
C TOB/SAM complex
D 393111 samm50; sorting and assembly machinery component 50 homolog A K07277 SAM50; outer membrane protein insertion porin family
D 492471 samm50l; sorting and assembly machinery component 50 homolog B K07277 SAM50; outer membrane protein insertion porin family
C Porin
D 334582 vdac1; voltage-dependent anion-selective channel protein 1 K05862 VDAC1; voltage-dependent anion channel protein 1
D 322126 vdac2; voltage-dependent anion-selective channel protein 2 K15040 VDAC2; voltage-dependent anion channel protein 2
D 406529 vdac3; voltage-dependent anion-selective channel protein 3 K15041 VDAC3; voltage-dependent anion channel protein 3
D 393186 zgc:56235; Voltage-dependent anion-selective channel protein 2-like K15041 VDAC3; voltage-dependent anion channel protein 3
C ERMES complex
C Other outer membrane factor
D 286740 mtx1b; metaxin-1b K17776 MTX; metaxin
D 402916 mtx3; metaxin-3 K17776 MTX; metaxin
D 556917 mtx1a; metaxin-1a K17776 MTX; metaxin
D 286741 mtx2; metaxin-2 K17776 MTX; metaxin
D 562279 myo19; unconventional myosin-XIX K25838 MYO19; myosin XIX
D 378742 marc1; mitochondrial amidoxime-reducing component 1 K27318 MTARC; mitochondrial amidoxime-reducing component [EC:1.7.-.-]
B Inter membrane space
C Transporter inner membrane (TIM) 9/10 complex
D 282678 timm9; mitochondrial import inner membrane translocase subunit Tim9 K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9
D 436951 timm10; mitochondrial import inner membrane translocase subunit Tim10 K17778 TIM10; mitochondrial import inner membrane translocase subunit TIM10
D 550527 timm10b; mitochondrial import inner membrane translocase subunit Tim10 B K17779 TIM10B; mitochondrial import inner membrane translocase subunit TIM10B
C TIM8/13 complex
D 793663 timm8b; mitochondrial import inner membrane translocase subunit Tim8 B K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8
D 445243 timm8a; mitochondrial import inner membrane translocase subunit Tim8 A K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8
D 436738 timm13; mitochondrial import inner membrane translocase subunit Tim13 K17781 TIM13; mitochondrial import inner membrane translocase subunit TIM13
C Mitochondrial intermembrane space assembly (MIA) complex
D 445144 chchd4a; mitochondrial intermembrane space import and assembly protein 40 K17782 MIA40; mitochondrial intermembrane space import and assembly protein 40
D 450030 chchd4b; coiled-coil-helix-coiled-coil-helix domain containing 4b K17782 MIA40; mitochondrial intermembrane space import and assembly protein 40
D 560433 gfer; FAD-linked sulfhydryl oxidase ALR K17783 ERV1; mitochondrial FAD-linked sulfhydryl oxidase [EC:1.8.3.2]
B Inner mambrane
C MICOS complex
D 751699 micos10; MICOS complex subunit MIC10 K17784 MICOS10; MICOS complex subunit MIC10
D 327206 immt; MICOS complex subunit MIC60 K17785 IMMT; MICOS complex subunit MIC60
D 558738 micos13; MICOS complex subunit MIC13 K24624 MICOS13; MICOS complex subunit MIC13
D 325751 chchd3b; coiled-coil-helix-coiled-coil-helix domain containing 3b K17563 CHCHD3; MICOS complex subunit MIC19
D 407730 chchd3a; coiled-coil-helix-coiled-coil-helix domain containing 3a isoform 2 K17563 CHCHD3; MICOS complex subunit MIC19
D 492522 chchd6b; coiled-coil-helix-coiled-coil-helix domain containing 6b K17564 CHCHD6; MICOS complex subunit MIC25
D 449542 chchd6a; MICOS complex subunit mic25a K17564 CHCHD6; MICOS complex subunit MIC25
D 641319 apooa; apolipoprotein O, a isoform b K24625 APOO; MICOS complex subunit MIC26
D 449837 apoob; apolipoprotein O, b K24625 APOO; MICOS complex subunit MIC26
D 541537 apool; MICOS complex subunit MIC27 K24626 APOOL; MICOS complex subunit MIC27
C MICOS complex (yeast)
D 751699 micos10; MICOS complex subunit MIC10 K17784 MICOS10; MICOS complex subunit MIC10
D 327206 immt; MICOS complex subunit MIC60 K17785 IMMT; MICOS complex subunit MIC60
C TIM22 complex
D 100537779 timm22; mitochondrial import inner membrane translocase subunit Tim22 K17790 TIM22; mitochondrial import inner membrane translocase subunit TIM22
C TIM23 complex
D 100535463 timm23b; mitochondrial import inner membrane translocase subunit Tim23 K17794 TIM23; mitochondrial import inner membrane translocase subunit TIM23
D 798429 timm23a; mitochondrial import inner membrane translocase subunit Tim23 K17794 TIM23; mitochondrial import inner membrane translocase subunit TIM23
D 386636 timm17a; mitochondrial import inner membrane translocase subunit Tim17-A K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17
D 562144 timm17b; mitochondrial import inner membrane translocase subunit Tim17-B K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17
D 560369 timm21; mitochondrial import inner membrane translocase subunit Tim21-like K17796 TIM21; mitochondrial import inner membrane translocase subunit TIM21
D 393638 timm50; mitochondrial import inner membrane translocase subunit TIM50 precursor K17496 TIM50; mitochondrial import inner membrane translocase subunit TIM50
C Mitochondrial calcium uniporter complex
D 768182 mcu; calcium uniporter protein, mitochondrial K20858 MCU; calcium uniporter protein, mitochondrial
D 561210 micu1; calcium uptake protein 1, mitochondrial K22827 MICU1; calcium uptake protein 1, mitochondrial
D 548335 micu2; calcium uptake protein 2, mitochondrial K22828 MICU2; calcium uptake protein 2, mitochondrial
D 100000862 smdt1b; single-pass membrane protein with aspartate-rich tail 1b K22830 SMDT1; essential MCU regulator, mitochondrial
D 550408 zgc:165532; mitochondrial calcium uniporter regulator 1 K22137 MCUR1; mitochondrial calcium uniporter regulator 1
C Other inner membrane factors
D 570745 letm1; mitochondrial proton/calcium exchanger protein K17800 LETM1; LETM1 and EF-hand domain-containing protein 1, mitochondrial
D 795154 immp1l; mitochondrial inner membrane protease subunit 1 isoform 1 K09647 IMP1; mitochondrial inner membrane protease subunit 1 [EC:3.4.21.-]
D 445299 immp2l; mitochondrial inner membrane protease subunit 2 K09648 IMP2; mitochondrial inner membrane protease subunit 2 [EC:3.4.21.-]
D 393771 tmem126a; transmembrane protein 126A K18157 TMEM126A; transmembrane protein 126A
D 436671 mpc1; mitochondrial pyruvate carrier 1 K22138 MPC1; mitochondrial pyruvate carrier 1
D 321611 mpc2b; mitochondrial pyruvate carrier 2b K22139 MPC2; mitochondrial pyruvate carrier 2
D 447924 mpc2a; uncharacterized protein LOC447924 K22139 MPC2; mitochondrial pyruvate carrier 2
D 393757 chchd10; coiled-coil-helix-coiled-coil-helix domain-containing protein 10, mitochondrial K22759 CHCHD10; coiled-coil-helix-coiled-coil-helix domain-containing protein 10
B Matrix
C MMC/PAM proteins
D 541380 timm44; mitochondrial import inner membrane translocase subunit TIM44 K17804 TIM44; mitochondrial import inner membrane translocase subunit TIM44
D 373085 hspa9; stress-70 protein, mitochondrial K04043 dnaK; molecular chaperone DnaK
D 559037 grpel1; grpE protein homolog 1, mitochondrial K03687 GRPE; molecular chaperone GrpE
D 100004941 grpel2; grpE protein homolog 2, mitochondrial K03687 GRPE; molecular chaperone GrpE
D 393734 dnajc19; mitochondrial import inner membrane translocase subunit TIM14 K09539 DNAJC19; DnaJ homolog subfamily C member 19
D 393777 pam16; mitochondrial import inner membrane translocase subunit tim16 K17805 PAM16; mitochondrial import inner membrane translocase subunit TIM16
C Other matrix factors
D 492801 pmpca; mitochondrial-processing peptidase subunit alpha K01412 PMPCA; mitochondrial-processing peptidase subunit alpha [EC:3.4.24.64]
D 503532 pmpcb; mitochondrial-processing peptidase subunit beta K17732 PMPCB; mitochondrial-processing peptidase subunit beta [EC:3.4.24.64]
D 557349 si:ch73-1a9.4; mitochondrial intermediate peptidase isoform X2 K01410 MIPEP; mitochondrial intermediate peptidase [EC:3.4.24.59]
D 100005953 mipep; mitochondrial intermediate peptidase K01410 MIPEP; mitochondrial intermediate peptidase [EC:3.4.24.59]
D 282676 hspd1; 60 kDa heat shock protein, mitochondrial K04077 groEL; chaperonin GroEL [EC:5.6.1.7]
D 58041 hspe1; 10 kDa heat shock protein, mitochondrial isoform 1 K04078 groES; chaperonin GroES
D 335894 dnaja3a; DnaJ heat shock protein family (Hsp40) member A3a K09504 DNAJA3; DnaJ homolog subfamily A member 3
D 394242 dnaja3b; DnaJ heat shock protein family (Hsp40) member A3b K09504 DNAJA3; DnaJ homolog subfamily A member 3
D 554962 uncharacterized protein LOC554962 K09504 DNAJA3; DnaJ homolog subfamily A member 3
D 641323 tamm41; phosphatidate cytidylyltransferase, mitochondrial precursor K17807 TAM41; mitochondrial translocator assembly and maintenance protein 41
D 791166 dnlz; DNL-type zinc finger protein K17808 ZIM17; mitochondrial protein import protein ZIM17
D 405865 ethe1; persulfide dioxygenase ETHE1, mitochondrial K17725 ETHE1; sulfur dioxygenase [EC:1.13.11.18]
D 100000398 poldip2; polymerase delta-interacting protein 2 K17809 POLDIP2; polymerase delta-interacting protein 2
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AMitochondrial quality control factors
B Regulator of mitochondrial biogenesis
C Ubiquitas transcription factors
D 573207 creb1a; cyclic AMP-responsive element-binding protein 1a K05870 CREB1; cyclic AMP-responsive element-binding protein 1
D 558184 gfm2; ribosome-releasing factor 2, mitochondrial K02355 fusA; elongation factor G
D 561840 gfm1; elongation factor G, mitochondrial K02355 fusA; elongation factor G
D 324109 sp1; transcription factor Sp1 K04684 SP1; transcription factor Sp1
D 322397 yy1a; transcriptional repressor protein YY1a K09201 YY; transcription factor YY
D 406394 yy1b; transcriptional repressor protein YY1b K09201 YY; transcription factor YY
D 561215 gabpb2b; GA-binding protein subunit beta-2b K09454 GABPB; GA-binding protein transcription factor, beta
D 768285 gabpb1; GA-binding protein subunit beta-1 K09454 GABPB; GA-binding protein transcription factor, beta
D 554849 gabpb2a; GA-binding protein subunit beta-2a K09454 GABPB; GA-binding protein transcription factor, beta
D 571106 tfam; transcription factor A, mitochondrial K11830 TFAM; transcription factor A, mitochondrial
C Nuclear respiratory factors
D 64604 nrf1; nuclear respiratory factor 1 isoform 1 K11831 NRF1; nuclear respiratory factor 1
D 360149 nfe2l2a; nuclear factor erythroid 2-related factor 2a K05638 NFE2L2; nuclear factor erythroid 2-related factor 2
D 100174951 mt2; metallothionein-2 K14739 MT1_2; metallothionein 1/2
D 569445 mtbl; metallothionein-B-like K14739 MT1_2; metallothionein 1/2
D 30282 mt; metallothionein-1 K14739 MT1_2; metallothionein 1/2
C Coactivators
D 553418 ppargc1a; peroxisome proliferator-activated receptor gamma coactivator 1-alpha isoform X3 K07202 PPARGC1A; alpha peroxisome proliferator-activated receptor gamma coactivator 1-alpha
D 555906 ppargc1b; peroxisome proliferator-activated receptor gamma coactivator 1-beta K17962 PPARGC1B; peroxisome proliferator-activated receptor gamma coactivator 1-beta
D 100002463 pprc1; peroxisome proliferator-activated receptor gamma coactivator-related protein 1 K17963 PPRC1; peroxisome proliferator-activated receptor gamma coactivator-related protein 1
D 768293 crtc1a; uncharacterized protein LOC768293 K15309 CRTC1; CREB-regulated transcription coactivator 1
D 101886240 crtc1b; CREB-regulated transcription coactivator 1b K15309 CRTC1; CREB-regulated transcription coactivator 1
D 559273 ep300a; histone acetyltransferase p300 isoform X1 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48]
D 565612 ep300b; histone acetyltransferase p300 isoform X1 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48]
D 566841 crebbpa; CREB-binding protein isoform X1 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48]
D 567111 crebbpb; CREB binding protein b K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48]
C Proteins involved in Fe-S cluster biogenesis
D 562714 nfs1; cysteine desulfurase, mitochondrial K04487 iscS; cysteine desulfurase [EC:2.8.1.7]
D 445238 iscua; iron-sulfur cluster assembly enzyme ISCU, mitochondrial K22068 ISCU; iron-sulfur cluster assembly enzyme ISCU, mitochondrial
D 550498 iscub; iron-sulfur cluster assembly enzyme b K22068 ISCU; iron-sulfur cluster assembly enzyme ISCU, mitochondrial
D 100302660 lyrm4; LYR motif-containing protein 4 K22069 LYRM4; LYR motif-containing protein 4
D 103909737 LYR motif-containing protein 4 K22069 LYRM4; LYR motif-containing protein 4
D 556389 fxn; frataxin, mitochondrial K19054 FXN; frataxin [EC:1.16.3.1]
D 100126232 fdx1; adrenodoxin K22070 FDX1; ferredoxin-1, mitochondrial
D 562135 fdx1b; ferredoxin 1b K22070 FDX1; ferredoxin-1, mitochondrial
D 767726 fdx2; ferredoxin-2, mitochondrial precursor K22071 FDX2; ferredoxin-2, mitochondrial
D 100536115 fdxr; NADPH:adrenodoxin oxidoreductase, mitochondrial K18914 FDXR; adrenodoxin-NADP+ reductase [EC:1.18.1.6]
D 373085 hspa9; stress-70 protein, mitochondrial K04043 dnaK; molecular chaperone DnaK
D 100150029 hscb; iron-sulfur cluster co-chaperone protein HscB K04082 hscB; molecular chaperone HscB
D 568308 si:ch211-195b11.7; nucleotide exchange factor SIL1 K14001 SIL1; nucleotide exchange factor SIL1
D 406294 glrx5; glutaredoxin-related protein 5, mitochondrial K07390 grxD; monothiol glutaredoxin
D 573999 isca1; iron-sulfur cluster assembly 1 homolog, mitochondrial precursor K22063 ISCA1; iron-sulfur cluster assembly 1
D 100150438 isca2; iron-sulfur cluster assembly 2 homolog, mitochondrial K22072 ISCA2; iron-sulfur cluster assembly 2
D 100330979 iba57; putative transferase CAF17 homolog, mitochondrial K22073 IBA57; transferase CAF17, mitochondrial [EC:2.1.-.-]
D 403053 nfu1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial K22074 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial
D 796111 zgc:110319; uncharacterized protein LOC796111 K22074 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial
D 445163 bola1; bolA-like protein 1 K22066 BOLA1; BolA-like protein 1
D 445131 bola3; bolA-like protein 3 K22075 BOLA3; BolA-like protein 3
D 445143 sfxn1; sideroflexin-1 K23500 SFXN1_3; sideroflexin-1/3
D 791182 sfxn3; sideroflexin-3 K23500 SFXN1_3; sideroflexin-1/3
D 334757 sfxn2; sideroflexin-2 K23501 SFXN2; sideroflexin-2
D 556121 sfxn4; sideroflexin-4 K23502 SFXN4; sideroflexin-4
D 561995 sfxn5b; sideroflexin-5b K23503 SFXN5; sideroflexin-5
D 562654 sfxn5a; sideroflexin-5a K23503 SFXN5; sideroflexin-5
C Other regulator of mitochondrial biogenesis
D 560000 cpt1ab; carnitine O-palmitoyltransferase 1, liver isoform isoform X2 K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
D 558088 cpt1aa; carnitine palmitoyltransferase 1Aa (liver) K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
D 100333227 carnitine O-palmitoyltransferase 1, liver isoform-like K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
D 449677 cpt1b; carnitine O-palmitoyltransferase 1, muscle isoform K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
D 550361 cpt1cb; carnitine O-palmitoyltransferase 1, liver isoform isoform X2 K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21]
D 494076 dhtkd1; 2-oxoadipate dehydrogenase complex component E1 K15791 DHKTD1; 2-oxoadipate dehydrogenase E1 component [EC:1.2.4.-]
D 492349 fbxl4; F-box/LRR-repeat protein 4 K10270 FBXL4; F-box and leucine-rich repeat protein 4
D 564853 hcfc1a; host cell factor 1a K14966 HCFC1; host cell factor 1
D 565206 hcfc1b; host cell factor 1b K14966 HCFC1; host cell factor 1
D 550401 hcfc2; host cell factor 2 K27390 HCFC2; host cell factor 2
D 30214 htt; huntingtin K04533 HD; huntingtin
D 405891 esrra; steroid hormone receptor ERR1 K08552 NR3B1; estrogen-related receptor alpha
D 407693 esrrb; steroid hormone receptor ERR2 K08553 NR3B2; estrogen-related receptor beta
D 405890 esrrga; estrogen-related receptor gamma a K08554 NR3B3; estrogen-related receptor gamma
D 407691 esrrgb; estrogen-related receptor gamma b K08554 NR3B3; estrogen-related receptor gamma
D 407692 esrrd; estrogen-related receptor gamma K08554 NR3B3; estrogen-related receptor gamma
D 100001853 nrip1b; nuclear receptor-interacting protein 1 K17965 NRIP1; nuclear receptor-interacting protein 1
D 796407 nrip1a; nuclear receptor-interacting protein 1 K17965 NRIP1; nuclear receptor-interacting protein 1
D 572074 prkaa2; 5'-AMP-activated protein kinase catalytic subunit alpha-2 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 100001198 prkaa1; 5'-AMP-activated protein kinase catalytic subunit alpha-1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 563257 lonp1; lon protease homolog, mitochondrial K08675 PRSS15; ATP-dependent Lon protease [EC:3.4.21.53]
D 797132 sirt1; NAD-dependent protein deacetylase sirtuin-1 isoform X1 K11411 SIRT1; NAD-dependent protein deacetylase sirtuin 1 [EC:2.3.1.286]
D 568022 serac1; protein SERAC1 K23504 SERAC1; protein SERAC1
D 447933 uxt; protein UXT K26537 UXT; protein UXT
B Mitochondrial respiratory chain complex assembly factors
C Complex-I assembly factors
D 503714 ndufaf1; complex I intermediate-associated protein 30, mitochondrial K18159 NDUFAF1; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 1
D 100003850 ndufaf2; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2 K18160 NDUFAF2; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2
D 791133 ndufaf3; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3 K09008 NDUFAF3; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3
D 794169 ndufaf4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4 K18161 NDUFAF4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4
D 794020 ndufaf5; arginine-hydroxylase NDUFAF5, mitochondrial precursor K18162 NDUFAF5; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 5 [EC:2.1.1.-]
D 569692 ndufaf6; NADH dehydrogenase (ubiquinone) complex I, assembly factor 6 K18163 NDUFAF6; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 6
D 767796 ndufaf7; protein arginine methyltransferase NDUFAF7, mitochondrial precursor K18164 NDUFAF7; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 7
D 386981 ndufaf8; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 8 K24726 NDUFAF8; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 8
D 569243 ecsit; evolutionarily conserved signaling intermediate in Toll pathway, mitochondrial K04405 ECSIT; evolutionarily conserved signaling intermediate in Toll pathway
D 724002 acad9; complex I assembly factor ACAD9, mitochondrial K15980 ACAD9; acyl-CoA dehydrogenase family member 9 [EC:1.3.99.-]
D 436715 nubpl; iron-sulfur protein NUBPL K03593 mrp; ATP-binding protein involved in chromosome partitioning
D 556387 foxred1; FAD-dependent oxidoreductase domain-containing protein 1 K18166 FOXRED1; FAD-dependent oxidoreductase domain-containing protein 1
D 393323 rtn4ip1; reticulon-4-interacting protein 1 homolog, mitochondrial K23164 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial
D 550526 timmdc1; complex I assembly factor TIMMDC1, mitochondrial K23505 TIMMDC1; complex I assembly factor TIMMDC1
C Complex-II assembly factors
D 606612 sdhaf1; succinate dehydrogenase assembly factor 1, mitochondrial K18167 SDHAF1; succinate dehydrogenase assembly factor 1
D 569482 sdhaf2; succinate dehydrogenase assembly factor 2, mitochondrial precursor K18168 SDHAF2; succinate dehydrogenase assembly factor 2
C Complex-III assembly factors
D 394157 bcs1l; mitochondrial chaperone BCS1 K08900 BCS1; mitochondrial chaperone BCS1
D 564788 ttc19; tetratricopeptide repeat protein 19, mitochondrial K18169 TTC19; tetratricopeptide repeat protein 19, mitochondrial
D 100002948 lyrm7; complex III assembly factor LYRM7 K18170 LYRM7; complex III assembly factor LYRM7
D 767788 uqcc1; ubiquinol-cytochrome-c reductase complex assembly factor 1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3
D 393731 uqcc2; ubiquinol-cytochrome-c reductase complex assembly factor 2 K17682 MNF1; mitochondrial nucleoid factor 1
D 558925 uqcc3; ubiquinol-cytochrome-c reductase complex assembly factor 3 K23165 UQCC3; ubiquinol-cytochrome-c reductase complex assembly factor 3
D 101882877 uqcc4; protein CCSMST1-like K27339 UQCC4; ubiquinol-cytochrome c reductase complex assembly factor 4
D 100332503 smim4; small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5
D 100190888 uqcc6; ubiquinol-cytochrome-c reductase complex assembly factor 6 K27341 UQCC6; ubiquinol-cytochrome c reductase complex assembly factor 6
D 100170826 stmp1; short transmembrane mitochondrial protein 1 K27319 STMP1; short transmembrane mitochondrial protein 1
C Complex-IV assembly factors
D 406630 cmc1; COX assembly mitochondrial protein homolog K18171 CMC1; COX assembly mitochondrial protein 1
D 368857 cmc2; COX assembly mitochondrial protein 2 homolog K18172 CMC2; COX assembly mitochondrial protein 2
D 108179075 coa1; cytochrome c oxidase assembly factor 1 homolog isoform X1 K18173 COA1; cytochrome c oxidase assembly factor 1
D 100141351 coa3a; cytochrome c oxidase assembly factor 3 homolog, mitochondrial K18175 CCDC56; cytochrome c oxidase assembly factor 3, animal type
D 335493 coa3b; cytochrome C oxidase assembly factor 3b K18175 CCDC56; cytochrome c oxidase assembly factor 3, animal type
D 796017 coa4; cytochrome c oxidase assembly factor 4 homolog, mitochondrial K18177 COA4; cytochrome c oxidase assembly factor 4
D 751633 coa5; cytochrome c oxidase assembly factor 5 K18178 COA5; cytochrome c oxidase assembly factor 5
D 100150991 coa6; cytochrome c oxidase assembly factor 6 homolog K18179 COA6; cytochrome c oxidase assembly factor 6
D 555268 coa7; cytochrome c oxidase assembly factor 7 K18180 COA7; cytochrome c oxidase assembly factor 7
D 553384 cox10; protoheme IX farnesyltransferase, mitochondrial K02257 COX10; heme o synthase [EC:2.5.1.141]
D 100005158 cox11; cytochrome c oxidase assembly protein COX11, mitochondrial K02258 COX11; cytochrome c oxidase assembly protein subunit 11
D 568423 cox14; cytochrome c oxidase assembly protein COX14 homolog K18181 COX14; cytochrome c oxidase assembly factor 14
D 394181 cox15; cytochrome c oxidase assembly protein COX15 homolog K02259 COX15; heme a synthase [EC:1.17.99.9]
D 550257 cox16; cytochrome c oxidase assembly protein COX16 homolog, mitochondrial K18182 COX16; cytochrome c oxidase assembly protein subunit 16
D 447914 cox17; cytochrome c oxidase copper chaperone K02260 COX17; cytochrome c oxidase assembly protein subunit 17
D 100000948 cox18; cytochrome c oxidase assembly protein COX18, mitochondrial K17797 COX18; mitochondrial inner membrane protein COX18
D 100004173 cox19; cytochrome c oxidase assembly protein COX19 K18183 COX19; cytochrome c oxidase assembly protein subunit 19
D 436985 cox20; cytochrome c oxidase assembly protein COX20, mitochondrial K18184 COX20; cytochrome c oxidase assembly protein subunit 20
D 100330275 mss51; putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51
D 103908684 putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51
D 100334510 pet100; protein PET100 homolog, mitochondrial K18186 PET100; protein PET100, animal type
D 100303756 pet117; protein PET117 homolog, mitochondrial precursor K18188 PET117; protein PET117
D 562963 oxa1l; mitochondrial inner membrane protein OXA1L K03217 yidC; YidC/Oxa1 family membrane protein insertase
D 557970 surf1; surfeit locus protein 1 K14998 SURF1; surfeit locus 1 family protein
D 796572 sco1; protein SCO1 homolog, mitochondrial K07152 SCO1; protein SCO1
D 606683 sco2; protein SCO2 homolog, mitochondrial K23755 SCO2; protein SCO2
D 100534805 translational activator of cytochrome c oxidase 1-like K18189 TACO1; translational activator of cytochrome c oxidase 1
D 570857 taco1; translational activator of cytochrome c oxidase 1 K18189 TACO1; translational activator of cytochrome c oxidase 1
D 557195 lrpprc; leucine-rich PPR motif-containing protein, mitochondrial K17964 LRPPRC; leucine-rich PPR motif-containing protein, mitochondrial
D 798687 coa8; cytochrome c oxidase assembly factor 8 K23506 APOPT1; apoptogenic protein 1
D 100170826 stmp1; short transmembrane mitochondrial protein 1 K27319 STMP1; short transmembrane mitochondrial protein 1
D 100332503 smim4; small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5
D 445200 tmem223; transmembrane protein 223 K27342 TMEM223; transmembrane protein 223
C Complex-V assembly factors
D 550606 atpaf1; ATP synthase mitochondrial F1 complex assembly factor 1 K07555 ATPeAF1; ATP synthase mitochondrial F1 complex assembly factor 1
D 560253 atpaf2; ATP synthase mitochondrial F1 complex assembly factor 2 K07556 ATPeAF2; ATP synthase mitochondrial F1 complex assembly factor 2
D 100002535 tmem70; transmembrane protein 70, mitochondrial K17966 TMEM70; transmembrane protein 70, mitochondrial
D 557217 atp5mj; ATP synthase subunit ATP5MPL, mitochondrial K18193 MP68; 6.8 kDa mitochondrial proteolipid
D 794625 atp5md; ATP synthase membrane subunit DAPIT, mitochondrial K18194 USMG5; up-regulated during skeletal muscle growth protein 5
B Mitochondrial dynamics
C Fission and Fusion factors
D 393620 mfn1b; mitofusin-1b K21356 MFN1; mitofusin 1 [EC:3.6.5.-]
D 567448 mfn2; mitofusin-2 K06030 MFN2; mitofusin 2 [EC:3.6.5.-]
D 492332 opa1; dynamin-like 120 kDa protein, mitochondrial precursor K17079 OPA1; optic atrophy protein 1 [EC:3.6.5.5]
D 497278 opa3; optic atrophy 3 protein homolog K23166 OPA3; optic atrophy 3 protein
D 550367 triap1; TP53-regulated inhibitor of apoptosis 1 K17968 TRIAP1; TRIAP1/MDM35 family protein
D 541485 parla; presenilin-associated rhomboid-like protein A, mitochondrial precursor K09650 PARL; rhomboid-like protein [EC:3.4.21.105]
D 792889 parl; presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105]
D 58081 baxa; BCL2 associated X, apoptosis regulator a K02159 BAX; apoptosis regulator BAX
D 100004321 apoptosis regulator BAX-like K02159 BAX; apoptosis regulator BAX
D 767645 zgc:153993; uncharacterized protein LOC767645 K02159 BAX; apoptosis regulator BAX
D 566871 si:dkey-32e23.4; dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 393896 dnm1l; dynamin-1-like protein K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 797988 fis1; mitochondrial fission 1 protein K17969 FIS1; mitochondrial fission 1 protein
D 100334083 sumo2a; small ubiquitin like modifier 2a K12160 SUMO; small ubiquitin-related modifier
D 406398 sumo3a; small ubiquitin-related modifier 3-like K12160 SUMO; small ubiquitin-related modifier
D 436950 sumo3b; small ubiquitin-related modifier 3 K12160 SUMO; small ubiquitin-related modifier
D 445027 sumo2b; small ubiquitin-related modifier 2 K12160 SUMO; small ubiquitin-related modifier
D 406438 sumo1; small ubiquitin-related modifier 1 K12160 SUMO; small ubiquitin-related modifier
D 792229 sh3glb1a; endophilin-B1a K11248 SH3GLB1; endophilin-B1
D 334911 sh3glb1b; endophilin-B1b K11248 SH3GLB1; endophilin-B1
D 30655 mtch2; mitochondrial carrier homolog 2 K17885 MTCH; mitochondrial carrier
D 393508 mffa; mitochondrial fission factor homolog B K22076 MFF; mitochondrial fission factor
D 553588 mffb; mitochondrial fission factor homolog A K22076 MFF; mitochondrial fission factor
D 100000713 mitochondrial fission factor-like isoform 1 K22076 MFF; mitochondrial fission factor
D 553702 gdap1; ganglioside-induced differentiation-associated protein 1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1
D 562163 gdap1l1; ganglioside-induced differentiation-associated protein 1-like 1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1
D 368752 vat1; synaptic vesicle membrane protein VAT-1 homolog K23167 VAT1; synaptic vesicle membrane protein VAT-1
D 564985 mief1; mitochondrial dynamics protein MID51 K23507 MIEF1_2; mitochondrial dynamics protein MID51/49
D 767710 mief2; mitochondrial dynamics protein MID49 K23507 MIEF1_2; mitochondrial dynamics protein MID51/49
D 567338 pld6; mitochondrial cardiolipin hydrolase K16862 PLD6; mitochondrial cardiolipin hydrolase [EC:3.1.4.-]
D 541431 miga2; mitoguardin 2 K27289 MIGA; mitoguardin
D 450070 miga1; mitoguardin 1 K27289 MIGA; mitoguardin
C Actin cytoskeleton organization
D 57934 actb1; actin, cytoplasmic 1 K05692 ACTB_G1; actin beta/gamma 1
D 57935 actb2; actin, cytoplasmic 2 K05692 ACTB_G1; actin beta/gamma 1
D 541516 naa20; N-alpha-acetyltransferase 20 K17972 NAA20; N-terminal acetyltransferase B complex catalytic subunit [EC:2.3.1.254]
D 568789 naa25; N-alpha-acetyltransferase 25, NatB auxiliary subunit K17973 NAA25; N-terminal acetyltransferase B complex non-catalytic subunit
C Mitochondrial movement
D 321346 phb; prohibitin K17080 PHB1; prohibitin 1
D 324421 phb2a; prohibitin-2a K17081 PHB2; prohibitin 2
D 436954 phb2b; prohibitin-2b K17081 PHB2; prohibitin 2
D 368207 ktn1; kinectin isoform 1 K17975 KTN1; kinectin
C Retention of mitochondria
D 566871 si:dkey-32e23.4; dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 393896 dnm1l; dynamin-1-like protein K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5]
D 562676 myo5c; unconventional myosin-Vc K10357 MYO5; myosin V
D 567402 myo5b; unconventional myosin-Vb K10357 MYO5; myosin V
D 565267 myo5ab; unconventional myosin-Va K10357 MYO5; myosin V
D 562188 myo5aa; unconventional myosin-Va isoform X6 K10357 MYO5; myosin V
D 568760 si:dkey-110c1.10; unconventional myosin-Vb isoform X1 K10357 MYO5; myosin V
D 373108 xiap; E3 ubiquitin-protein ligase XIAP K04725 XIAP; E3 ubiquitin-protein ligase XIAP [EC:2.3.2.27]
D 393317 diabloa; diablo, IAP-binding mitochondrial protein a K10522 DIABLO; diablo
D 570425 diablob; diablo, IAP-binding mitochondrial protein b K10522 DIABLO; diablo
C Morphogenesis factors
D 793657 snx25; sorting nexin-25 K17887 SNX25; sorting nexin-25
D 327143 rhot1a; mitochondrial Rho GTPase 1-A K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 561933 rhot1b; mitochondrial Rho GTPase 1b K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-]
D 327206 immt; MICOS complex subunit MIC60 K17785 IMMT; MICOS complex subunit MIC60
D 393659 mtfp1; mitochondrial fission process protein 1 K17981 MTFP1; mitochondrial fission process protein 1
D 559007 dap3; 28S ribosomal protein S29, mitochondrial K17408 DAP3; small subunit ribosomal protein S29
D 571418 oxr1a; oxidation resistance protein 1a K25437 OXR1; oxidation resistance protein 1
D 570476 oxr1b; oxidation resistance protein 1b K25437 OXR1; oxidation resistance protein 1
D 334306 msto1; protein misato homolog 1 K27320 MSTO1; protein misato
B Mitophagy factors
C Autophagy-related proteins
D 101883461 si:ch73-45o6.2; autophagy-related protein 2 homolog A isoform X1 K17906 ATG2; autophagy-related protein 2
D 336632 atg3; ubiquitin-like-conjugating enzyme ATG3 K08343 ATG3; ubiquitin-like-conjugating enzyme ATG3
D 554140 atg4a; cysteine protease ATG4A K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 415193 atg4c; cysteine protease ATG4C K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 448859 atg4b; cysteine protease ATG4B K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 795933 atg4da; cysteine protease atg4da K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 101884161 cysteine protease ATG4D-like K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-]
D 494180 atg5; autophagy protein 5 K08339 ATG5; autophagy-related protein 5
D 393846 becn1; beclin-1 K08334 BECN; beclin
D 100333016 atg7; LOW QUALITY PROTEIN: ubiquitin-like modifier-activating enzyme ATG7 K08337 ATG7; ubiquitin-like modifier-activating enzyme ATG7
D 403036 gabarapl2; gamma-aminobutyric acid receptor-associated protein-like 2 K08341 GABARAP; GABA(A) receptor-associated protein
D 793200 gabarapb; GABA(A) receptor-associated protein b K08341 GABARAP; GABA(A) receptor-associated protein
D 326974 gabarapa; GABA(A) receptor-associated protein a K08341 GABARAP; GABA(A) receptor-associated protein
D 100000242 zgc:92606; uncharacterized protein LOC100000242 K08341 GABARAP; GABA(A) receptor-associated protein
D 100009663 atg9a; autophagy-related protein 9A K17907 ATG9; autophagy-related protein 9
D 791223 atg9b; autophagy-related protein 9B K17907 ATG9; autophagy-related protein 9
D 641330 atg10; ubiquitin-like-conjugating enzyme ATG10 K17888 ATG10L; ubiquitin-like-conjugating enzyme ATG10
D 570965 atg12; ubiquitin-like protein ATG12 K08336 ATG12; ubiquitin-like protein ATG12
D 407686 atg14; beclin 1-associated autophagy-related key regulator K17889 ATG14L; beclin 1-associated autophagy-related key regulator
D 550552 atg16l1; autophagy-related protein 16-1 K17890 ATG16L1; autophagy-related protein 16-1
D 100034627 atg16l2; autophagy-related protein 16-2 K20868 ATG16L2; autophagy-related protein 16-2
D 100332293 WD repeat domain phosphoinositide-interacting protein 1-like K17908 WIPI1_2; autophagy-related protein 18
D 393362 wipi1; WD repeat domain phosphoinositide-interacting protein 1 K17908 WIPI1_2; autophagy-related protein 18
D 437002 wipi2; WD repeat domain phosphoinositide-interacting protein 2 K17908 WIPI1_2; autophagy-related protein 18
C Parkin-dependent mechanism factors
D 550328 prkn; E3 ubiquitin-protein ligase parkin K04556 PARK2; parkin [EC:2.3.2.31]
D 406837 rnf41; E3 ubiquitin-protein ligase NRDP1 K11981 RNF41; E3 ubiquitin-protein ligase NRDP1 [EC:2.3.2.27]
D 393184 clec16a; protein CLEC16A isoform X1 K19513 CLEC16A; protein CLEC16A
D 494085 pink1; serine/threonine-protein kinase PINK1, mitochondrial K05688 PINK1; PTEN induced putative kinase 1 [EC:2.7.11.1]
D 541485 parla; presenilin-associated rhomboid-like protein A, mitochondrial precursor K09650 PARL; rhomboid-like protein [EC:3.4.21.105]
D 792889 parl; presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105]
D 406452 sqstm1; sequestosome-1 K14381 SQSTM1; sequestosome 1
D 324152 tax1bp1b; tax1-binding protein 1 homolog B K21347 TAX1BP1; Tax1-binding protein 1
D 561219 tax1bp1a; tax1-binding protein 1 homolog A K21347 TAX1BP1; Tax1-binding protein 1
D 553776 calcoco2; calcium-binding and coiled-coil domain-containing protein 2 K21348 CALCOCO2; calcium-binding and coiled-coil domain-containing protein 2
D 100332642 ambra1a; activating molecule in BECN1-regulated autophagy protein 1A K17985 AMBRA1; activating molecule in BECN1-regulated autophagy protein 1
D 559106 ambra1b; activating molecule in BECN1-regulated autophagy protein 1B K17985 AMBRA1; activating molecule in BECN1-regulated autophagy protein 1
C Parkin-independent mechanism factors
D 393405 atg13; autophagy-related protein 13 K08331 ATG13; autophagy-related protein 13
D 558848 ulk1b; serine/threonine-protein kinase ULK1 isoform X1 K21357 ULK1; serine/threonine-protein kinase ULK1 [EC:2.7.11.1]
D 100170793 ulk1a; serine/threonine-protein kinase ULK1a K21357 ULK1; serine/threonine-protein kinase ULK1 [EC:2.7.11.1]
D 100329702 ulk2; serine/threonine-protein kinase ULK2 K08269 ULK2; serine/threonine-protein kinase ULK2 [EC:2.7.11.1]
D 100332174 rb1cc1; RB1-inducible coiled-coil protein 1 K17589 RB1CC1; RB1-inducible coiled-coil protein 1
D 30573 hsp90ab1; heat shock protein HSP 90-beta K04079 HSP90A; molecular chaperone HtpG
D 30591 hsp90aa1.1; heat shock protein HSP 90-alpha 1 K04079 HSP90A; molecular chaperone HtpG
D 565155 hsp90aa1.2; heat shock protein 90, alpha (cytosolic), class A member 1, tandem duplicate 2 K04079 HSP90A; molecular chaperone HtpG
D 394013 cdc37; hsp90 co-chaperone Cdc37 K09554 CDC37; cell division cycle protein 37
D 563633 smurf2; E3 ubiquitin-protein ligase SMURF2 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26]
D 321695 smurf1; E3 ubiquitin-protein ligase SMURF1 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26]
D 554650 bnip3lb; BCL2 interacting protein 3 like b K15465 BNIP3L; BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like
D 323563 bnip3la; BCL2 interacting protein 3 like a K15465 BNIP3L; BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like
D 436984 fundc1; FUN14 domain-containing protein 1 K17986 FUNDC1; FUN14 domain-containing protein 1
C Other mitophagy factors
D 572074 prkaa2; 5'-AMP-activated protein kinase catalytic subunit alpha-2 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 100001198 prkaa1; 5'-AMP-activated protein kinase catalytic subunit alpha-1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31]
D 322425 map1lc3b; microtubule-associated proteins 1A/1B light chain 3B K10435 MAP1LC; microtubule-associated protein 1 light chain
D 393268 map1lc3c; microtubule-associated proteins 1A/1B light chain 3C K10435 MAP1LC; microtubule-associated protein 1 light chain
D 406466 map1lc3a; microtubule-associated proteins 1A/1B light chain 3A K10435 MAP1LC; microtubule-associated protein 1 light chain
D 100330105 map1lc3cl; microtubule-associated proteins 1A/1B light chain 3C-like K10435 MAP1LC; microtubule-associated protein 1 light chain
D 337168 nbr1a; NBR1 autophagy cargo receptor a K17987 NBR1; next to BRCA1 gene 1 protein
D 555713 nbr1b; next to BRCA1 gene 1 protein K17987 NBR1; next to BRCA1 gene 1 protein
D 100151338 tecpr1b; tectonin beta-propeller repeat-containing protein 1 K17988 TECPR1; tectonin beta-propeller repeat-containing protein 1
D 556500 tecpr1a; tectonin beta-propeller repeat-containing protein 1 isoform X2 K17988 TECPR1; tectonin beta-propeller repeat-containing protein 1
D 563140 si:ch211-11n16.2; zinc finger FYVE domain-containing protein 1 isoform X2 K17603 ZFYVE1; zinc finger FYVE domain-containing protein 1
D 100005732 zfyve1; zinc finger FYVE domain-containing protein 1 K17603 ZFYVE1; zinc finger FYVE domain-containing protein 1
D 447838 coasy; bifunctional coenzyme A synthase precursor K02318 COASY; phosphopantetheine adenylyltransferase / dephospho-CoA kinase [EC:2.7.7.3 2.7.1.24]
D 406370 pla2g6; 85/88 kDa calcium-independent phospholipase A2 K16343 PLA2G6; calcium-independent phospholipase A2 [EC:3.1.1.4]
D 550358 zgc:112052; protein C19orf12 homolog K23168 MPAN; protein MPAN
D 100537173 si:ch211-260e23.8; protein C19orf12 homolog K23168 MPAN; protein MPAN
D 100004554 si:ch211-260e23.7; protein C19orf12 homolog K23168 MPAN; protein MPAN
D 447894 zgc:101715; Protein C19orf12 homolog-like K23168 MPAN; protein MPAN
D 792181 fundc2; FUN14 domain-containing protein 2 K24308 FUNDC2; FUN14 domain-containing protein 2
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#[ BRITE | KEGG2 | KEGG ]
#Last updated: March 14, 2024