+D #

  Mitochondrial Biogenesis - Heterocephalus glaber (naked mole-rat)

% ! AMitochondrial DNA transcription, translation, and replication factors B Mitochondrial DNA-encoded proteins C Mitochondrial respiratory chain complex I D 10201222 ND1; NADH dehydrogenase subunit 1 K03878 ND1; NADH-ubiquinone oxidoreductase chain 1 [EC:7.1.1.2] D 10201215 ND2; NADH dehydrogenase subunit 2 K03879 ND2; NADH-ubiquinone oxidoreductase chain 2 [EC:7.1.1.2] D 10201214 ND3; NADH dehydrogenase subunit 3 K03880 ND3; NADH-ubiquinone oxidoreductase chain 3 [EC:7.1.1.2] D 10201219 ND4; NADH dehydrogenase subunit 4 K03881 ND4; NADH-ubiquinone oxidoreductase chain 4 [EC:7.1.1.2] D 10201217 ND4L; NADH dehydrogenase subunit 4L K03882 ND4L; NADH-ubiquinone oxidoreductase chain 4L [EC:7.1.1.2] D 10201218 ND5; NADH dehydrogenase subunit 5 K03883 ND5; NADH-ubiquinone oxidoreductase chain 5 [EC:7.1.1.2] D 10201220 ND6; NADH dehydrogenase subunit 6 K03884 ND6; NADH-ubiquinone oxidoreductase chain 6 [EC:7.1.1.2] C Mitochondrial respiratory chain complex III D 10201221 CYTB; cytochrome b K00412 CYTB; ubiquinol-cytochrome c reductase cytochrome b subunit C Cytochrome c oxidase D 10201216 COX1; cytochrome c oxidase subunit I K02256 COX1; cytochrome c oxidase subunit 1 [EC:7.1.1.9] D 10201212 COX2; cytochrome c oxidase subunit II K02261 COX2; cytochrome c oxidase subunit 2 D 10201210 COX3; cytochrome c oxidase subunit III K02262 COX3; cytochrome c oxidase subunit 3 C F-type ATPase D 10201213 ATP8; ATP synthase F0 subunit 8 K02125 ATPeF08; F-type H+-transporting ATPase subunit 8 D 10201211 ATP6; ATP synthase F0 subunit 6 K02126 ATPeF0A; F-type H+-transporting ATPase subunit a B Mitochondrial transcription and translation factors C Mitochondrial RNA polymerase D 101721232 Polrmt; RNA polymerase mitochondrial K10908 POLRMT; DNA-directed RNA polymerase, mitochondrial [EC:2.7.7.6] C Mitochondrial transcription factors D 101698418 Tfam; transcription factor A, mitochondrial K11830 TFAM; transcription factor A, mitochondrial D 101709903 Tfb1m; transcription factor B1, mitochondrial K15266 TFB1M; dimethyladenosine transferase 1, mitochondrial [EC:2.1.1.-] D 101721509 Tfb2m; transcription factor B2, mitochondrial K17653 TFB2M; dimethyladenosine transferase 2, mitochondrial [EC:2.1.1.-] C Mitochondrial translation factors D 101711400 Mtif2; mitochondrial translational initiation factor 2 K02519 infB; translation initiation factor IF-2 D 101716869 Mtif3; mitochondrial translational initiation factor 3 K02520 infC; translation initiation factor IF-3 D 101700241 Tsfm; Ts translation elongation factor, mitochondrial K02357 tsf; elongation factor Ts D 101717230 Tufm; Tu translation elongation factor, mitochondrial K02358 tuf; elongation factor Tu D 101697641 Gfm1; G elongation factor mitochondrial 1 K02355 fusA; elongation factor G D 101708331 Gfm2; G elongation factor mitochondrial 2 K02355 fusA; elongation factor G D 101721332 Mterf2; mitochondrial transcription termination factor 2 K15031 MTERF; mitochondrial transcription termination factor family protein D 101726599 Mterf1; mitochondrial transcription termination factor 1 K15031 MTERF; mitochondrial transcription termination factor family protein D 101707951 Mterf3; mitochondrial transcription termination factor 3 K15031 MTERF; mitochondrial transcription termination factor family protein D 101712149 Mterf4; mitochondrial transcription termination factor 4 K15031 MTERF; mitochondrial transcription termination factor family protein D 101703247 translation factor Guf1, mitochondrial-like K21594 GUF1; translation factor GUF1, mitochondrial [EC:3.6.5.-] D 101721953 Guf1; GUF1 homolog, GTPase K21594 GUF1; translation factor GUF1, mitochondrial [EC:3.6.5.-] C RNase MRP D 101713471 Pop1; POP1 homolog, ribonuclease P/MRP subunit K01164 POP1; ribonuclease P/MRP protein subunit POP1 [EC:3.1.26.5] D 101709670 Pop4; POP4 homolog, ribonuclease P/MRP subunit K03538 POP4; ribonuclease P protein subunit POP4 [EC:3.1.26.5] D 101725877 Pop5; POP5 homolog, ribonuclease P/MRP subunit K03537 POP5; ribonuclease P/MRP protein subunit POP5 [EC:3.1.26.5] D 101719658 Rpp30; ribonuclease P/MRP subunit p30 K03539 RPP1; ribonuclease P/MRP protein subunit RPP1 [EC:3.1.26.5] D 101710275 Pop7; POP7 homolog, ribonuclease P/MRP subunit K14527 RPP20; ribonuclease P/MRP protein subunit RPP20 [EC:3.1.26.5] D 101705221 Rpp25l; ribonuclease P/MRP subunit p25 like K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5] D 101714753 Rpp25; ribonuclease P/MRP subunit p25 K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5] D 101696941 Rpp38; ribonuclease P/MRP subunit p38 K14523 RPP38; ribonucleases P/MRP protein subunit RPP38 [EC:3.1.26.5] D 101720765 Rpp40; ribonuclease P/MRP subunit p40 K14530 RPP40; ribonucleases P/MRP protein subunit RPP40 [EC:3.1.26.5] C Mitochondrial ribonuclease P D 101720714 Trmt10c; tRNA methyltransferase 10C, mitochondrial RNase P subunit K17654 TRMT10C; mitochondrial ribonuclease P protein 1 [EC:2.1.1.-] D 101717306 mitochondrial ribonuclease P protein 1-like K17654 TRMT10C; mitochondrial ribonuclease P protein 1 [EC:2.1.1.-] D 101712281 Hsd17b10; hydroxysteroid 17-beta dehydrogenase 10 K08683 HSD17B10; 3-hydroxyacyl-CoA dehydrogenase / 3-hydroxy-2-methylbutyryl-CoA dehydrogenase [EC:1.1.1.35 1.1.1.178] D 101704541 Kiaa0391; mitochondrial ribonuclease P protein 3 K17655 MRPP3; mitochondrial ribonuclease P protein 3 D 106007936 mitochondrial ribonuclease P protein 3-like K17655 MRPP3; mitochondrial ribonuclease P protein 3 C Other mitochondrial DNA transcription and translation factors D 101707807 Mss51; MSS51 mitochondrial translational activator K17656 MSS51; mitochondrial splicing suppressor protein 51 D 101720083 Tefm; transcription elongation factor, mitochondrial K17658 TEFM; transcription elongation factor, mitochondrial D 101696935 Ptcd1; pentatricopeptide repeat-containing protein 1, mitochondrial K17710 PTCD1; pentatricopeptide repeat domain-containing protein 1 D 101722330 Ptcd2; pentatricopeptide repeat domain 2 K17711 PTCD2; pentatricopeptide repeat domain-containing protein 2 D 101697820 Ptcd3; pentatricopeptide repeat domain 3 K17659 PTCD3; pentatricopeptide repeat domain-containing protein 3 D 101700443 Dhx30; DExH-box helicase 30 K13185 DHX30; ATP-dependent RNA helicase DHX30 [EC:5.6.2.6] D 101697349 ubiquinol-cytochrome-c reductase complex assembly factor 1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3 D 101699966 Lace1; lactation elevated 1 K18798 AFG1; peroxisome-assembly ATPase [EC:3.6.4.7] D 101696938 Atp23; ATP23 metallopeptidase and ATP synthase assembly factor homolog K18156 ATP23; mitochondrial inner membrane protease ATP23 [EC:3.4.24.-] D 101707930 Supv3l1; Suv3 like RNA helicase K17675 SUPV3L1; ATP-dependent RNA helicase SUPV3L1/SUV3 [EC:5.6.2.6] D 101698932 Lactb2; lactamase beta 2 K16639 LACTB2; endoribonuclease LACTB2 [EC:3.1.27.-] D 101706144 Slc25a4; solute carrier family 25 member 4 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31 D 101698774 Slc25a31; solute carrier family 25 member 31 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31 D 101703823 Slc25a6; solute carrier family 25 member 6 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31 D 101697130 Slc25a5; solute carrier family 25 member 5 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31 D 101714681 Slc25a28; solute carrier family 25 member 28 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37 D 101701717 Slc25a37; solute carrier family 25 member 37 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37 D 101725344 Malsu1; mitochondrial assembly of ribosomal large subunit 1 K25803 MALSU1; mitochondrial assembly of ribosomal large subunit protein 1 D 101719291 Eral1; Era like 12S mitochondrial rRNA chaperone 1 K03595 era; GTPase D 101723833 Yars; tyrosyl-tRNA synthetase K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1] D 101711336 Yars2; tyrosyl-tRNA synthetase 2 K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1] D 101699853 Lars2; leucyl-tRNA synthetase 2, mitochondrial K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4] D 101697750 Lars; leucyl-tRNA synthetase K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4] D 101724449 Dars2; aspartyl-tRNA synthetase 2, mitochondrial K01876 DARS2; aspartyl-tRNA synthetase [EC:6.1.1.12] D 101723530 Gars; glycyl-tRNA synthetase K01880 GARS; glycyl-tRNA synthetase [EC:6.1.1.14] D 101712302 Rars; arginyl-tRNA synthetase K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19] D 101701322 Rars2; arginyl-tRNA synthetase 2, mitochondrial K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19] D 101706522 Qrsl1; glutaminyl-tRNA synthase (glutamine-hydrolyzing)-like 1 K02433 gatA; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit A [EC:6.3.5.6 6.3.5.7] D 101715571 Gatb; glutamyl-tRNA amidotransferase subunit B K02434 gatB; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit B [EC:6.3.5.6 6.3.5.7] D 101696840 Gatc; glutamyl-tRNA amidotransferase subunit C K02435 gatC; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit C [EC:6.3.5.6 6.3.5.7] D 101711487 Mtpap; mitochondrial poly(A) polymerase K18060 MTPAP; poly(A) RNA polymerase, mitochondrial [EC:2.7.7.19] D 101710298 Pde12; phosphodiesterase 12 K19612 PDE12; 2',5'-phosphodiesterase [EC:3.1.13.4 3.1.4.-] D 101726455 Mtg1; mitochondrial ribosome associated GTPase 1 K19828 MTG1; mitochondrial GTPase 1 D 101718562 Noa1; nitric oxide associated 1 K19832 NOA1; nitric oxide-associated protein 1 D 101724598 Nsun3; NOP2/Sun RNA methyltransferase family member 3 K21969 NSUN3; tRNA (cytosine34-C5)-methyltransferase [EC:2.1.1.-] D 101721265 Nsun4; NOP2/Sun RNA methyltransferase family member 4 K21970 NSUN4; 5-methylcytosine rRNA methyltransferase NSUN4 [EC:2.1.1.-] D 101698887 Rpusd3; RNA pseudouridylate synthase domain containing 3 K22537 RPUSD3; mitochondrial RNA pseudouridine synthase RPUSD3 [EC:5.4.99.-] D 101711493 Rpusd4; RNA pseudouridylate synthase domain containing 4 K22538 RPUSD4; mitochondrial RNA pseudouridine synthase RPUSD4 [EC:5.4.99.-] D 101720236 Rcc1l; RCC1 like K23495 RCC1L; RCC1-like G exchanging factor-like protein D 101712392 Ngrn; neugrin, neurite outgrowth associated K23496 NGRN; neugrin D 101697242 Trub2; TruB pseudouridine synthase family member 2 K23497 TRUB2; mitochondrial mRNA pseudouridine synthase TRUB2 [EC:5.4.99.-] D 101714635 Fastkd2; FAST kinase domains 2 K18190 FASTKD2; FAST kinase domain-containing protein 2 D 101720631 chromosome unknown open reading frame, human C12orf65 K23498 COXPD7; peptide chain release factor D 106010192 probable peptide chain release factor C12orf65 homolog, mitochondrial K23498 COXPD7; peptide chain release factor D 101716672 Rmnd1; required for meiotic nuclear division 1 homolog K23499 RMND1; required for meiotic nuclear division protein 1 D 101720791 Grsf1; G-rich RNA sequence binding factor 1 K24984 GRSF1; G-rich sequence factor 1 D 101705663 Mettl15; methyltransferase like 15 K25876 METTL15; 12S rRNA N4-methylcytidine (m4C) methyltransferase [EC:2.1.1.-] D 101725428 chromosome unknown open reading frame, human C12orf10 K25877 MYG1; MYG1 exonuclease [EC:3.1.-.-] D 101704011 chromosome unknown open reading frame, human C6orf203 K26186 MTRES1; mitochondrial transcription rescue factor 1 B Mitochondrial DNA replication factors C Mitochondrial DNA polymerase D 101700433 Polg; DNA polymerase gamma, catalytic subunit K02332 POLG; DNA polymerase gamma 1 [EC:2.7.7.7] D 101705657 Polg2; DNA polymerase gamma 2, accessory subunit K02333 POLG2; DNA polymerase gamma 2 D 101703853 Primpol; primase and DNA directed polymerase K22761 PRIMPOL; DNA-directed primase/polymerase protein [EC:2.7.7.102 2.7.7.7] C Mitochondrial DNA maintenance factors D 101717186 Endog; endonuclease G K01173 ENDOG; endonuclease G, mitochondrial D 101713650 Mgme1; mitochondrial genome maintenance exonuclease 1 K19465 MGME1; mitochondrial genome maintenance exonuclease 1 [EC:3.1.-.-] D 101710473 Exog; exo/endonuclease G K15050 EXOG; nuclease EXOG, mitochondrial D 101719932 Twnk; twinkle mtDNA helicase K17680 PEO1; twinkle protein [EC:5.6.2.3] D 101700455 Pif1; PIF1 5'-to-3' DNA helicase K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3] C Other Mitochondrial DNA replication factors D 101707844 Ssbp1; single stranded DNA binding protein 1 K03111 ssb; single-strand DNA-binding protein D 101709814 Atad3a; ATPase family AAA domain-containing protein 3 K17681 ATAD3A_B; ATPase family AAA domain-containing protein 3A/B D 101706352 Mnf1; ubiquinol-cytochrome-c reductase complex assembly factor 2 K17682 MNF1; mitochondrial nucleoid factor 1 # AMitochondrial protein import machinery B Endoplasmic reticulum membrane and cytosol C ER-mitochondria encounter structure (ERMES) complex C Other ER-memrane and cytosol factors D 101699482 Dnaja2; DnaJ heat shock protein family (Hsp40) member A2 K09503 DNAJA2; DnaJ homolog subfamily A member 2 D 101704036 Tomm34; translocase of outer mitochondrial membrane 34 K17766 TOM34; mitochondrial import receptor subunit TOM34 D 101713608 mitochondrial Rho GTPase 1-like K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-] D 101723834 Rhot1; ras homolog family member T1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-] D 101699805 Hspa1l; heat shock 70 kDa protein 1-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 101700637 heat shock 70 kDa protein 1B K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 101701238 Hspa6; heat shock protein family A (Hsp70) member 6 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 101708313 Hspa8; heat shock protein family A (Hsp70) member 8 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 101700666 Aip; aryl hydrocarbon receptor interacting protein K17767 AIP; AH receptor-interacting protein D 101707637 Aipl1; aryl hydrocarbon receptor interacting protein like 1 K17767 AIP; AH receptor-interacting protein B Outer membrane C Transporter outer membrane (TOM) complex D 101716859 Tomm40; translocase of outer mitochondrial membrane 40 K11518 TOM40; mitochondrial import receptor subunit TOM40 D 101699629 Tomm40l; translocase of outer mitochondrial membrane 40 like K11518 TOM40; mitochondrial import receptor subunit TOM40 D 101714783 Tomm70; translocase of outer mitochondrial membrane 70 K17768 TOM70; mitochondrial import receptor subunit TOM70 D 101704532 Tomm22; translocase of outer mitochondrial membrane 22 K17769 TOM22; mitochondrial import receptor subunit TOM22 D 101699852 Tomm20; translocase of outer mitochondrial membrane 20 K17770 TOM20; mitochondrial import receptor subunit TOM20 D 101699993 Tomm7; translocase of outer mitochondrial membrane 7 K17771 TOM7; mitochondrial import receptor subunit TOM7 D 101710551 Tomm6; translocase of outer mitochondrial membrane 6 K17772 TOM6; mitochondrial import receptor subunit TOM6 D 101705195 Tomm5; translocase of outer mitochondrial membrane 5 K17773 TOM5; mitochondrial import receptor subunit TOM5 C TOB/SAM complex D 101716589 Samm50; SAMM50 sorting and assembly machinery component K07277 SAM50; outer membrane protein insertion porin family C Porin D 101708247 Vdac1; voltage dependent anion channel 1 K05862 VDAC1; voltage-dependent anion channel protein 1 D 101723570 Vdac2; voltage dependent anion channel 2 K15040 VDAC2; voltage-dependent anion channel protein 2 D 101709540 Vdac3; voltage dependent anion channel 3 K15041 VDAC3; voltage-dependent anion channel protein 3 C ERMES complex C Other outer membrane factor D 101725669 Mtx3; metaxin 3 K17776 MTX; metaxin D 101703494 Mtx1; metaxin 1 K17776 MTX; metaxin D 101725461 Mtx2; metaxin 2 K17776 MTX; metaxin D 101701500 Myo19; myosin XIX K25838 MYO19; myosin XIX D 101697912 armadillo repeat-containing X-linked protein 1 K26187 ARMCX1; armadillo repeat-containing X-linked protein 1 D 101711429 Armcx1; armadillo repeat containing, X-linked 1 K26187 ARMCX1; armadillo repeat-containing X-linked protein 1 D 101709635 Armcx2; armadillo repeat containing, X-linked 2 K26188 ARMCX2; armadillo repeat-containing X-linked protein 2 D 101710702 Armcx3; armadillo repeat containing, X-linked 3 K26189 ARMCX3; armadillo repeat-containing X-linked protein 3 D 101711055 Armcx6; armadillo repeat containing, X-linked 6 K26190 ARMCX6; armadillo repeat-containing X-linked protein 6 D 101712958 Marc2; mitochondrial amidoxime reducing component 2 K27318 MTARC; mitochondrial amidoxime-reducing component [EC:1.7.-.-] D 101713580 Marc1; mitochondrial amidoxime reducing component 1 K27318 MTARC; mitochondrial amidoxime-reducing component [EC:1.7.-.-] B Inter membrane space C Transporter inner membrane (TIM) 9/10 complex D 101725619 mitochondrial import inner membrane translocase subunit Tim9-like K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9 D 106009015 mitochondrial import inner membrane translocase subunit Tim9-like K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9 D 101698915 mitochondrial import inner membrane translocase subunit Tim9-like K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9 D 101706790 mitochondrial import inner membrane translocase subunit Tim9-like K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9 D 101701715 mitochondrial import inner membrane translocase subunit Tim9-like K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9 D 101723606 mitochondrial import inner membrane translocase subunit Tim9-like K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9 D 101716864 mitochondrial import inner membrane translocase subunit Tim9-like K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9 D 101720208 mitochondrial import inner membrane translocase subunit Tim9-like K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9 D 101717150 mitochondrial import inner membrane translocase subunit Tim9-like K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9 D 101720275 mitochondrial import inner membrane translocase subunit Tim9-like K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9 D 101705604 mitochondrial import inner membrane translocase subunit Tim9-like K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9 D 106010944 mitochondrial import inner membrane translocase subunit Tim9-like K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9 D 101706496 Timm9; translocase of inner mitochondrial membrane 9 K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9 D 101707007 mitochondrial import inner membrane translocase subunit Tim9-like K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9 D 106008757 mitochondrial import inner membrane translocase subunit Tim9-like K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9 D 101726401 Timm10; translocase of inner mitochondrial membrane 10 K17778 TIM10; mitochondrial import inner membrane translocase subunit TIM10 D 101704644 Timm10b; translocase of inner mitochondrial membrane 10B K17779 TIM10B; mitochondrial import inner membrane translocase subunit TIM10B C TIM8/13 complex D 101700068 mitochondrial import inner membrane translocase subunit Tim8 A K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8 D 101701661 Timm8b; translocase of inner mitochondrial membrane 8 homolog B K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8 D 101715600 Timm8a; translocase of inner mitochondrial membrane 8 homolog A (yeast) K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8 D 101717605 mitochondrial import inner membrane translocase subunit Tim8 A K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8 D 101699941 mitochondrial import inner membrane translocase subunit Tim8 A K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8 D 101702512 mitochondrial import inner membrane translocase subunit Tim13 K17781 TIM13; mitochondrial import inner membrane translocase subunit TIM13 D 101707329 Timm13; translocase of inner mitochondrial membrane 13 K17781 TIM13; mitochondrial import inner membrane translocase subunit TIM13 C Mitochondrial intermembrane space assembly (MIA) complex D 101709269 Chchd4; coiled-coil-helix-coiled-coil-helix domain containing 4 K17782 MIA40; mitochondrial intermembrane space import and assembly protein 40 D 101721514 Gfer; growth factor, augmenter of liver regeneration K17783 ERV1; mitochondrial FAD-linked sulfhydryl oxidase [EC:1.8.3.2] B Inner mambrane C MICOS complex D 101707836 Minos1; mitochondrial inner membrane organizing system 1 K17784 MICOS10; MICOS complex subunit MIC10 D 101726109 Immt; inner membrane mitochondrial protein K17785 IMMT; MICOS complex subunit MIC60 D 101711280 chromosome unknown open reading frame, human C19orf70 K24624 MICOS13; MICOS complex subunit MIC13 D 101722598 Chchd3; coiled-coil-helix-coiled-coil-helix domain containing 3 K17563 CHCHD3; MICOS complex subunit MIC19 D 101697996 Chchd6; coiled-coil-helix-coiled-coil-helix domain containing 6 K17564 CHCHD6; MICOS complex subunit MIC25 D 101696400 Apoo; apolipoprotein O K24625 APOO; MICOS complex subunit MIC26 D 101701262 Apool; apolipoprotein O like K24626 APOOL; MICOS complex subunit MIC27 C MICOS complex (yeast) D 101707836 Minos1; mitochondrial inner membrane organizing system 1 K17784 MICOS10; MICOS complex subunit MIC10 D 101726109 Immt; inner membrane mitochondrial protein K17785 IMMT; MICOS complex subunit MIC60 C TIM22 complex D 101710728 Timm22; translocase of inner mitochondrial membrane 22 K17790 TIM22; mitochondrial import inner membrane translocase subunit TIM22 C TIM23 complex D 101708805 Timm23b; translocase of inner mitochondrial membrane 23 homolog B K17794 TIM23; mitochondrial import inner membrane translocase subunit TIM23 D 101710584 Timm17b; translocase of inner mitochondrial membrane 17 homolog B (yeast) K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17 D 101717832 Timm17a; translocase of inner mitochondrial membrane 17 homolog A (yeast) K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17 D 101712569 Timm21; translocase of inner mitochondrial membrane 21 K17796 TIM21; mitochondrial import inner membrane translocase subunit TIM21 D 101725971 Timm50; translocase of inner mitochondrial membrane 50 K17496 TIM50; mitochondrial import inner membrane translocase subunit TIM50 C Mitochondrial calcium uniporter complex D 101700272 Mcu; mitochondrial calcium uniporter K20858 MCU; calcium uniporter protein, mitochondrial D 101699193 Micu1; mitochondrial calcium uptake 1 K22827 MICU1; calcium uptake protein 1, mitochondrial D 101702226 Micu2; mitochondrial calcium uptake 2 K22828 MICU2; calcium uptake protein 2, mitochondrial D 101706115 Mcub; mitochondrial calcium uniporter dominant negative beta subunit K22829 MCUB; calcium uniporter regulatory subunit MCUb, mitochondrial D 101725774 Smdt1; single-pass membrane protein with aspartate rich tail 1 K22830 SMDT1; essential MCU regulator, mitochondrial D 101718201 Mcur1; mitochondrial calcium uniporter regulator 1 K22137 MCUR1; mitochondrial calcium uniporter regulator 1 C Other inner membrane factors D 101710555 Letm1; leucine zipper and EF-hand containing transmembrane protein 1 K17800 LETM1; LETM1 and EF-hand domain-containing protein 1, mitochondrial D 101709166 Immp1l; inner mitochondrial membrane peptidase subunit 1 K09647 IMP1; mitochondrial inner membrane protease subunit 1 [EC:3.4.21.-] D 101722832 Immp2l; inner mitochondrial membrane peptidase subunit 2 K09648 IMP2; mitochondrial inner membrane protease subunit 2 [EC:3.4.21.-] D 101710322 Tmem126a; transmembrane protein 126A K18157 TMEM126A; transmembrane protein 126A D 101703138 Mpc1l; mitochondrial pyruvate carrier 1-like K22138 MPC1; mitochondrial pyruvate carrier 1 D 101709554 Mpc1; mitochondrial pyruvate carrier 1 K22138 MPC1; mitochondrial pyruvate carrier 1 D 101726246 Mpc2; mitochondrial pyruvate carrier 2 K22139 MPC2; mitochondrial pyruvate carrier 2 D 101700511 Chchd10; coiled-coil-helix-coiled-coil-helix domain containing 10 K22759 CHCHD10; coiled-coil-helix-coiled-coil-helix domain-containing protein 10 B Matrix C MMC/PAM proteins D 101713213 Timm44; translocase of inner mitochondrial membrane 44 K17804 TIM44; mitochondrial import inner membrane translocase subunit TIM44 D 101715170 Hspa9; heat shock protein family A (Hsp70) member 9 K04043 dnaK; molecular chaperone DnaK D 101716240 Grpel1; GrpE like 1, mitochondrial K03687 GRPE; molecular chaperone GrpE D 101713615 Grpel2; GrpE like 2, mitochondrial K03687 GRPE; molecular chaperone GrpE D 101722454 Dnajc19; DnaJ heat shock protein family (Hsp40) member C19 K09539 DNAJC19; DnaJ homolog subfamily C member 19 C Other matrix factors D 101701124 Pmpca; peptidase, mitochondrial processing alpha subunit K01412 PMPCA; mitochondrial-processing peptidase subunit alpha [EC:3.4.24.64] D 101721772 Pmpcb; peptidase, mitochondrial processing beta subunit K17732 PMPCB; mitochondrial-processing peptidase subunit beta [EC:3.4.24.64] D 101696293 Mipep; mitochondrial intermediate peptidase K01410 MIPEP; mitochondrial intermediate peptidase [EC:3.4.24.59] D 101706498 Hspd1; heat shock protein family D (Hsp60) member 1 K04077 groEL; chaperonin GroEL [EC:5.6.1.7] D 101720637 Dnaja3; DnaJ heat shock protein family (Hsp40) member A3 K09504 DNAJA3; DnaJ homolog subfamily A member 3 D 101712188 Tamm41; TAM41 mitochondrial translocator assembly and maintenance homolog K17807 TAM41; mitochondrial translocator assembly and maintenance protein 41 D 106009788 Dnlz; DNL-type zinc finger K17808 ZIM17; mitochondrial protein import protein ZIM17 D 101700567 Ethe1; ETHE1, persulfide dioxygenase K17725 ETHE1; sulfur dioxygenase [EC:1.13.11.18] D 101704391 Poldip2; DNA polymerase delta interacting protein 2 K17809 POLDIP2; polymerase delta-interacting protein 2 # AMitochondrial quality control factors B Regulator of mitochondrial biogenesis C Ubiquitas transcription factors D 101712503 Creb1; cAMP responsive element binding protein 1 K05870 CREB1; cyclic AMP-responsive element-binding protein 1 D 101697641 Gfm1; G elongation factor mitochondrial 1 K02355 fusA; elongation factor G D 101708331 Gfm2; G elongation factor mitochondrial 2 K02355 fusA; elongation factor G D 101697506 Sp1; Sp1 transcription factor K04684 SP1; transcription factor Sp1 D 101705706 Yy1; YY1 transcription factor K09201 YY; transcription factor YY D 101721965 transcriptional repressor protein YY1 K09201 YY; transcription factor YY D 106007838 Yy2; YY2 transcription factor K09201 YY; transcription factor YY D 101711074 Gabpb1; GA binding protein transcription factor beta subunit 1 K09454 GABPB; GA-binding protein transcription factor, beta D 101708800 Gabpb2; GA binding protein transcription factor beta subunit 2 K09454 GABPB; GA-binding protein transcription factor, beta D 101698418 Tfam; transcription factor A, mitochondrial K11830 TFAM; transcription factor A, mitochondrial C Nuclear respiratory factors D 101703414 Nrf1; nuclear respiratory factor 1 K11831 NRF1; nuclear respiratory factor 1 D 101698153 Nfe2l2; nuclear factor, erythroid 2 like 2 K05638 NFE2L2; nuclear factor erythroid 2-related factor 2 D 101701172 metallothionein-1E K14739 MT1_2; metallothionein 1/2 D 101701546 Mt1e; metallothionein 1E K14739 MT1_2; metallothionein 1/2 D 101705074 Mt4; metallothionein 4 K14741 MT4; metallothionein 4 C Coactivators D 101703716 Ppargc1a; PPARG coactivator 1 alpha K07202 PPARGC1A; alpha peroxisome proliferator-activated receptor gamma coactivator 1-alpha D 101717446 Ppargc1b; PPARG coactivator 1 beta K17962 PPARGC1B; peroxisome proliferator-activated receptor gamma coactivator 1-beta D 101707931 Pprc1; peroxisome proliferator-activated receptor gamma, coactivator-related 1 K17963 PPRC1; peroxisome proliferator-activated receptor gamma coactivator-related protein 1 D 101702435 Crtc1; CREB regulated transcription coactivator 1 K15309 CRTC1; CREB-regulated transcription coactivator 1 D 101711512 Ep300; E1A binding protein p300 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48] D 101714025 Crebbp; CREB binding protein K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48] C Proteins involved in Fe-S cluster biogenesis D 101724186 Nfs1; NFS1, cysteine desulfurase K04487 iscS; cysteine desulfurase [EC:2.8.1.7] D 101713201 Iscu; iron-sulfur cluster assembly enzyme K22068 ISCU; iron-sulfur cluster assembly enzyme ISCU, mitochondrial D 101719586 Lyrm4; LYR motif containing 4 K22069 LYRM4; LYR motif-containing protein 4 D 101724952 Fxn; frataxin K19054 FXN; frataxin [EC:1.16.3.1] D 106010403 Fdx1; ferredoxin 1 K22070 FDX1; ferredoxin-1, mitochondrial D 101714715 Fdx1l; ferredoxin 1 like K22071 FDX2; ferredoxin-2, mitochondrial D 101700719 Fdxr; ferredoxin reductase K18914 FDXR; adrenodoxin-NADP+ reductase [EC:1.18.1.6] D 101715170 Hspa9; heat shock protein family A (Hsp70) member 9 K04043 dnaK; molecular chaperone DnaK D 101722394 Hscb; HscB mitochondrial iron-sulfur cluster cochaperone K04082 hscB; molecular chaperone HscB D 101700419 iron-sulfur cluster co-chaperone protein HscB, mitochondrial-like K04082 hscB; molecular chaperone HscB D 101716450 Sil1; SIL1 nucleotide exchange factor K14001 SIL1; nucleotide exchange factor SIL1 D 101722704 Glrx5; glutaredoxin 5 K07390 grxD; monothiol glutaredoxin D 101697806 Isca1; iron-sulfur cluster assembly 1 K22063 ISCA1; iron-sulfur cluster assembly 1 D 101700464 Isca2; iron-sulfur cluster assembly 2 K22072 ISCA2; iron-sulfur cluster assembly 2 D 101719992 Iba57; IBA57 homolog, iron-sulfur cluster assembly K22073 IBA57; transferase CAF17, mitochondrial [EC:2.1.-.-] D 101700550 Nfu1; NFU1 iron-sulfur cluster scaffold K22074 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial D 101710835 Bola1; bolA family member 1 K22066 BOLA1; BolA-like protein 1 D 101706962 Bola3; bolA family member 3 K22075 BOLA3; BolA-like protein 3 D 101719287 Sfxn1; sideroflexin 1 K23500 SFXN1_3; sideroflexin-1/3 D 101724056 Sfxn3; sideroflexin 3 K23500 SFXN1_3; sideroflexin-1/3 D 101696968 Sfxn2; sideroflexin 2 K23501 SFXN2; sideroflexin-2 D 101710443 Sfxn5; sideroflexin 5 K23503 SFXN5; sideroflexin-5 C Other regulator of mitochondrial biogenesis D 101716055 Cpt1a; carnitine palmitoyltransferase 1A K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21] D 101724285 Cpt1b; carnitine palmitoyltransferase 1B K19523 CPT1B; carnitine O-palmitoyltransferase 1, muscle isoform [EC:2.3.1.21] D 101719936 Cpt1c; carnitine palmitoyltransferase 1C K19524 CPT1C; carnitine O-palmitoyltransferase 1, brain isoform [EC:2.3.1.21] D 101721202 Dhtkd1; dehydrogenase E1 and transketolase domain containing 1 K15791 DHKTD1; 2-oxoadipate dehydrogenase E1 component [EC:1.2.4.-] D 101717262 Fbxl4; F-box and leucine rich repeat protein 4 K10270 FBXL4; F-box and leucine-rich repeat protein 4 D 101697902 Hcfc1; host cell factor C1 K14966 HCFC1; host cell factor 1 D 101701605 Hcfc2; host cell factor C2 K27390 HCFC2; host cell factor 2 D 101697599 Htt; huntingtin K04533 HD; huntingtin D 101725053 Esrra; estrogen related receptor alpha K08552 NR3B1; estrogen-related receptor alpha D 101711089 Esrrb; estrogen related receptor beta K08553 NR3B2; estrogen-related receptor beta D 101704198 estrogen-related receptor gamma-like K08554 NR3B3; estrogen-related receptor gamma D 101705764 Esrrg; estrogen related receptor gamma K08554 NR3B3; estrogen-related receptor gamma D 101713774 Nrip1; nuclear receptor interacting protein 1 K17965 NRIP1; nuclear receptor-interacting protein 1 D 101698482 Prkaa2; protein kinase AMP-activated catalytic subunit alpha 2 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31] D 101722998 Prkaa1; protein kinase AMP-activated catalytic subunit alpha 1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31] D 101710908 Lonp1; lon peptidase 1, mitochondrial K08675 PRSS15; ATP-dependent Lon protease [EC:3.4.21.53] D 101720282 Sirt1; sirtuin 1 K11411 SIRT1; NAD-dependent protein deacetylase sirtuin 1 [EC:2.3.1.286] D 101700820 Serac1; serine active site containing 1 K23504 SERAC1; protein SERAC1 D 101725948 Uxt; ubiquitously expressed prefoldin like chaperone K26537 UXT; protein UXT D 101696347 Perm1; PPARGC1 and ESRR induced regulator, muscle 1 K26738 PERM1; PGC-1 and ERR-induced regulator in muscle protein 1 B Mitochondrial respiratory chain complex assembly factors C Complex-I assembly factors D 101724974 Ndufaf1; NADH:ubiquinone oxidoreductase complex assembly factor 1 K18159 NDUFAF1; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 1 D 101724515 Ndufaf2; NADH:ubiquinone oxidoreductase complex assembly factor 2 K18160 NDUFAF2; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2 D 101699477 Ndufaf3; NADH:ubiquinone oxidoreductase complex assembly factor 3 K09008 NDUFAF3; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3 D 101704407 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4-like K18161 NDUFAF4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4 D 101710036 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4-like K18161 NDUFAF4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4 D 101720511 Ndufaf4; NADH:ubiquinone oxidoreductase complex assembly factor 4 K18161 NDUFAF4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4 D 101704983 Ndufaf5; NADH:ubiquinone oxidoreductase complex assembly factor 5 K18162 NDUFAF5; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 5 [EC:2.1.1.-] D 101697719 NADH dehydrogenase (ubiquinone) complex I, assembly factor 6-like K18163 NDUFAF6; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 6 D 101709514 Ndufaf6; NADH:ubiquinone oxidoreductase complex assembly factor 6 K18163 NDUFAF6; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 6 D 101697184 Ndufaf7; NADH:ubiquinone oxidoreductase complex assembly factor 7 K18164 NDUFAF7; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 7 D 101699285 Ndufaf8; NADH:ubiquinone oxidoreductase complex assembly factor 8 K24726 NDUFAF8; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 8 D 101711031 Tmem126b; transmembrane protein 126B K18165 TMEM126B; complex I assembly factor TMEM126B D 101706998 complex I assembly factor TMEM126B, mitochondrial-like K18165 TMEM126B; complex I assembly factor TMEM126B D 106007788 complex I assembly factor TMEM126B, mitochondrial-like K18165 TMEM126B; complex I assembly factor TMEM126B D 101716127 Ecsit; ECSIT signalling integrator K04405 ECSIT; evolutionarily conserved signaling intermediate in Toll pathway D 101698399 Acad9; acyl-CoA dehydrogenase family member 9, mitochondrial K15980 ACAD9; acyl-CoA dehydrogenase family member 9 [EC:1.3.99.-] D 101720553 acyl-CoA dehydrogenase family member 9, mitochondrial-like K15980 ACAD9; acyl-CoA dehydrogenase family member 9 [EC:1.3.99.-] D 101697814 Nubpl; nucleotide binding protein like K03593 mrp; ATP-binding protein involved in chromosome partitioning D 101714249 Foxred1; FAD dependent oxidoreductase domain containing 1 K18166 FOXRED1; FAD-dependent oxidoreductase domain-containing protein 1 D 101705574 Rtn4ip1; reticulon 4 interacting protein 1 K23164 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial D 101706057 Timmdc1; translocase of inner mitochondrial membrane domain containing 1 K23505 TIMMDC1; complex I assembly factor TIMMDC1 C Complex-II assembly factors D 101708716 Sdhaf1; succinate dehydrogenase complex assembly factor 1 K18167 SDHAF1; succinate dehydrogenase assembly factor 1 D 101705940 Sdhaf2; succinate dehydrogenase complex assembly factor 2 K18168 SDHAF2; succinate dehydrogenase assembly factor 2 C Complex-III assembly factors D 101703804 mitochondrial chaperone BCS1 K08900 BCS1; mitochondrial chaperone BCS1 D 101708781 Ttc19; tetratricopeptide repeat domain 19 K18169 TTC19; tetratricopeptide repeat protein 19, mitochondrial D 101700105 Lyrm7; LYR motif containing 7 K18170 LYRM7; complex III assembly factor LYRM7 D 101697349 ubiquinol-cytochrome-c reductase complex assembly factor 1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3 D 101706352 Mnf1; ubiquinol-cytochrome-c reductase complex assembly factor 2 K17682 MNF1; mitochondrial nucleoid factor 1 D 101724106 ubiquinol-cytochrome-c reductase complex assembly factor 3 K23165 UQCC3; ubiquinol-cytochrome-c reductase complex assembly factor 3 D 101718821 chromosome unknown open reading frame, human C16orf91 K27339 UQCC4; ubiquinol-cytochrome c reductase complex assembly factor 4 D 101699795 Smim4; small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5 D 101703807 chromosome unknown open reading frame, human C12orf73 K27341 UQCC6; ubiquinol-cytochrome c reductase complex assembly factor 6 D 101712858 chromosome unknown open reading frame, human C7orf73 K27319 STMP1; short transmembrane mitochondrial protein 1 C Complex-IV assembly factors D 101702589 Cmc1; C-X9-C motif containing 1 K18171 CMC1; COX assembly mitochondrial protein 1 D 101725751 Cmc2; C-X9-C motif containing 2 K18172 CMC2; COX assembly mitochondrial protein 2 D 101707497 cytochrome c oxidase assembly factor 1 homolog K18173 COA1; cytochrome c oxidase assembly factor 1 D 101712798 cytochrome c oxidase assembly factor 3 homolog, mitochondrial K18175 CCDC56; cytochrome c oxidase assembly factor 3, animal type D 101715323 cytochrome c oxidase assembly factor 4 homolog, mitochondrial K18177 COA4; cytochrome c oxidase assembly factor 4 D 101718187 cytochrome c oxidase assembly factor 5 K18178 COA5; cytochrome c oxidase assembly factor 5 D 101702099 cytochrome c oxidase assembly factor 6 homolog K18179 COA6; cytochrome c oxidase assembly factor 6 D 101708769 Selrc1; cytochrome c oxidase assembly factor 7 K18180 COA7; cytochrome c oxidase assembly factor 7 D 101726271 protoheme IX farnesyltransferase, mitochondrial K02257 COX10; heme o synthase [EC:2.5.1.141] D 101700350 cytochrome c oxidase assembly protein COX11, mitochondrial K02258 COX11; cytochrome c oxidase assembly protein subunit 11 D 101701927 cytochrome c oxidase assembly protein COX14 K18181 COX14; cytochrome c oxidase assembly factor 14 D 101715399 cytochrome c oxidase assembly protein COX15 homolog K02259 COX15; heme a synthase [EC:1.17.99.9] D 101698905 cytochrome c oxidase assembly protein COX16 homolog, mitochondrial K18182 COX16; cytochrome c oxidase assembly protein subunit 16 D 101702679 cytochrome c oxidase copper chaperone K02260 COX17; cytochrome c oxidase assembly protein subunit 17 D 101726570 mitochondrial inner membrane protein COX18 K17797 COX18; mitochondrial inner membrane protein COX18 D 101702478 cytochrome c oxidase assembly protein COX19 K18183 COX19; cytochrome c oxidase assembly protein subunit 19 D 101726175 cytochrome c oxidase protein 20 homolog K18184 COX20; cytochrome c oxidase assembly protein subunit 20 D 101707807 Mss51; MSS51 mitochondrial translational activator K17656 MSS51; mitochondrial splicing suppressor protein 51 D 101701469 Pet100; PET100 homolog K18186 PET100; protein PET100, animal type D 101715522 Pet117; PET117 homolog K18188 PET117; protein PET117 D 101725503 Oxa1l; OXA1L, mitochondrial inner membrane protein K03217 yidC; YidC/Oxa1 family membrane protein insertase D 101710326 Surf1; surfeit 1 K14998 SURF1; surfeit locus 1 family protein D 101701770 protein SCO1 homolog, mitochondrial K07152 SCO1; protein SCO1 D 106007592 protein SCO2 homolog, mitochondrial K23755 SCO2; protein SCO2 D 101703967 translational activator of cytochrome c oxidase 1 K18189 TACO1; translational activator of cytochrome c oxidase 1 D 101724140 Lrpprc; leucine rich pentatricopeptide repeat containing K17964 LRPPRC; leucine-rich PPR motif-containing protein, mitochondrial D 101710003 Apopt1; apoptogenic 1, mitochondrial K23506 APOPT1; apoptogenic protein 1 D 101712858 chromosome unknown open reading frame, human C7orf73 K27319 STMP1; short transmembrane mitochondrial protein 1 D 101699795 Smim4; small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5 D 101697899 Tmem223; transmembrane protein 223 K27342 TMEM223; transmembrane protein 223 C Complex-V assembly factors D 101724337 Atpaf1; ATP synthase mitochondrial F1 complex assembly factor 1 K07555 ATPeAF1; ATP synthase mitochondrial F1 complex assembly factor 1 D 101700646 Atpaf2; ATP synthase mitochondrial F1 complex assembly factor 2 K07556 ATPeAF2; ATP synthase mitochondrial F1 complex assembly factor 2 D 101723313 Tmem70; transmembrane protein 70 K17966 TMEM70; transmembrane protein 70, mitochondrial D 101712319 6.8 kDa mitochondrial proteolipid-like K18193 MP68; 6.8 kDa mitochondrial proteolipid D 101723331 6.8 kDa mitochondrial proteolipid-like K18193 MP68; 6.8 kDa mitochondrial proteolipid D 101707999 chromosome unknown open reading frame, human C14orf2 K18193 MP68; 6.8 kDa mitochondrial proteolipid D 101701875 6.8 kDa mitochondrial proteolipid-like K18193 MP68; 6.8 kDa mitochondrial proteolipid D 101699300 up-regulated during skeletal muscle growth protein 5 K18194 USMG5; up-regulated during skeletal muscle growth protein 5 D 101703467 Usmg5; up-regulated during skeletal muscle growth 5 homolog (mouse) K18194 USMG5; up-regulated during skeletal muscle growth protein 5 D 101719391 up-regulated during skeletal muscle growth protein 5-like K18194 USMG5; up-regulated during skeletal muscle growth protein 5 B Mitochondrial dynamics C Fission and Fusion factors D 101715379 Mfn1; mitofusin 1 K21356 MFN1; mitofusin 1 [EC:3.6.5.-] D 101715674 Mfn2; mitofusin 2 K06030 MFN2; mitofusin 2 [EC:3.6.5.-] D 101698766 Opa1; OPA1, mitochondrial dynamin like GTPase K17079 OPA1; optic atrophy protein 1 [EC:3.6.5.5] D 101707936 Opa3; optic atrophy 3 protein K23166 OPA3; optic atrophy 3 protein D 101720060 optic atrophy 3 protein-like K23166 OPA3; optic atrophy 3 protein D 101698065 Triap1; TP53 regulated inhibitor of apoptosis 1 K17968 TRIAP1; TRIAP1/MDM35 family protein D 101700343 TP53-regulated inhibitor of apoptosis 1 K17968 TRIAP1; TRIAP1/MDM35 family protein D 101719514 Parl; presenilin associated rhomboid like K09650 PARL; rhomboid-like protein [EC:3.4.21.105] D 101707336 Bak1; BCL2 antagonist/killer 1 K14021 BAK; Bcl-2 homologous antagonist/killer D 101713575 Bax; BCL2 associated X, apoptosis regulator K02159 BAX; apoptosis regulator BAX D 101712251 dynamin-1-like protein K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5] D 101713152 Dnm1l; dynamin 1 like K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5] D 101723592 dynamin-1-like protein K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5] D 101700353 Fis1; fission, mitochondrial 1 K17969 FIS1; mitochondrial fission 1 protein D 101697682 small ubiquitin-related modifier 2 K12160 SUMO; small ubiquitin-related modifier D 101702378 Sumo3; small ubiquitin-like modifier 3 K12160 SUMO; small ubiquitin-related modifier D 101703415 small ubiquitin-related modifier 2-like K12160 SUMO; small ubiquitin-related modifier D 101706735 small ubiquitin-related modifier 2 K12160 SUMO; small ubiquitin-related modifier D 101711853 Sumo2; small ubiquitin-like modifier 2 K12160 SUMO; small ubiquitin-related modifier D 101713191 small ubiquitin-related modifier 2-like K12160 SUMO; small ubiquitin-related modifier D 101714060 small ubiquitin-related modifier 2-like K12160 SUMO; small ubiquitin-related modifier D 101718438 small ubiquitin-related modifier 3 K12160 SUMO; small ubiquitin-related modifier D 101703609 Sumo1; small ubiquitin-like modifier 1 K12160 SUMO; small ubiquitin-related modifier D 101699535 small ubiquitin-related modifier 2-like K12160 SUMO; small ubiquitin-related modifier D 101702999 small ubiquitin-related modifier 2-like K12160 SUMO; small ubiquitin-related modifier D 101708379 Sh3glb1; SH3 domain containing GRB2 like endophilin B1 K11248 SH3GLB1; endophilin-B1 D 101696634 Mtch2; mitochondrial carrier 2 K17885 MTCH; mitochondrial carrier D 101706976 Mtch1; mitochondrial carrier 1 K17885 MTCH; mitochondrial carrier D 101711030 Mff; mitochondrial fission factor K22076 MFF; mitochondrial fission factor D 101711728 Gdap1l1; ganglioside induced differentiation associated protein 1 like 1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1 D 101720956 Gdap1; ganglioside induced differentiation associated protein 1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1 D 101721305 Vat1; vesicle amine transport 1 K23167 VAT1; synaptic vesicle membrane protein VAT-1 D 101696982 Mief2; mitochondrial elongation factor 2 K23507 MIEF1_2; mitochondrial dynamics protein MID51/49 D 101724633 Mief1; mitochondrial elongation factor 1 K23507 MIEF1_2; mitochondrial dynamics protein MID51/49 D 101713335 Pld6; phospholipase D family member 6 K16862 PLD6; mitochondrial cardiolipin hydrolase [EC:3.1.4.-] D 101702713 Miga1; mitoguardin 1 K27289 MIGA; mitoguardin D 101709149 Miga2; mitoguardin 2 K27289 MIGA; mitoguardin C Actin cytoskeleton organization D 101702483 Actg1; actin gamma 1 K05692 ACTB_G1; actin beta/gamma 1 D 101717255 Actb; actin beta K05692 ACTB_G1; actin beta/gamma 1 D 101725350 Naa20; N(alpha)-acetyltransferase 20, NatB catalytic subunit K17972 NAA20; N-terminal acetyltransferase B complex catalytic subunit [EC:2.3.1.254] D 101724988 Naa25; N(alpha)-acetyltransferase 25, NatB auxiliary subunit K17973 NAA25; N-terminal acetyltransferase B complex non-catalytic subunit C Mitochondrial movement D 101723661 Phb; prohibitin K17080 PHB1; prohibitin 1 D 101725906 Phb2; prohibitin 2 K17081 PHB2; prohibitin 2 D 101725048 Ktn1; kinectin 1 K17975 KTN1; kinectin C Retention of mitochondria D 101712251 dynamin-1-like protein K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5] D 101713152 Dnm1l; dynamin 1 like K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5] D 101723592 dynamin-1-like protein K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5] D 101697151 Myo5a; myosin VA K10357 MYO5; myosin V D 101698272 Myo5c; myosin VC K10357 MYO5; myosin V D 101722462 Myo5b; myosin VB K10357 MYO5; myosin V D 101715865 Xiap; X-linked inhibitor of apoptosis K04725 XIAP; E3 ubiquitin-protein ligase XIAP [EC:2.3.2.27] D 101708166 Diablo; diablo IAP-binding mitochondrial protein K10522 DIABLO; diablo C Morphogenesis factors D 101707851 Snx25; sorting nexin 25 K17887 SNX25; sorting nexin-25 D 101713608 mitochondrial Rho GTPase 1-like K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-] D 101723834 Rhot1; ras homolog family member T1 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-] D 101726109 Immt; inner membrane mitochondrial protein K17785 IMMT; MICOS complex subunit MIC60 D 101720158 Mtfp1; mitochondrial fission process 1 K17981 MTFP1; mitochondrial fission process protein 1 D 101724202 Dap3; death associated protein 3 K17408 DAP3; small subunit ribosomal protein S29 D 101712885 Nedd4; neural precursor cell expressed, developmentally down-regulated 4, E3 ubiquitin protein ligase K10591 NEDD4; E3 ubiquitin-protein ligase NEDD4 [EC:2.3.2.26] D 101701845 Oxr1; oxidation resistance 1 K25437 OXR1; oxidation resistance protein 1 D 101725678 Msto1; misato 1, mitochondrial distribution and morphology regulator K27320 MSTO1; protein misato B Mitophagy factors C Autophagy-related proteins D 101706866 Atg2a; autophagy related 2A K17906 ATG2; autophagy-related protein 2 D 101716535 Atg2b; autophagy related 2B K17906 ATG2; autophagy-related protein 2 D 101697524 Atg3; autophagy related 3 K08343 ATG3; ubiquitin-like-conjugating enzyme ATG3 D 101713656 Atg4c; autophagy related 4C cysteine peptidase K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 101720949 Atg4a; autophagy related 4A cysteine peptidase K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 101719929 Atg4d; autophagy related 4D cysteine peptidase K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 101719832 Atg4b; autophagy related 4B cysteine peptidase K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 101707624 Atg5; autophagy related 5 K08339 ATG5; autophagy-related protein 5 D 101713661 beclin-2-like K08334 BECN; beclin D 101712212 Becn1; beclin 1 K08334 BECN; beclin D 101714077 Atg7; autophagy related 7 K08337 ATG7; ubiquitin-like modifier-activating enzyme ATG7 D 101706208 Gabarapl2; GABA type A receptor associated protein like 2 K08341 GABARAP; GABA(A) receptor-associated protein D 101710547 Gabarapl1; GABA type A receptor associated protein like 1 K08341 GABARAP; GABA(A) receptor-associated protein D 101711840 Gabarap; GABA type A receptor-associated protein K08341 GABARAP; GABA(A) receptor-associated protein D 101710743 Atg9b; autophagy related 9B K17907 ATG9; autophagy-related protein 9 D 101720635 Atg9a; autophagy related 9A K17907 ATG9; autophagy-related protein 9 D 101707298 Atg10; autophagy related 10 K17888 ATG10L; ubiquitin-like-conjugating enzyme ATG10 D 101721642 Atg12; autophagy related 12 K08336 ATG12; ubiquitin-like protein ATG12 D 101723970 Atg14; autophagy related 14 K17889 ATG14L; beclin 1-associated autophagy-related key regulator D 101715799 Atg16l1; autophagy related 16 like 1 K17890 ATG16L1; autophagy-related protein 16-1 D 101723082 Atg16l2; autophagy related 16 like 2 K20868 ATG16L2; autophagy-related protein 16-2 D 101722436 Wipi1; WD repeat domain, phosphoinositide interacting 1 K17908 WIPI1_2; autophagy-related protein 18 D 101722837 Wipi2; WD repeat domain, phosphoinositide interacting 2 K17908 WIPI1_2; autophagy-related protein 18 C Parkin-dependent mechanism factors D 101700770 Park2; parkin RBR E3 ubiquitin protein ligase K04556 PARK2; parkin [EC:2.3.2.31] D 101713294 Rnf41; ring finger protein 41 K11981 RNF41; E3 ubiquitin-protein ligase NRDP1 [EC:2.3.2.27] D 101722045 Clec16a; C-type lectin domain family 16 member A K19513 CLEC16A; protein CLEC16A D 101716045 Pink1; PTEN induced putative kinase 1 K05688 PINK1; PTEN induced putative kinase 1 [EC:2.7.11.1] D 101719514 Parl; presenilin associated rhomboid like K09650 PARL; rhomboid-like protein [EC:3.4.21.105] D 101724587 Sqstm1; sequestosome 1 K14381 SQSTM1; sequestosome 1 D 101704862 Tax1bp1; Tax1 binding protein 1 K21347 TAX1BP1; Tax1-binding protein 1 D 101710475 tax1-binding protein 1 homolog K21347 TAX1BP1; Tax1-binding protein 1 D 101715405 Calcoco2; calcium binding and coiled-coil domain 2 K21348 CALCOCO2; calcium-binding and coiled-coil domain-containing protein 2 D 101725050 Ambra1; autophagy and beclin 1 regulator 1 K17985 AMBRA1; activating molecule in BECN1-regulated autophagy protein 1 C Parkin-independent mechanism factors D 101722321 Atg13; autophagy related 13 K08331 ATG13; autophagy-related protein 13 D 101714353 Ulk1; unc-51 like autophagy activating kinase 1 K21357 ULK1; serine/threonine-protein kinase ULK1 [EC:2.7.11.1] D 101712848 Ulk2; unc-51 like autophagy activating kinase 2 K08269 ULK2; serine/threonine-protein kinase ULK2 [EC:2.7.11.1] D 101696553 Rb1cc1; RB1 inducible coiled-coil 1 K17589 RB1CC1; RB1-inducible coiled-coil protein 1 D 101721047 RB1-inducible coiled-coil protein 1-like K17589 RB1CC1; RB1-inducible coiled-coil protein 1 D 101725326 Hsp90aa1; heat shock protein 90 alpha family class A member 1 K04079 HSP90A; molecular chaperone HtpG D 101710837 heat shock protein HSP 90-alpha-like K04079 HSP90A; molecular chaperone HtpG D 101726120 heat shock protein HSP 90-beta-like K04079 HSP90A; molecular chaperone HtpG D 101699803 Hsp90ab1; heat shock protein 90 alpha family class B member 1 K04079 HSP90A; molecular chaperone HtpG D 101716587 Cdc37; cell division cycle 37 K09554 CDC37; cell division cycle protein 37 D 101723417 Smurf1; SMAD specific E3 ubiquitin protein ligase 1 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26] D 101697984 Smurf2; SMAD specific E3 ubiquitin protein ligase 2 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26] D 101709497 Bnip3l; BCL2 interacting protein 3 like K15465 BNIP3L; BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like D 101722581 FUN14 domain-containing protein 1-like K17986 FUNDC1; FUN14 domain-containing protein 1 D 101705175 Fundc1; FUN14 domain containing 1 K17986 FUNDC1; FUN14 domain-containing protein 1 D 101697101 FUN14 domain-containing protein 1-like K17986 FUNDC1; FUN14 domain-containing protein 1 C Other mitophagy factors D 101698482 Prkaa2; protein kinase AMP-activated catalytic subunit alpha 2 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31] D 101722998 Prkaa1; protein kinase AMP-activated catalytic subunit alpha 1 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31] D 101709236 Map1lc3b; microtubule associated protein 1 light chain 3 beta K10435 MAP1LC; microtubule-associated protein 1 light chain D 101710069 Map1lc3a; microtubule associated protein 1 light chain 3 alpha K10435 MAP1LC; microtubule-associated protein 1 light chain D 101704622 Nbr1; NBR1, autophagy cargo receptor K17987 NBR1; next to BRCA1 gene 1 protein D 101716786 Tecpr1; tectonin beta-propeller repeat containing 1 K17988 TECPR1; tectonin beta-propeller repeat-containing protein 1 D 101717361 Zfyve1; zinc finger FYVE-type containing 1 K17603 ZFYVE1; zinc finger FYVE domain-containing protein 1 D 101718395 Coasy; Coenzyme A synthase K02318 COASY; phosphopantetheine adenylyltransferase / dephospho-CoA kinase [EC:2.7.7.3 2.7.1.24] D 101710669 Pla2g6; phospholipase A2 group VI K16343 PLA2G6; calcium-independent phospholipase A2 [EC:3.1.1.4] D 101711101 chromosome unknown open reading frame, human C19orf12 K23168 MPAN; protein MPAN D 101721988 Fundc2; FUN14 domain containing 2 K24308 FUNDC2; FUN14 domain-containing protein 2 ! #
#[ BRITE | KEGG2 | KEGG ]
#Last updated: March 14, 2024