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  Mitochondrial Biogenesis - Nasonia vitripennis (jewel wasp)

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AMitochondrial DNA transcription, translation, and replication factors B Mitochondrial DNA-encoded proteins C Mitochondrial respiratory chain complex I C Mitochondrial respiratory chain complex III C Cytochrome c oxidase D 116418257 LOW QUALITY PROTEIN: cytochrome c oxidase subunit 1-like K02256 COX1; cytochrome c oxidase subunit 1 [EC:7.1.1.9] C F-type ATPase B Mitochondrial transcription and translation factors C Mitochondrial RNA polymerase D 100113753 DNA-directed RNA polymerase, mitochondrial isoform X1 K10908 POLRMT; DNA-directed RNA polymerase, mitochondrial [EC:2.7.7.6] C Mitochondrial transcription factors D 100114857 transcription factor A, mitochondrial K11830 TFAM; transcription factor A, mitochondrial D 100116230 dimethyladenosine transferase 1, mitochondrial K15266 TFB1M; dimethyladenosine transferase 1, mitochondrial [EC:2.1.1.-] D 100121237 dimethyladenosine transferase 2, mitochondrial K17653 TFB2M; dimethyladenosine transferase 2, mitochondrial [EC:2.1.1.-] C Mitochondrial translation factors D 100115504 translation initiation factor IF-2, mitochondrial K02519 infB; translation initiation factor IF-2 D 100678779 uncharacterized protein LOC100678779 K02520 infC; translation initiation factor IF-3 D 100114209 elongation factor Ts, mitochondrial K02357 tsf; elongation factor Ts D 100122793 elongation factor Tu K02358 tuf; elongation factor Tu D 100121273 elongation factor Tu, mitochondrial K02358 tuf; elongation factor Tu D 100119401 elongation factor G, mitochondrial K02355 fusA; elongation factor G D 100116534 ribosome-releasing factor 2, mitochondrial K02355 fusA; elongation factor G D 100117152 uncharacterized protein LOC100117152 K15031 MTERF; mitochondrial transcription termination factor family protein D 100114274 transcription termination factor 3, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein D 100118727 translation factor GUF1 homolog, mitochondrial K21594 GUF1; translation factor GUF1, mitochondrial [EC:3.6.5.-] C RNase MRP D 100115548 ribonucleases P/MRP protein subunit POP1 K01164 POP1; ribonuclease P/MRP protein subunit POP1 [EC:3.1.26.5] D 100122856 ribonuclease P protein subunit p29 isoform X2 K03538 POP4; ribonuclease P protein subunit POP4 [EC:3.1.26.5] D 100680529 uncharacterized protein LOC100680529 K03537 POP5; ribonuclease P/MRP protein subunit POP5 [EC:3.1.26.5] D 100170021 Rpp30; RNaseP protein p30 K03539 RPP1; ribonuclease P/MRP protein subunit RPP1 [EC:3.1.26.5] D 100116662 ribonuclease P protein subunit p20 K14527 RPP20; ribonuclease P/MRP protein subunit RPP20 [EC:3.1.26.5] D 100679008 uncharacterized protein LOC100679008 K14523 RPP38; ribonucleases P/MRP protein subunit RPP38 [EC:3.1.26.5] D 100119502 ribonuclease P protein subunit p40 K14530 RPP40; ribonucleases P/MRP protein subunit RPP40 [EC:3.1.26.5] C Mitochondrial ribonuclease P D 100121051 mitochondrial ribonuclease P protein 1 homolog K17654 TRMT10C; mitochondrial ribonuclease P protein 1 [EC:2.1.1.-] D 100114736 3-hydroxyacyl-CoA dehydrogenase type-2 K08683 HSD17B10; 3-hydroxyacyl-CoA dehydrogenase / 3-hydroxy-2-methylbutyryl-CoA dehydrogenase [EC:1.1.1.35 1.1.1.178] D 100119811 mitochondrial ribonuclease P catalytic subunit K17655 MRPP3; mitochondrial ribonuclease P protein 3 C Other mitochondrial DNA transcription and translation factors D 103315579 putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51 D 100119431 uncharacterized protein LOC100119431 isoform X1 K17656 MSS51; mitochondrial splicing suppressor protein 51 D 100680401 uncharacterized protein LOC100680401 K17658 TEFM; transcription elongation factor, mitochondrial D 100123139 pentatricopeptide repeat-containing protein 1, mitochondrial K17710 PTCD1; pentatricopeptide repeat domain-containing protein 1 D 100121091 pentatricopeptide repeat-containing protein 2, mitochondrial K17711 PTCD2; pentatricopeptide repeat domain-containing protein 2 D 100121935 protein PTCD3 homolog, mitochondrial K17659 PTCD3; pentatricopeptide repeat domain-containing protein 3 D 100116427 ATP-dependent RNA helicase DHX30 K13185 DHX30; ATP-dependent RNA helicase DHX30 [EC:5.6.2.6] D 100679452 ubiquinol-cytochrome-c reductase complex assembly factor 1 isoform X1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3 D 100678489 putative ATPase N2B isoform X1 K18798 AFG1; peroxisome-assembly ATPase [EC:3.6.4.7] D 100122860 mitochondrial inner membrane protease ATP23 homolog K18156 ATP23; mitochondrial inner membrane protease ATP23 [EC:3.4.24.-] D 100123955 ATP-dependent RNA helicase SUV3 homolog, mitochondrial K17675 SUPV3L1; ATP-dependent RNA helicase SUPV3L1/SUV3 [EC:5.6.2.6] D 100117058 ADP,ATP carrier protein 2 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31 D 100120798 mitoferrin-1 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37 D 100121436 mitochondrial assembly of ribosomal large subunit protein 1 K25803 MALSU1; mitochondrial assembly of ribosomal large subunit protein 1 D 100117908 GTPase Era, mitochondrial isoform X1 K03595 era; GTPase D 100119473 tyrosine--tRNA ligase, cytoplasmic isoform X1 K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1] D 100123580 tyrosine--tRNA ligase, mitochondrial K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1] D 100122168 probable leucine--tRNA ligase, mitochondrial isoform X1 K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4] D 100115181 leucine--tRNA ligase, cytoplasmic K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4] D 100120650 aspartate--tRNA ligase, mitochondrial K01876 DARS2; aspartyl-tRNA synthetase [EC:6.1.1.12] D 100123216 glycine--tRNA ligase K01880 GARS; glycyl-tRNA synthetase [EC:6.1.1.14] D 100120462 probable arginine--tRNA ligase, mitochondrial K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19] D 100121004 arginine--tRNA ligase, cytoplasmic isoform X1 K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19] D 100121002 glutamyl-tRNA(Gln) amidotransferase subunit A, mitochondrial K02433 gatA; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit A [EC:6.3.5.6 6.3.5.7] D 100114474 glutamyl-tRNA(Gln) amidotransferase subunit B, mitochondrial K02434 gatB; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit B [EC:6.3.5.6 6.3.5.7] D 103316089 glutamyl-tRNA(Gln) amidotransferase subunit C, mitochondrial K02435 gatC; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit C [EC:6.3.5.6 6.3.5.7] D 100123807 poly(A) RNA polymerase, mitochondrial K18060 MTPAP; poly(A) RNA polymerase, mitochondrial [EC:2.7.7.19] D 100113824 nitric oxide-associated protein 1 K19832 NOA1; nitric oxide-associated protein 1 D 100123684 5-methylcytosine rRNA methyltransferase NSUN4 K21970 NSUN4; 5-methylcytosine rRNA methyltransferase NSUN4 [EC:2.1.1.-] D 100120685 RCC1-like G exchanging factor-like protein isoform X1 K23495 RCC1L; RCC1-like G exchanging factor-like protein D 100117506 mitochondrial mRNA pseudouridine synthase Trub2 K23497 TRUB2; mitochondrial mRNA pseudouridine synthase TRUB2 [EC:5.4.99.-] D 100119418 FAST kinase domain-containing protein 1, mitochondrial K18190 FASTKD2; FAST kinase domain-containing protein 2 D 100677906 uncharacterized protein LOC100677906 K18190 FASTKD2; FAST kinase domain-containing protein 2 D 100116673 uncharacterized protein LOC100116673 isoform X1 K18190 FASTKD2; FAST kinase domain-containing protein 2 D 100677888 uncharacterized protein LOC100677888 K18190 FASTKD2; FAST kinase domain-containing protein 2 D 100121597 probable peptide chain release factor C12orf65, mitochondrial K23498 COXPD7; peptide chain release factor D 100119195 required for meiotic nuclear division protein 1 homolog K23499 RMND1; required for meiotic nuclear division protein 1 D 100118944 probable methyltransferase-like protein 15 homolog K25876 METTL15; 12S rRNA N4-methylcytidine (m4C) methyltransferase [EC:2.1.1.-] D 100118825 UPF0160 protein MYG1, mitochondrial isoform X1 K25877 MYG1; MYG1 exonuclease [EC:3.1.-.-] D 100499182 uncharacterized protein LOC100499182 K26186 MTRES1; mitochondrial transcription rescue factor 1 B Mitochondrial DNA replication factors C Mitochondrial DNA polymerase D 100118160 DNA polymerase subunit gamma-1, mitochondrial K02332 POLG; DNA polymerase gamma 1 [EC:2.7.7.7] D 100120904 DNA polymerase subunit gamma-2, mitochondrial K02333 POLG2; DNA polymerase gamma 2 D 100120024 DNA-directed primase/polymerase protein isoform X1 K22761 PRIMPOL; DNA-directed primase/polymerase protein [EC:2.7.7.102 2.7.7.7] D 116417824 uncharacterized protein LOC116417824 isoform X1 K22761 PRIMPOL; DNA-directed primase/polymerase protein [EC:2.7.7.102 2.7.7.7] D 107981859 uncharacterized protein LOC107981859 K22761 PRIMPOL; DNA-directed primase/polymerase protein [EC:2.7.7.102 2.7.7.7] D 116416412 uncharacterized protein LOC116416412 K22761 PRIMPOL; DNA-directed primase/polymerase protein [EC:2.7.7.102 2.7.7.7] C Mitochondrial DNA maintenance factors D 100120468 endonuclease G, mitochondrial isoform X2 K01173 ENDOG; endonuclease G, mitochondrial D 100122976 mitochondrial genome maintenance exonuclease 1 K19465 MGME1; mitochondrial genome maintenance exonuclease 1 [EC:3.1.-.-] D 100120404 twinkle protein, mitochondrial K17680 PEO1; twinkle protein [EC:5.6.2.3] D 116417730 ATP-dependent DNA helicase PIF1-like K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3] D 116417954 ATP-dependent DNA helicase PIF1-like K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3] D 103315880 ATP-dependent DNA helicase PIF1-like K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3] D 103317178 ATP-dependent DNA helicase PIF1-like K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3] D 116417287 ATP-dependent DNA helicase PIF1-like K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3] D 116418163 ATP-dependent DNA helicase pfh1-like K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3] C Other Mitochondrial DNA replication factors D 100117646 single-stranded DNA-binding protein, mitochondrial K03111 ssb; single-strand DNA-binding protein D 100121271 ATPase family AAA domain-containing protein 3A homolog K17681 ATAD3A_B; ATPase family AAA domain-containing protein 3A/B # AMitochondrial protein import machinery B Endoplasmic reticulum membrane and cytosol C ER-mitochondria encounter structure (ERMES) complex C Other ER-memrane and cytosol factors D 100119170 mitochondrial Rho GTPase isoform X4 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-] D 100114493 HSC70; heat shock cognate 70 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 100114907 heat shock protein 68 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 100114095 heat shock cognate 71 kDa protein-like isoform X2 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 100120280 heat shock 70 kDa protein cognate 4-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 100119971 heat shock protein 68 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 100113492 heat shock protein 68-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 100117320 aryl-hydrocarbon-interacting protein-like 1 isoform X2 K17767 AIP; AH receptor-interacting protein B Outer membrane C Transporter outer membrane (TOM) complex D 100124015 mitochondrial import receptor subunit TOM40 homolog 1 K11518 TOM40; mitochondrial import receptor subunit TOM40 D 100121090 mitochondrial import receptor subunit TOM40 homolog 1-like K11518 TOM40; mitochondrial import receptor subunit TOM40 D 100121167 mitochondrial import receptor subunit TOM70 K17768 TOM70; mitochondrial import receptor subunit TOM70 D 100113711 mitochondrial import receptor subunit TOM22 homolog K17769 TOM22; mitochondrial import receptor subunit TOM22 D 100216321 Tomm20; mitochondrial import receptor subunit TOM20 homolog K17770 TOM20; mitochondrial import receptor subunit TOM20 D 100113971 TOM7; translocase of outer mitochondrial membrane 7 homolog K17771 TOM7; mitochondrial import receptor subunit TOM7 C TOB/SAM complex D 100119887 sorting and assembly machinery component 50 homolog isoform X2 K07277 SAM50; outer membrane protein insertion porin family C Porin D 100120516 voltage-dependent anion-selective channel K15040 VDAC2; voltage-dependent anion channel protein 2 D 100122593 voltage-dependent anion-selective channel-like K15040 VDAC2; voltage-dependent anion channel protein 2 C ERMES complex C Other outer membrane factor D 100117580 metaxin-1 isoform X1 K17776 MTX; metaxin D 100119679 metaxin-2 isoform X1 K17776 MTX; metaxin D 100121392 mitochondrial amidoxime reducing component 2 K27318 MTARC; mitochondrial amidoxime-reducing component [EC:1.7.-.-] D 100123356 mitochondrial amidoxime-reducing component 1 K27318 MTARC; mitochondrial amidoxime-reducing component [EC:1.7.-.-] B Inter membrane space C Transporter inner membrane (TIM) 9/10 complex D 100115021 mitochondrial import inner membrane translocase subunit Tim9 K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9 D 100114656 mitochondrial import inner membrane translocase subunit Tim10 K17778 TIM10; mitochondrial import inner membrane translocase subunit TIM10 D 103316509 mitochondrial import inner membrane translocase subunit Tim10 B K17779 TIM10B; mitochondrial import inner membrane translocase subunit TIM10B C TIM8/13 complex D 100680191 mitochondrial import inner membrane translocase subunit Tim8 K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8 D 100122302 mitochondrial import inner membrane translocase subunit Tim13 K17781 TIM13; mitochondrial import inner membrane translocase subunit TIM13 C Mitochondrial intermembrane space assembly (MIA) complex D 100678899 FAD-linked sulfhydryl oxidase ALR K17783 ERV1; mitochondrial FAD-linked sulfhydryl oxidase [EC:1.8.3.2] B Inner mambrane C MICOS complex D 100114008 MICOS complex subunit Mic10 K17784 MICOS10; MICOS complex subunit MIC10 D 100123668 MICOS complex subunit Mic60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60 D 100115502 MICOS complex subunit MIC13 homolog QIL1 K24624 MICOS13; MICOS complex subunit MIC13 D 100116843 MICOS complex subunit mic25a K17563 CHCHD3; MICOS complex subunit MIC19 D 100121109 APOOL; apolipoprotein O-like K24626 APOOL; MICOS complex subunit MIC27 C MICOS complex (yeast) D 100114008 MICOS complex subunit Mic10 K17784 MICOS10; MICOS complex subunit MIC10 D 100123668 MICOS complex subunit Mic60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60 C TIM22 complex D 100114187 mitochondrial import inner membrane translocase subunit Tim22 K17790 TIM22; mitochondrial import inner membrane translocase subunit TIM22 C TIM23 complex D 100119130 mitochondrial import inner membrane translocase subunit Tim23 isoform X2 K17794 TIM23; mitochondrial import inner membrane translocase subunit TIM23 D 100118104 mitochondrial import inner membrane translocase subunit Tim17-B K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17 D 100680383 mitochondrial import inner membrane translocase subunit Tim21 K17796 TIM21; mitochondrial import inner membrane translocase subunit TIM21 D 100124003 Timm50; translocase of inner mitochondrial membrane 50 homolog K17496 TIM50; mitochondrial import inner membrane translocase subunit TIM50 C Mitochondrial calcium uniporter complex D 100120233 calcium uniporter protein, mitochondrial isoform X2 K20858 MCU; calcium uniporter protein, mitochondrial D 100117661 calcium uptake protein 1 homolog, mitochondrial isoform X2 K22827 MICU1; calcium uptake protein 1, mitochondrial D 116416395 essential MCU regulator, mitochondrial K22830 SMDT1; essential MCU regulator, mitochondrial C Other inner membrane factors D 103317046 mitochondrial proton/calcium exchanger protein isoform X1 K17800 LETM1; LETM1 and EF-hand domain-containing protein 1, mitochondrial D 100115538 mitochondrial pyruvate carrier 1 K22138 MPC1; mitochondrial pyruvate carrier 1 D 100113891 mitochondrial pyruvate carrier 1 K22138 MPC1; mitochondrial pyruvate carrier 1 D 100119487 mitochondrial pyruvate carrier 2 K22139 MPC2; mitochondrial pyruvate carrier 2 D 100122616 mitochondrial pyruvate carrier 2-like K22139 MPC2; mitochondrial pyruvate carrier 2 B Matrix C MMC/PAM proteins D 100114146 mitochondrial import inner membrane translocase subunit TIM44 isoform X2 K17804 TIM44; mitochondrial import inner membrane translocase subunit TIM44 D 100114552 heat shock 70 kDa protein cognate 5 K04043 dnaK; molecular chaperone DnaK D 100115704 grpE protein homolog 1, mitochondrial isoform X1 K03687 GRPE; molecular chaperone GrpE D 100120792 mitochondrial import inner membrane translocase subunit TIM14 K09539 DNAJC19; DnaJ homolog subfamily C member 19 D 100117106 mitochondrial import inner membrane translocase subunit Tim16 K17805 PAM16; mitochondrial import inner membrane translocase subunit TIM16 C Other matrix factors D 100120518 PMPCA; mitochondrial-processing peptidase subunit alpha K01412 PMPCA; mitochondrial-processing peptidase subunit alpha [EC:3.4.24.64] D 100115333 Pmpcb; mitochondrial-processing peptidase subunit beta K17732 PMPCB; mitochondrial-processing peptidase subunit beta [EC:3.4.24.64] D 100119769 mitochondrial intermediate peptidase K01410 MIPEP; mitochondrial intermediate peptidase [EC:3.4.24.59] D 100114031 heat shock protein 60A K04077 groEL; chaperonin GroEL [EC:5.6.1.7] D 100114790 10 kDa heat shock protein, mitochondrial K04078 groES; chaperonin GroES D 100121882 protein tumorous imaginal discs, mitochondrial isoform X1 K09504 DNAJA3; DnaJ homolog subfamily A member 3 D 103315890 phosphatidate cytidylyltransferase, mitochondrial K17807 TAM41; mitochondrial translocator assembly and maintenance protein 41 D 100121151 DNL-type zinc finger protein K17808 ZIM17; mitochondrial protein import protein ZIM17 D 100120487 persulfide dioxygenase ETHE1, mitochondrial isoform X2 K17725 ETHE1; sulfur dioxygenase [EC:1.13.11.18] D 100123965 uncharacterized protein LOC100123965 isoform X1 K17725 ETHE1; sulfur dioxygenase [EC:1.13.11.18] D 100117524 polymerase delta-interacting protein 2 isoform X1 K17809 POLDIP2; polymerase delta-interacting protein 2 # AMitochondrial quality control factors B Regulator of mitochondrial biogenesis C Ubiquitas transcription factors D 100121641 Creb; cyclic-AMP response element binding protein isoform 1 K05870 CREB1; cyclic AMP-responsive element-binding protein 1 D 100119401 elongation factor G, mitochondrial K02355 fusA; elongation factor G D 100116534 ribosome-releasing factor 2, mitochondrial K02355 fusA; elongation factor G D 100119779 transcriptional repressor protein YY1 isoform X1 K09201 YY; transcription factor YY D 100121072 GA-binding protein subunit beta-2 K09454 GABPB; GA-binding protein transcription factor, beta D 100114857 transcription factor A, mitochondrial K11830 TFAM; transcription factor A, mitochondrial C Nuclear respiratory factors D 100123022 DNA-binding protein P3A2 isoform X9 K11831 NRF1; nuclear respiratory factor 1 C Coactivators D 100115904 serine/arginine repetitive matrix protein 2 isoform X3 K17963 PPRC1; peroxisome proliferator-activated receptor gamma coactivator-related protein 1 D 100116193 CREB-regulated transcription coactivator 1 isoform X1 K15309 CRTC1; CREB-regulated transcription coactivator 1 D 100123220 histone acetyltransferase p300 isoform X2 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48] C Proteins involved in Fe-S cluster biogenesis D 100122735 cysteine desulfurase, mitochondrial K04487 iscS; cysteine desulfurase [EC:2.8.1.7] D 100115291 iron-sulfur cluster assembly scaffold protein IscU K22068 ISCU; iron-sulfur cluster assembly enzyme ISCU, mitochondrial D 100114190 adrenodoxin-like protein 2, mitochondrial K22070 FDX1; ferredoxin-1, mitochondrial D 100118135 adrenodoxin-like protein 1, mitochondrial K22071 FDX2; ferredoxin-2, mitochondrial D 100118934 NADPH:adrenodoxin oxidoreductase, mitochondrial K18914 FDXR; adrenodoxin-NADP+ reductase [EC:1.18.1.6] D 100114552 heat shock 70 kDa protein cognate 5 K04043 dnaK; molecular chaperone DnaK D 100678921 iron-sulfur cluster co-chaperone protein HscB K04082 hscB; molecular chaperone HscB D 100122879 nucleotide exchange factor Sil1 K14001 SIL1; nucleotide exchange factor SIL1 D 100121623 glutaredoxin-related protein 5, mitochondrial K07390 grxD; monothiol glutaredoxin D 100124241 iron-sulfur cluster assembly 1 homolog, mitochondrial isoform X1 K22063 ISCA1; iron-sulfur cluster assembly 1 D 100114280 iron-sulfur cluster assembly 2 homolog, mitochondrial K22072 ISCA2; iron-sulfur cluster assembly 2 D 100115222 putative transferase CAF17 homolog, mitochondrial isoform X1 K22073 IBA57; transferase CAF17, mitochondrial [EC:2.1.-.-] D 100680154 NFU1 iron-sulfur cluster scaffold homolog, mitochondrial K22074 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial D 100122269 DNA-binding transcriptional regulator BolA K22066 BOLA1; BolA-like protein 1 D 100114450 bolA-like protein 3 K22075 BOLA3; BolA-like protein 3 D 100117626 sideroflexin-1 K23500 SFXN1_3; sideroflexin-1/3 D 100113883 sideroflexin-2 K23501 SFXN2; sideroflexin-2 C Other regulator of mitochondrial biogenesis D 100121693 carnitine O-palmitoyltransferase 1, liver isoform isoform X2 K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21] D 100123741 probable 2-oxoglutarate dehydrogenase E1 component DHKTD1 homolog, mitochondrial isoform X2 K15791 DHKTD1; 2-oxoadipate dehydrogenase E1 component [EC:1.2.4.-] D 100121023 F-box/LRR-repeat protein 4 K10270 FBXL4; F-box and leucine-rich repeat protein 4 D 100122420 host cell factor isoform X1 K14966 HCFC1; host cell factor 1 D 100120106 huntingtin isoform X1 K04533 HD; huntingtin D 100120450 5'-AMP-activated protein kinase catalytic subunit alpha-2 isoform X2 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31] D 100119946 lon protease homolog, mitochondrial isoform X1 K08675 PRSS15; ATP-dependent Lon protease [EC:3.4.21.53] D 100122518 NAD-dependent protein deacetylase sirtuin-1 K11411 SIRT1; NAD-dependent protein deacetylase sirtuin 1 [EC:2.3.1.286] D 100123623 protein SERAC1 K23504 SERAC1; protein SERAC1 D 100678522 protein UXT homolog K26537 UXT; protein UXT B Mitochondrial respiratory chain complex assembly factors C Complex-I assembly factors D 100123421 complex I intermediate-associated protein 30, mitochondrial K18159 NDUFAF1; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 1 D 100119047 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2 K18160 NDUFAF2; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2 D 100679620 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3 K09008 NDUFAF3; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3 D 116416966 protein NDUFAF4 homolog K18161 NDUFAF4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4 D 100116856 arginine-hydroxylase NDUFAF5, mitochondrial K18162 NDUFAF5; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 5 [EC:2.1.1.-] D 100122909 NADH dehydrogenase (ubiquinone) complex I, assembly factor 6 K18163 NDUFAF6; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 6 D 100116178 protein arginine methyltransferase NDUFAF7, mitochondrial K18164 NDUFAF7; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 7 D 100123735 evolutionarily conserved signaling intermediate in Toll pathway, mitochondrial K04405 ECSIT; evolutionarily conserved signaling intermediate in Toll pathway D 100119581 complex I assembly factor ACAD9, mitochondrial K15980 ACAD9; acyl-CoA dehydrogenase family member 9 [EC:1.3.99.-] D 100114376 iron-sulfur protein NUBPL K03593 mrp; ATP-binding protein involved in chromosome partitioning D 100115336 reticulon-4-interacting protein 1 homolog, mitochondrial K23164 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial D 103316383 reticulon-4-interacting protein 1, mitochondrial K23164 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial D 100187719 140up; upstream of RpII140 K23505 TIMMDC1; complex I assembly factor TIMMDC1 C Complex-II assembly factors D 100120858 succinate dehydrogenase assembly factor 2, mitochondrial K18168 SDHAF2; succinate dehydrogenase assembly factor 2 D 100122134 succinate dehydrogenase assembly factor 2, mitochondrial K18168 SDHAF2; succinate dehydrogenase assembly factor 2 C Complex-III assembly factors D 116415701 mitochondrial chaperone BCS1 K08900 BCS1; mitochondrial chaperone BCS1 D 100122208 tetratricopeptide repeat protein 19 homolog, mitochondrial K18169 TTC19; tetratricopeptide repeat protein 19, mitochondrial D 100680037 complex III assembly factor LYRM7 K18170 LYRM7; complex III assembly factor LYRM7 D 100679452 ubiquinol-cytochrome-c reductase complex assembly factor 1 isoform X1 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3 D 103315466 uncharacterized protein LOC103315466 isoform X1 K27339 UQCC4; ubiquinol-cytochrome c reductase complex assembly factor 4 D 107980512 small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5 D 107980513 uncharacterized protein C12orf73 K27341 UQCC6; ubiquinol-cytochrome c reductase complex assembly factor 6 C Complex-IV assembly factors D 100113876 COX assembly mitochondrial protein homolog K18171 CMC1; COX assembly mitochondrial protein 1 D 100123148 uncharacterized protein LOC100123148 K18173 COA1; cytochrome c oxidase assembly factor 1 D 100677919 peptidyl-tRNA hydrolase 2, mitochondrial isoform X1 K18177 COA4; cytochrome c oxidase assembly factor 4 D 100123622 cytochrome c oxidase assembly factor 5 K18178 COA5; cytochrome c oxidase assembly factor 5 D 100117961 cytochrome c oxidase assembly factor 7 homolog K18180 COA7; cytochrome c oxidase assembly factor 7 D 100123510 protoheme IX farnesyltransferase, mitochondrial K02257 COX10; heme o synthase [EC:2.5.1.141] D 100124142 cytochrome c oxidase assembly protein COX11, mitochondrial K02258 COX11; cytochrome c oxidase assembly protein subunit 11 D 100118968 Cox15; cytochrome c oxidase assembly protein COX15 homolog K02259 COX15; heme a synthase [EC:1.17.99.9] D 100113542 cytochrome c oxidase copper chaperone K02260 COX17; cytochrome c oxidase assembly protein subunit 17 D 100120581 cytochrome c oxidase assembly protein COX18, mitochondrial K17797 COX18; mitochondrial inner membrane protein COX18 D 100679182 cytochrome c oxidase assembly protein COX18, mitochondrial K17797 COX18; mitochondrial inner membrane protein COX18 D 100123877 cytochrome c oxidase assembly protein COX19 K18183 COX19; cytochrome c oxidase assembly protein subunit 19 D 100121768 cytochrome c oxidase assembly protein COX20, mitochondrial K18184 COX20; cytochrome c oxidase assembly protein subunit 20 D 103315579 putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51 D 100119431 uncharacterized protein LOC100119431 isoform X1 K17656 MSS51; mitochondrial splicing suppressor protein 51 D 100119579 protein PET100 homolog, mitochondrial K18186 PET100; protein PET100, animal type D 100121087 protein PET117 homolog, mitochondrial K18188 PET117; protein PET117 D 100117732 mitochondrial inner membrane protein OXA1L K03217 yidC; YidC/Oxa1 family membrane protein insertase D 100122561 surfeit locus protein 1 K14998 SURF1; surfeit locus 1 family protein D 100122150 protein SCO1 homolog, mitochondrial K07152 SCO1; protein SCO1 D 100678100 translational activator of cytochrome c oxidase 1 K18189 TACO1; translational activator of cytochrome c oxidase 1 D 100118422 leucine-rich PPR motif-containing protein, mitochondrial K17964 LRPPRC; leucine-rich PPR motif-containing protein, mitochondrial D 100122661 leucine-rich PPR motif-containing protein, mitochondrial K17964 LRPPRC; leucine-rich PPR motif-containing protein, mitochondrial D 107980512 small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5 D 100678230 uncharacterized protein LOC100678230 K27342 TMEM223; transmembrane protein 223 C Complex-V assembly factors D 100122922 ATP synthase mitochondrial F1 complex assembly factor 2 K07556 ATPeAF2; ATP synthase mitochondrial F1 complex assembly factor 2 D 100679640 transmembrane protein 70 homolog, mitochondrial K17966 TMEM70; transmembrane protein 70, mitochondrial D 100119798 ATP synthase membrane subunit DAPIT, mitochondrial K18194 USMG5; up-regulated during skeletal muscle growth protein 5 B Mitochondrial dynamics C Fission and Fusion factors D 100121959 transmembrane GTPase Marf isoform X1 K06030 MFN2; mitofusin 2 [EC:3.6.5.-] D 100116450 dynamin-like 120 kDa protein, mitochondrial isoform X1 K17079 OPA1; optic atrophy protein 1 [EC:3.6.5.5] D 100118653 putative OPA3-like protein CG13603 K23166 OPA3; optic atrophy 3 protein D 103316126 optic atrophy 3 protein homolog K23166 OPA3; optic atrophy 3 protein D 100116397 TP53-regulated inhibitor of apoptosis 1 isoform X2 K17968 TRIAP1; TRIAP1/MDM35 family protein D 100122241 presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105] D 100124244 dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5] D 100115745 mitochondrial fission 1 protein isoform X1 K17969 FIS1; mitochondrial fission 1 protein D 100113961 small ubiquitin-related modifier 3 K12160 SUMO; small ubiquitin-related modifier D 100113962 small ubiquitin-related modifier K12160 SUMO; small ubiquitin-related modifier D 100117086 endophilin-B2 isoform X1 K11248 SH3GLB1; endophilin-B1 D 100117246 mitochondrial carrier homolog 2 K17885 MTCH; mitochondrial carrier D 103318082 transport and Golgi organization protein 11 isoform X1 K22076 MFF; mitochondrial fission factor D 100119848 mitoguardin isoform X1 K27289 MIGA; mitoguardin C Actin cytoskeleton organization D 100116604 Arp1; actin related protein 1 K05692 ACTB_G1; actin beta/gamma 1 D 100113694 N-alpha-acetyltransferase 20 K17972 NAA20; N-terminal acetyltransferase B complex catalytic subunit [EC:2.3.1.254] D 100123105 N-alpha-acetyltransferase 25, NatB auxiliary subunit isoform X1 K17973 NAA25; N-terminal acetyltransferase B complex non-catalytic subunit C Mitochondrial movement D 100114121 protein l(2)37Cc K17080 PHB1; prohibitin 1 D 100115233 prohibitin-2 isoform X1 K17081 PHB2; prohibitin 2 C Retention of mitochondria D 100124244 dynamin-1-like protein isoform X1 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5] D 100120420 unconventional myosin-Va isoform X2 K10357 MYO5; myosin V D 100379130 unconventional myosin-Va isoform X2 K10357 MYO5; myosin V C Morphogenesis factors D 100122047 sorting nexin-25 isoform X2 K17887 SNX25; sorting nexin-25 D 100119170 mitochondrial Rho GTPase isoform X4 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-] D 100123668 MICOS complex subunit Mic60 isoform X1 K17785 IMMT; MICOS complex subunit MIC60 D 100116768 mitochondrial fission process protein 1 K17981 MTFP1; mitochondrial fission process protein 1 D 100124263 28S ribosomal protein S29, mitochondrial K17408 DAP3; small subunit ribosomal protein S29 D 100115069 Nedd4; neural precursor cell expressed, developmentally down-regulated 4 K10591 NEDD4; E3 ubiquitin-protein ligase NEDD4 [EC:2.3.2.26] D 100122457 protein misato K27320 MSTO1; protein misato B Mitophagy factors C Autophagy-related proteins D 100123456 autophagy-related protein 2 homolog A K17906 ATG2; autophagy-related protein 2 D 100117868 ubiquitin-like-conjugating enzyme ATG3 K08343 ATG3; ubiquitin-like-conjugating enzyme ATG3 D 100170109 Atg4; autophagy-specific gene 4 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 100121532 autophagy protein 5 K08339 ATG5; autophagy-related protein 5 D 100117105 beclin-1-like protein isoform X1 K08334 BECN; beclin D 100123917 ubiquitin-like modifier-activating enzyme ATG7 K08337 ATG7; ubiquitin-like modifier-activating enzyme ATG7 D 100679003 gamma-aminobutyric acid receptor-associated protein K08341 GABARAP; GABA(A) receptor-associated protein D 100115862 Atg9; autophagy-related protein 9 K17907 ATG9; autophagy-related protein 9 D 116415991 ubiquitin-like-conjugating enzyme ATG10 K17888 ATG10L; ubiquitin-like-conjugating enzyme ATG10 D 100115078 autophagy protein 12-like K08336 ATG12; ubiquitin-like protein ATG12 D 100123342 beclin 1-associated autophagy-related key regulator K17889 ATG14L; beclin 1-associated autophagy-related key regulator D 100119823 autophagy-related protein 16 isoform X2 K17890 ATG16L1; autophagy-related protein 16-1 D 100121906 WD repeat domain phosphoinositide-interacting protein 2 isoform X3 K17908 WIPI1_2; autophagy-related protein 18 C Parkin-dependent mechanism factors D 100122062 E3 ubiquitin-protein ligase parkin K04556 PARK2; parkin [EC:2.3.2.31] D 100118782 E3 ubiquitin-protein ligase NRDP1 K11981 RNF41; E3 ubiquitin-protein ligase NRDP1 [EC:2.3.2.27] D 100117870 protein CLEC16A homolog isoform X1 K19513 CLEC16A; protein CLEC16A D 100122372 serine/threonine-protein kinase PINK1, mitochondrial isoform X1 K05688 PINK1; PTEN induced putative kinase 1 [EC:2.7.11.1] D 100122241 presenilins-associated rhomboid-like protein, mitochondrial K09650 PARL; rhomboid-like protein [EC:3.4.21.105] D 100124264 sequestosome-1 K14381 SQSTM1; sequestosome 1 D 100680119 serine-rich adhesin for platelets isoform X1 K17985 AMBRA1; activating molecule in BECN1-regulated autophagy protein 1 C Parkin-independent mechanism factors D 100117853 autophagy-related protein 13 isoform X1 K08331 ATG13; autophagy-related protein 13 D 100123698 serine/threonine-protein kinase unc-51 isoform X3 K08269 ULK2; serine/threonine-protein kinase ULK2 [EC:2.7.11.1] D 100114875 RB1-inducible coiled-coil protein 1 isoform X1 K17589 RB1CC1; RB1-inducible coiled-coil protein 1 D 100117412 heat shock protein 83 K04079 HSP90A; molecular chaperone HtpG D 100116702 heat shock protein 83 K04079 HSP90A; molecular chaperone HtpG D 100116887 hsp90 co-chaperone Cdc37 isoform X2 K09554 CDC37; cell division cycle protein 37 D 100122994 E3 ubiquitin-protein ligase SMURF2 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26] D 103317723 FUN14 domain-containing protein 1 isoform X2 K17986 FUNDC1; FUN14 domain-containing protein 1 C Other mitophagy factors D 100120450 5'-AMP-activated protein kinase catalytic subunit alpha-2 isoform X2 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31] D 116416799 microtubule-associated proteins 1A/1B light chain 3B K10435 MAP1LC; microtubule-associated protein 1 light chain D 100114727 tectonin beta-propeller repeat-containing protein isoform X1 K17988 TECPR1; tectonin beta-propeller repeat-containing protein 1 D 100118062 zinc finger FYVE domain-containing protein 1 K17603 ZFYVE1; zinc finger FYVE domain-containing protein 1 D 100116195 bifunctional coenzyme A synthase K02318 COASY; phosphopantetheine adenylyltransferase / dephospho-CoA kinase [EC:2.7.7.3 2.7.1.24] D 100121363 85/88 kDa calcium-independent phospholipase A2 isoform X1 K16343 PLA2G6; calcium-independent phospholipase A2 [EC:3.1.1.4] D 100113748 protein C19orf12 homolog K23168 MPAN; protein MPAN ! #
#[ BRITE | KEGG2 | KEGG ]
#Last updated: March 14, 2024