+D #

  Mitochondrial Biogenesis - Pan paniscus (bonobo)

% ! AMitochondrial DNA transcription, translation, and replication factors B Mitochondrial DNA-encoded proteins C Mitochondrial respiratory chain complex I D 807884 ND1; NADH dehydrogenase subunit 1 K03878 ND1; NADH-ubiquinone oxidoreductase chain 1 [EC:7.1.1.2] D 807883 ND2; NADH dehydrogenase subunit 2 K03879 ND2; NADH-ubiquinone oxidoreductase chain 2 [EC:7.1.1.2] D 807879 ND3; NADH dehydrogenase subunit 3 K03880 ND3; NADH-ubiquinone oxidoreductase chain 3 [EC:7.1.1.2] D 807875 ND4; NADH dehydrogenase subunit 4 K03881 ND4; NADH-ubiquinone oxidoreductase chain 4 [EC:7.1.1.2] D 807881 ND4L; NADH dehydrogenase subunit 4L K03882 ND4L; NADH-ubiquinone oxidoreductase chain 4L [EC:7.1.1.2] D 807878 ND5; NADH dehydrogenase subunit 5 K03883 ND5; NADH-ubiquinone oxidoreductase chain 5 [EC:7.1.1.2] D 807873 ND6; NADH dehydrogenase subunit 6 K03884 ND6; NADH-ubiquinone oxidoreductase chain 6 [EC:7.1.1.2] C Mitochondrial respiratory chain complex III D 807882 CYTB; cytochrome b K00412 CYTB; ubiquinol-cytochrome c reductase cytochrome b subunit C Cytochrome c oxidase D 807872 COX1; cytochrome c oxidase subunit I K02256 COX1; cytochrome c oxidase subunit 1 [EC:7.1.1.9] D 807874 COX2; cytochrome c oxidase subunit II K02261 COX2; cytochrome c oxidase subunit 2 D 807877 COX3; cytochrome c oxidase subunit III K02262 COX3; cytochrome c oxidase subunit 3 C F-type ATPase D 807876 ATP8; ATP synthase F0 subunit 8 K02125 ATPeF08; F-type H+-transporting ATPase subunit 8 D 807880 ATP6; ATP synthase F0 subunit 6 K02126 ATPeF0A; F-type H+-transporting ATPase subunit a B Mitochondrial transcription and translation factors C Mitochondrial RNA polymerase D 117976577 LOW QUALITY PROTEIN: DNA-directed RNA polymerase, mitochondrial-like K10908 POLRMT; DNA-directed RNA polymerase, mitochondrial [EC:2.7.7.6] D 100969314 POLRMT; DNA-directed RNA polymerase, mitochondrial isoform X1 K10908 POLRMT; DNA-directed RNA polymerase, mitochondrial [EC:2.7.7.6] C Mitochondrial transcription factors D 100974915 TFAM; transcription factor A, mitochondrial isoform X2 K11830 TFAM; transcription factor A, mitochondrial D 100975128 TFB1M; dimethyladenosine transferase 1, mitochondrial isoform X1 K15266 TFB1M; dimethyladenosine transferase 1, mitochondrial [EC:2.1.1.-] D 100989984 TFB2M; dimethyladenosine transferase 2, mitochondrial isoform X1 K17653 TFB2M; dimethyladenosine transferase 2, mitochondrial [EC:2.1.1.-] C Mitochondrial translation factors D 100977996 MTIF2; translation initiation factor IF-2, mitochondrial isoform X1 K02519 infB; translation initiation factor IF-2 D 100981088 MTIF3; translation initiation factor IF-3, mitochondrial isoform X2 K02520 infC; translation initiation factor IF-3 D 100973237 EEF1AKMT3; elongation factor Ts, mitochondrial isoform X1 K02357 tsf; elongation factor Ts D 100992686 TUFM; elongation factor Tu, mitochondrial K02358 tuf; elongation factor Tu D 100991789 GFM2; ribosome-releasing factor 2, mitochondrial isoform X1 K02355 fusA; elongation factor G D 100981523 GFM1; elongation factor G, mitochondrial isoform X2 K02355 fusA; elongation factor G D 100987055 MTERF1; transcription termination factor 1, mitochondrial isoform X2 K15031 MTERF; mitochondrial transcription termination factor family protein D 100968938 MTERF2; transcription termination factor 2, mitochondrial K15031 MTERF; mitochondrial transcription termination factor family protein D 100986797 MTERF3; transcription termination factor 3, mitochondrial isoform X1 K15031 MTERF; mitochondrial transcription termination factor family protein D 100994807 MTERF4; transcription termination factor 4, mitochondrial isoform X1 K15031 MTERF; mitochondrial transcription termination factor family protein D 100991948 GUF1; translation factor GUF1, mitochondrial isoform X1 K21594 GUF1; translation factor GUF1, mitochondrial [EC:3.6.5.-] C RNase MRP D 100991865 POP1; ribonucleases P/MRP protein subunit POP1 isoform X1 K01164 POP1; ribonuclease P/MRP protein subunit POP1 [EC:3.1.26.5] D 100974550 POP4; ribonuclease P protein subunit p29 K03538 POP4; ribonuclease P protein subunit POP4 [EC:3.1.26.5] D 100967999 POP5; ribonuclease P/MRP protein subunit POP5 isoform X1 K03537 POP5; ribonuclease P/MRP protein subunit POP5 [EC:3.1.26.5] D 100981598 RPP30; ribonuclease P protein subunit p30 isoform X2 K03539 RPP1; ribonuclease P/MRP protein subunit RPP1 [EC:3.1.26.5] D 100981838 POP7; ribonuclease P protein subunit p20 K14527 RPP20; ribonuclease P/MRP protein subunit RPP20 [EC:3.1.26.5] D 100975082 RPP25L; ribonuclease P protein subunit p25-like protein K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5] D 117976063 RPP25; ribonuclease P protein subunit p25 K14525 RPP25; ribonucleases P/MRP protein subunit RPP25 [EC:3.1.26.5] D 100968684 RPP38; ribonuclease P protein subunit p38 K14523 RPP38; ribonucleases P/MRP protein subunit RPP38 [EC:3.1.26.5] D 100978407 RPP40; ribonuclease P protein subunit p40 isoform X1 K14530 RPP40; ribonucleases P/MRP protein subunit RPP40 [EC:3.1.26.5] C Mitochondrial ribonuclease P D 100987585 TRMT10C; tRNA methyltransferase 10 homolog C K17654 TRMT10C; mitochondrial ribonuclease P protein 1 [EC:2.1.1.-] D 100971848 HSD17B10; 3-hydroxyacyl-CoA dehydrogenase type-2 K08683 HSD17B10; 3-hydroxyacyl-CoA dehydrogenase / 3-hydroxy-2-methylbutyryl-CoA dehydrogenase [EC:1.1.1.35 1.1.1.178] D 100988151 PRORP; mitochondrial ribonuclease P catalytic subunit isoform X1 K17655 MRPP3; mitochondrial ribonuclease P protein 3 C Other mitochondrial DNA transcription and translation factors D 100967316 MSS51; putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51 D 100985391 TEFM; transcription elongation factor, mitochondrial K17658 TEFM; transcription elongation factor, mitochondrial D 100975093 PTCD1; pentatricopeptide repeat-containing protein 1, mitochondrial K17710 PTCD1; pentatricopeptide repeat domain-containing protein 1 D 100972551 PTCD2; pentatricopeptide repeat-containing protein 2, mitochondrial isoform X1 K17711 PTCD2; pentatricopeptide repeat domain-containing protein 2 D 100973290 PTCD3; pentatricopeptide repeat domain-containing protein 3, mitochondrial K17659 PTCD3; pentatricopeptide repeat domain-containing protein 3 D 100986439 DHX30; ATP-dependent RNA helicase DHX30 isoform X1 K13185 DHX30; ATP-dependent RNA helicase DHX30 [EC:5.6.2.6] D 100983071 ubiquinol-cytochrome-c reductase complex assembly factor 1 isoform X4 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3 D 100971735 AFG1L; AFG1-like ATPase isoform X2 K18798 AFG1; peroxisome-assembly ATPase [EC:3.6.4.7] D 100970722 ATP23; mitochondrial inner membrane protease ATP23 homolog isoform X1 K18156 ATP23; mitochondrial inner membrane protease ATP23 [EC:3.4.24.-] D 100969288 SUPV3L1; ATP-dependent RNA helicase SUPV3L1, mitochondrial isoform X1 K17675 SUPV3L1; ATP-dependent RNA helicase SUPV3L1/SUV3 [EC:5.6.2.6] D 100975880 LACTB2; endoribonuclease LACTB2 K16639 LACTB2; endoribonuclease LACTB2 [EC:3.1.27.-] D 100991246 SLC25A5; ADP/ATP translocase 2 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31 D 100984012 SLC25A31; ADP/ATP translocase 4 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31 D 100981051 ADP/ATP translocase 3-like K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31 D 100971042 SLC25A4; ADP/ATP translocase 1 K05863 SLC25A4S; solute carrier family 25 (mitochondrial adenine nucleotide translocator), member 4/5/6/31 D 100968292 SLC25A37; mitoferrin-1 isoform X1 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37 D 100995805 SLC25A28; mitoferrin-2 isoform X1 K15113 SLC25A28_37; solute carrier family 25 (mitochondrial iron transporter), member 28/37 D 100992927 MALSU1; mitochondrial assembly of ribosomal large subunit protein 1 K25803 MALSU1; mitochondrial assembly of ribosomal large subunit protein 1 D 106634818 ERAL1; GTPase Era, mitochondrial isoform X1 K03595 era; GTPase D 100981833 YARS1; tyrosine--tRNA ligase, cytoplasmic K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1] D 100973857 YARS2; tyrosine--tRNA ligase, mitochondrial isoform X1 K01866 YARS; tyrosyl-tRNA synthetase [EC:6.1.1.1] D 100979256 LARS2; probable leucine--tRNA ligase, mitochondrial K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4] D 100994115 LARS1; leucine--tRNA ligase, cytoplasmic isoform X1 K01869 LARS; leucyl-tRNA synthetase [EC:6.1.1.4] D 100974379 DARS2; aspartate--tRNA ligase, mitochondrial isoform X1 K01876 DARS2; aspartyl-tRNA synthetase [EC:6.1.1.12] D 100983769 GARS1; glycine--tRNA ligase K01880 GARS; glycyl-tRNA synthetase [EC:6.1.1.14] D 100970857 RARS1; arginine--tRNA ligase, cytoplasmic K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19] D 100991764 RARS2; probable arginine--tRNA ligase, mitochondrial isoform X2 K01887 RARS; arginyl-tRNA synthetase [EC:6.1.1.19] D 100977392 QRSL1; glutamyl-tRNA(Gln) amidotransferase subunit A, mitochondrial isoform X1 K02433 gatA; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit A [EC:6.3.5.6 6.3.5.7] D 103786557 glutamyl-tRNA(Gln) amidotransferase subunit A, mitochondrial-like K02433 gatA; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit A [EC:6.3.5.6 6.3.5.7] D 100981193 GATB; glutamyl-tRNA(Gln) amidotransferase subunit B, mitochondrial isoform X1 K02434 gatB; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit B [EC:6.3.5.6 6.3.5.7] D 100967433 GATC; glutamyl-tRNA(Gln) amidotransferase subunit C, mitochondrial K02435 gatC; aspartyl-tRNA(Asn)/glutamyl-tRNA(Gln) amidotransferase subunit C [EC:6.3.5.6 6.3.5.7] D 100978933 MTPAP; poly(A) RNA polymerase, mitochondrial K18060 MTPAP; poly(A) RNA polymerase, mitochondrial [EC:2.7.7.19] D 100993820 PDE12; 2',5'-phosphodiesterase 12 isoform X1 K19612 PDE12; 2',5'-phosphodiesterase [EC:3.1.13.4 3.1.4.-] D 100990621 MTG1; mitochondrial ribosome-associated GTPase 1 isoform X2 K19828 MTG1; mitochondrial GTPase 1 D 100968392 NOA1; nitric oxide-associated protein 1 K19832 NOA1; nitric oxide-associated protein 1 D 100967719 NSUN3; tRNA (cytosine(34)-C(5))-methyltransferase, mitochondrial K21969 NSUN3; tRNA (cytosine34-C5)-methyltransferase [EC:2.1.1.-] D 100985399 NSUN4; 5-methylcytosine rRNA methyltransferase NSUN4 isoform X1 K21970 NSUN4; 5-methylcytosine rRNA methyltransferase NSUN4 [EC:2.1.1.-] D 100995616 RPUSD3; mitochondrial mRNA pseudouridine synthase RPUSD3 isoform X1 K22537 RPUSD3; mitochondrial RNA pseudouridine synthase RPUSD3 [EC:5.4.99.-] D 100977585 RPUSD4; mitochondrial RNA pseudouridine synthase RPUSD4 K22538 RPUSD4; mitochondrial RNA pseudouridine synthase RPUSD4 [EC:5.4.99.-] D 100976306 RCC1L; RCC1-like G exchanging factor-like protein K23495 RCC1L; RCC1-like G exchanging factor-like protein D 100973650 neugrin K23496 NGRN; neugrin D 100982474 NGRN; neugrin K23496 NGRN; neugrin D 100972875 TRUB2; mitochondrial mRNA pseudouridine synthase TRUB2 isoform X1 K23497 TRUB2; mitochondrial mRNA pseudouridine synthase TRUB2 [EC:5.4.99.-] D 100971833 FASTKD2; FAST kinase domain-containing protein 2, mitochondrial K18190 FASTKD2; FAST kinase domain-containing protein 2 D 100983270 C12H12orf65; probable peptide chain release factor C12orf65 homolog, mitochondrial K23498 COXPD7; peptide chain release factor D 100981945 RMND1; required for meiotic nuclear division protein 1 homolog isoform X1 K23499 RMND1; required for meiotic nuclear division protein 1 D 100992010 GRSF1; G-rich sequence factor 1 isoform X2 K24984 GRSF1; G-rich sequence factor 1 D 100982623 METTL15; 12S rRNA N4-methylcytidine (m4C) methyltransferase isoform X1 K25876 METTL15; 12S rRNA N4-methylcytidine (m4C) methyltransferase [EC:2.1.1.-] D 100987198 MYG1; UPF0160 protein MYG1, mitochondrial K25877 MYG1; MYG1 exonuclease [EC:3.1.-.-] D 100975595 MTRES1; mitochondrial transcription rescue factor 1 isoform X1 K26186 MTRES1; mitochondrial transcription rescue factor 1 B Mitochondrial DNA replication factors C Mitochondrial DNA polymerase D 100972962 POLG; DNA polymerase subunit gamma-1 isoform X1 K02332 POLG; DNA polymerase gamma 1 [EC:2.7.7.7] D 100978989 POLG2; DNA polymerase subunit gamma-2, mitochondrial isoform X1 K02333 POLG2; DNA polymerase gamma 2 D 100976043 PRIMPOL; DNA-directed primase/polymerase protein isoform X1 K22761 PRIMPOL; DNA-directed primase/polymerase protein [EC:2.7.7.102 2.7.7.7] C Mitochondrial DNA maintenance factors D 100993630 ENDOG; endonuclease G, mitochondrial isoform X2 K01173 ENDOG; endonuclease G, mitochondrial D 100969113 MGME1; mitochondrial genome maintenance exonuclease 1 isoform X2 K19465 MGME1; mitochondrial genome maintenance exonuclease 1 [EC:3.1.-.-] D 100993303 EXOG; nuclease EXOG, mitochondrial isoform X1 K15050 EXOG; nuclease EXOG, mitochondrial D 100972543 TWNK; twinkle protein, mitochondrial isoform X1 K17680 PEO1; twinkle protein [EC:5.6.2.3] D 100992270 PIF1; ATP-dependent DNA helicase PIF1 K15255 PIF1; ATP-dependent DNA helicase PIF1 [EC:5.6.2.3] C Other Mitochondrial DNA replication factors D 100994242 SSBP1; single-stranded DNA-binding protein, mitochondrial isoform X2 K03111 ssb; single-strand DNA-binding protein D 100967961 ATAD3B; ATPase family AAA domain-containing protein 3B isoform X1 K17681 ATAD3A_B; ATPase family AAA domain-containing protein 3A/B D 117979148 ATPase family AAA domain-containing protein 3A isoform X1 K17681 ATAD3A_B; ATPase family AAA domain-containing protein 3A/B D 100982351 ubiquinol-cytochrome-c reductase complex assembly factor 2 K17682 MNF1; mitochondrial nucleoid factor 1 # AMitochondrial protein import machinery B Endoplasmic reticulum membrane and cytosol C ER-mitochondria encounter structure (ERMES) complex C Other ER-memrane and cytosol factors D 100975674 DNAJA2; dnaJ homolog subfamily A member 2 K09503 DNAJA2; DnaJ homolog subfamily A member 2 D 100982812 TOMM34; mitochondrial import receptor subunit TOM34 K17766 TOM34; mitochondrial import receptor subunit TOM34 D 100987561 RHOT1; mitochondrial Rho GTPase 1 isoform X9 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-] D 100993344 HSPA1L; heat shock 70 kDa protein 1-like isoform X1 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 100975645 heat shock 70 kDa protein 1A K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 100974669 HSPA8; heat shock cognate 71 kDa protein K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 100968349 heat shock cognate 71 kDa protein-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 117976053 heat shock 70 kDa protein 6 K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 117976058 LOW QUALITY PROTEIN: heat shock 70 kDa protein 6-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 100975983 HSPA1A; heat shock 70 kDa protein 1A K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 100981595 LOW QUALITY PROTEIN: heat shock cognate 71 kDa protein-like K03283 HSPA1_6_8; heat shock 70kDa protein 1/6/8 D 100970167 AIPL1; aryl-hydrocarbon-interacting protein-like 1 K17767 AIP; AH receptor-interacting protein D 100987419 AIP; AH receptor-interacting protein isoform X1 K17767 AIP; AH receptor-interacting protein B Outer membrane C Transporter outer membrane (TOM) complex D 100975843 TOMM40L; mitochondrial import receptor subunit TOM40B isoform X1 K11518 TOM40; mitochondrial import receptor subunit TOM40 D 100967326 TOMM40; mitochondrial import receptor subunit TOM40 homolog K11518 TOM40; mitochondrial import receptor subunit TOM40 D 100979003 mitochondrial import receptor subunit TOM40 homolog K11518 TOM40; mitochondrial import receptor subunit TOM40 D 100982665 TOMM70; mitochondrial import receptor subunit TOM70 K17768 TOM70; mitochondrial import receptor subunit TOM70 D 100979618 TOMM22; mitochondrial import receptor subunit TOM22 homolog K17769 TOM22; mitochondrial import receptor subunit TOM22 D 100972772 mitochondrial import receptor subunit TOM22 homolog K17769 TOM22; mitochondrial import receptor subunit TOM22 D 117975569 mitochondrial import receptor subunit TOM22 homolog K17769 TOM22; mitochondrial import receptor subunit TOM22 D 100976046 TOMM20; mitochondrial import receptor subunit TOM20 homolog K17770 TOM20; mitochondrial import receptor subunit TOM20 D 100976895 TOMM20L; TOMM20-like protein 1 isoform X4 K17770 TOM20; mitochondrial import receptor subunit TOM20 D 100982023 LOW QUALITY PROTEIN: mitochondrial import receptor subunit TOM20 homolog K17770 TOM20; mitochondrial import receptor subunit TOM20 D 100976619 mitochondrial import receptor subunit TOM20 homolog K17770 TOM20; mitochondrial import receptor subunit TOM20 D 100996141 TOMM7; mitochondrial import receptor subunit TOM7 homolog K17771 TOM7; mitochondrial import receptor subunit TOM7 D 117980319 mitochondrial import receptor subunit TOM7 homolog K17771 TOM7; mitochondrial import receptor subunit TOM7 D 100987737 mitochondrial import receptor subunit TOM6 homolog K17772 TOM6; mitochondrial import receptor subunit TOM6 D 103784109 TOMM6; mitochondrial import receptor subunit TOM6 homolog K17772 TOM6; mitochondrial import receptor subunit TOM6 D 100970724 mitochondrial import receptor subunit TOM6 homolog K17772 TOM6; mitochondrial import receptor subunit TOM6 D 100985579 TOMM5; mitochondrial import receptor subunit TOM5 homolog isoform X2 K17773 TOM5; mitochondrial import receptor subunit TOM5 D 112440082 mitochondrial import receptor subunit TOM5 homolog K17773 TOM5; mitochondrial import receptor subunit TOM5 D 112439852 mitochondrial import receptor subunit TOM5 homolog K17773 TOM5; mitochondrial import receptor subunit TOM5 C TOB/SAM complex D 100986401 SAMM50; sorting and assembly machinery component 50 homolog isoform X1 K07277 SAM50; outer membrane protein insertion porin family C Porin D 100983168 VDAC1; voltage-dependent anion-selective channel protein 1 K05862 VDAC1; voltage-dependent anion channel protein 1 D 100982601 voltage-dependent anion-selective channel protein 1 K05862 VDAC1; voltage-dependent anion channel protein 1 D 100990596 VDAC2; voltage-dependent anion-selective channel protein 2 isoform X1 K15040 VDAC2; voltage-dependent anion channel protein 2 D 100987711 VDAC3; voltage-dependent anion-selective channel protein 3 isoform X2 K15041 VDAC3; voltage-dependent anion channel protein 3 C ERMES complex C Other outer membrane factor D 100989012 MTX2; metaxin-2 isoform X1 K17776 MTX; metaxin D 100978832 MTX3; metaxin-3 isoform X3 K17776 MTX; metaxin D 117974643 metaxin-1-like K17776 MTX; metaxin D 100987557 MTX1; metaxin-1 K17776 MTX; metaxin D 100990050 MYO19; unconventional myosin-XIX isoform X2 K25838 MYO19; myosin XIX D 100995132 ARMCX1; armadillo repeat-containing X-linked protein 1 K26187 ARMCX1; armadillo repeat-containing X-linked protein 1 D 100969468 ARMCX2; armadillo repeat-containing X-linked protein 2 K26188 ARMCX2; armadillo repeat-containing X-linked protein 2 D 100967623 ARMCX3; armadillo repeat-containing X-linked protein 3 K26189 ARMCX3; armadillo repeat-containing X-linked protein 3 D 100995817 protein ARMCX6 K26190 ARMCX6; armadillo repeat-containing X-linked protein 6 D 100988945 MTARC1; mitochondrial amidoxime-reducing component 1 isoform X2 K27318 MTARC; mitochondrial amidoxime-reducing component [EC:1.7.-.-] D 100994672 MTARC2; mitochondrial amidoxime reducing component 2 isoform X1 K27318 MTARC; mitochondrial amidoxime-reducing component [EC:1.7.-.-] B Inter membrane space C Transporter inner membrane (TIM) 9/10 complex D 100977557 TIMM9; mitochondrial import inner membrane translocase subunit Tim9 K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9 D 106635184 mitochondrial import inner membrane translocase subunit Tim9-like K17777 TIM9; mitochondrial import inner membrane translocase subunit TIM9 D 100968196 TIMM10; mitochondrial import inner membrane translocase subunit Tim10 K17778 TIM10; mitochondrial import inner membrane translocase subunit TIM10 D 100987189 mitochondrial import inner membrane translocase subunit Tim10-like K17778 TIM10; mitochondrial import inner membrane translocase subunit TIM10 D 100970900 TIMM10B; mitochondrial import inner membrane translocase subunit Tim10 B K17779 TIM10B; mitochondrial import inner membrane translocase subunit TIM10B C TIM8/13 complex D 100974578 TIMM8B; mitochondrial import inner membrane translocase subunit Tim8 B K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8 D 100994105 TIMM8A; mitochondrial import inner membrane translocase subunit Tim8 A isoform X1 K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8 D 117977580 mitochondrial import inner membrane translocase subunit Tim8 B-like K17780 TIM8; mitochondrial import inner membrane translocase subunit TIM8 D 100982430 TIMM13; mitochondrial import inner membrane translocase subunit Tim13 K17781 TIM13; mitochondrial import inner membrane translocase subunit TIM13 C Mitochondrial intermembrane space assembly (MIA) complex D 100994332 CHCHD4; mitochondrial intermembrane space import and assembly protein 40 isoform X2 K17782 MIA40; mitochondrial intermembrane space import and assembly protein 40 D 100969913 GFER; FAD-linked sulfhydryl oxidase ALR K17783 ERV1; mitochondrial FAD-linked sulfhydryl oxidase [EC:1.8.3.2] B Inner mambrane C MICOS complex D 100979124 MICOS10; MICOS complex subunit MIC10 K17784 MICOS10; MICOS complex subunit MIC10 D 100973643 IMMT; MICOS complex subunit MIC60 isoform X3 K17785 IMMT; MICOS complex subunit MIC60 D 100978699 MICOS13; MICOS complex subunit MIC13 isoform X2 K24624 MICOS13; MICOS complex subunit MIC13 D 100973039 CHCHD3; MICOS complex subunit MIC19 isoform X2 K17563 CHCHD3; MICOS complex subunit MIC19 D 100972824 CHCHD6; MICOS complex subunit MIC25 isoform X1 K17564 CHCHD6; MICOS complex subunit MIC25 D 100993010 APOO; MICOS complex subunit MIC26 isoform X2 K24625 APOO; MICOS complex subunit MIC26 D 100969810 APOOL; MICOS complex subunit MIC27 isoform X2 K24626 APOOL; MICOS complex subunit MIC27 C MICOS complex (yeast) D 100979124 MICOS10; MICOS complex subunit MIC10 K17784 MICOS10; MICOS complex subunit MIC10 D 100973643 IMMT; MICOS complex subunit MIC60 isoform X3 K17785 IMMT; MICOS complex subunit MIC60 C TIM22 complex D 100974109 TIMM22; mitochondrial import inner membrane translocase subunit Tim22 K17790 TIM22; mitochondrial import inner membrane translocase subunit TIM22 C TIM23 complex D 100968668 TIMM23; mitochondrial import inner membrane translocase subunit Tim23 K17794 TIM23; mitochondrial import inner membrane translocase subunit TIM23 D 117974580 TIMM23B; putative mitochondrial import inner membrane translocase subunit Tim23B K17794 TIM23; mitochondrial import inner membrane translocase subunit TIM23 D 100975700 TIMM17A; mitochondrial import inner membrane translocase subunit Tim17-A K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17 D 100981914 TIMM17B; mitochondrial import inner membrane translocase subunit Tim17-B isoform X2 K17795 TIM17; mitochondrial import inner membrane translocase subunit TIM17 D 100968552 TIMM21; mitochondrial import inner membrane translocase subunit Tim21 K17796 TIM21; mitochondrial import inner membrane translocase subunit TIM21 D 100972796 TIMM50; mitochondrial import inner membrane translocase subunit TIM50 isoform X1 K17496 TIM50; mitochondrial import inner membrane translocase subunit TIM50 C Mitochondrial calcium uniporter complex D 100990265 MCU; calcium uniporter protein, mitochondrial isoform X1 K20858 MCU; calcium uniporter protein, mitochondrial D 100988800 MICU1; calcium uptake protein 1, mitochondrial isoform X4 K22827 MICU1; calcium uptake protein 1, mitochondrial D 100979362 MICU2; calcium uptake protein 2, mitochondrial isoform X2 K22828 MICU2; calcium uptake protein 2, mitochondrial D 100973041 MCUB; calcium uniporter regulatory subunit MCUb, mitochondrial isoform X1 K22829 MCUB; calcium uniporter regulatory subunit MCUb, mitochondrial D 100993103 SMDT1; essential MCU regulator, mitochondrial K22830 SMDT1; essential MCU regulator, mitochondrial D 100979978 MCUR1; mitochondrial calcium uniporter regulator 1 K22137 MCUR1; mitochondrial calcium uniporter regulator 1 C Other inner membrane factors D 100976873 LETM1; mitochondrial proton/calcium exchanger protein isoform X1 K17800 LETM1; LETM1 and EF-hand domain-containing protein 1, mitochondrial D 100977438 IMMP1L; mitochondrial inner membrane protease subunit 1 isoform X3 K09647 IMP1; mitochondrial inner membrane protease subunit 1 [EC:3.4.21.-] D 100969941 IMMP2L; mitochondrial inner membrane protease subunit 2 isoform X1 K09648 IMP2; mitochondrial inner membrane protease subunit 2 [EC:3.4.21.-] D 100978373 TMEM126A; transmembrane protein 126A isoform X1 K18157 TMEM126A; transmembrane protein 126A D 100978555 transmembrane protein 126A-like K18157 TMEM126A; transmembrane protein 126A D 100973749 MPC1L; mitochondrial pyruvate carrier 1-like protein K22138 MPC1; mitochondrial pyruvate carrier 1 D 100973188 MPC1; mitochondrial pyruvate carrier 1 isoform X1 K22138 MPC1; mitochondrial pyruvate carrier 1 D 100975374 MPC2; mitochondrial pyruvate carrier 2 K22139 MPC2; mitochondrial pyruvate carrier 2 D 100972184 CHCHD10; coiled-coil-helix-coiled-coil-helix domain-containing protein 10, mitochondrial isoform X2 K22759 CHCHD10; coiled-coil-helix-coiled-coil-helix domain-containing protein 10 B Matrix C MMC/PAM proteins D 100975491 TIMM44; mitochondrial import inner membrane translocase subunit TIM44 K17804 TIM44; mitochondrial import inner membrane translocase subunit TIM44 D 100987639 HSPA9; stress-70 protein, mitochondrial K04043 dnaK; molecular chaperone DnaK D 100979138 GRPEL1; grpE protein homolog 1, mitochondrial K03687 GRPE; molecular chaperone GrpE D 100980721 GRPEL2; grpE protein homolog 2, mitochondrial K03687 GRPE; molecular chaperone GrpE D 117980991 grpE protein homolog 1, mitochondrial-like K03687 GRPE; molecular chaperone GrpE D 100974096 mitochondrial import inner membrane translocase subunit TIM14 K09539 DNAJC19; DnaJ homolog subfamily C member 19 D 103786829 LOW QUALITY PROTEIN: mitochondrial import inner membrane translocase subunit TIM14-like K09539 DNAJC19; DnaJ homolog subfamily C member 19 D 103785484 PAM16; mitochondrial import inner membrane translocase subunit TIM16 isoform X1 K17805 PAM16; mitochondrial import inner membrane translocase subunit TIM16 C Other matrix factors D 100975657 PMPCA; mitochondrial-processing peptidase subunit alpha isoform X1 K01412 PMPCA; mitochondrial-processing peptidase subunit alpha [EC:3.4.24.64] D 100986946 PMPCB; mitochondrial-processing peptidase subunit beta isoform X3 K17732 PMPCB; mitochondrial-processing peptidase subunit beta [EC:3.4.24.64] D 100984556 MIPEP; mitochondrial intermediate peptidase isoform X1 K01410 MIPEP; mitochondrial intermediate peptidase [EC:3.4.24.59] D 100981698 HSPD1; 60 kDa heat shock protein, mitochondrial K04077 groEL; chaperonin GroEL [EC:5.6.1.7] D 100975678 LOW QUALITY PROTEIN: 60 kDa heat shock protein, mitochondrial-like K04077 groEL; chaperonin GroEL [EC:5.6.1.7] D 100986001 10 kDa heat shock protein, mitochondrial-like K04078 groES; chaperonin GroES D 100987431 10 kDa heat shock protein, mitochondrial-like K04078 groES; chaperonin GroES D 100970928 10 kDa heat shock protein, mitochondrial-like K04078 groES; chaperonin GroES D 100995392 DNAJA3; dnaJ homolog subfamily A member 3, mitochondrial isoform X3 K09504 DNAJA3; DnaJ homolog subfamily A member 3 D 100976395 TAMM41; phosphatidate cytidylyltransferase, mitochondrial isoform X3 K17807 TAM41; mitochondrial translocator assembly and maintenance protein 41 D 100972950 DNLZ; DNL-type zinc finger protein K17808 ZIM17; mitochondrial protein import protein ZIM17 D 117977106 ETHE1; persulfide dioxygenase ETHE1, mitochondrial isoform X1 K17725 ETHE1; sulfur dioxygenase [EC:1.13.11.18] D 100981280 POLDIP2; polymerase delta-interacting protein 2 K17809 POLDIP2; polymerase delta-interacting protein 2 # AMitochondrial quality control factors B Regulator of mitochondrial biogenesis C Ubiquitas transcription factors D 100974672 CREB1; cyclic AMP-responsive element-binding protein 1 isoform X2 K05870 CREB1; cyclic AMP-responsive element-binding protein 1 D 100991789 GFM2; ribosome-releasing factor 2, mitochondrial isoform X1 K02355 fusA; elongation factor G D 100981523 GFM1; elongation factor G, mitochondrial isoform X2 K02355 fusA; elongation factor G D 100985203 SP1; transcription factor Sp1 isoform X2 K04684 SP1; transcription factor Sp1 D 100988915 YY2; transcription factor YY2 K09201 YY; transcription factor YY D 100990380 YY1; transcriptional repressor protein YY1 K09201 YY; transcription factor YY D 100970789 GABPB2; GA-binding protein subunit beta-2 isoform X3 K09454 GABPB; GA-binding protein transcription factor, beta D 100990750 GABPB1; GA-binding protein subunit beta-1 isoform X1 K09454 GABPB; GA-binding protein transcription factor, beta D 100974915 TFAM; transcription factor A, mitochondrial isoform X2 K11830 TFAM; transcription factor A, mitochondrial C Nuclear respiratory factors D 100986525 NRF1; nuclear respiratory factor 1 isoform X3 K11831 NRF1; nuclear respiratory factor 1 D 100985885 NFE2L2; nuclear factor erythroid 2-related factor 2 isoform X2 K05638 NFE2L2; nuclear factor erythroid 2-related factor 2 D 100991466 metallothionein-1H K14739 MT1_2; metallothionein 1/2 D 100968043 metallothionein-1F-like K14739 MT1_2; metallothionein 1/2 D 100986475 metallothionein-2 K14739 MT1_2; metallothionein 1/2 D 100986809 metallothionein-1E isoform X2 K14739 MT1_2; metallothionein 1/2 D 100987138 metallothionein-1X K14739 MT1_2; metallothionein 1/2 D 100987488 metallothionein-1F K14739 MT1_2; metallothionein 1/2 D 100987821 metallothionein-1B isoform X2 K14739 MT1_2; metallothionein 1/2 D 100988170 metallothionein-1E-like K14739 MT1_2; metallothionein 1/2 D 100986935 MT1HL1; metallothionein 1H-like protein 1 K14739 MT1_2; metallothionein 1/2 D 103783901 metallothionein-1L K14739 MT1_2; metallothionein 1/2 D 100971258 metallothionein-1L-like K14739 MT1_2; metallothionein 1/2 D 100988840 metallothionein-1H K14739 MT1_2; metallothionein 1/2 D 100989170 metallothionein-1A-like K14739 MT1_2; metallothionein 1/2 D 103786987 metallothionein-1L-like K14739 MT1_2; metallothionein 1/2 D 100983490 metallothionein-2-like K14739 MT1_2; metallothionein 1/2 D 103785106 metallothionein-1E-like K14739 MT1_2; metallothionein 1/2 D 117981754 metallothionein-1E-like K14739 MT1_2; metallothionein 1/2 D 100989519 MT3; metallothionein-3 K14740 MT3; metallothionein 3 D 112437434 MT4; metallothionein-4 isoform X2 K14741 MT4; metallothionein 4 C Coactivators D 100990453 PPARGC1A; peroxisome proliferator-activated receptor gamma coactivator 1-alpha isoform X4 K07202 PPARGC1A; alpha peroxisome proliferator-activated receptor gamma coactivator 1-alpha D 100977656 PPARGC1B; peroxisome proliferator-activated receptor gamma coactivator 1-beta isoform X1 K17962 PPARGC1B; peroxisome proliferator-activated receptor gamma coactivator 1-beta D 100983135 PPRC1; peroxisome proliferator-activated receptor gamma coactivator-related protein 1 isoform X1 K17963 PPRC1; peroxisome proliferator-activated receptor gamma coactivator-related protein 1 D 100968822 CRTC1; CREB-regulated transcription coactivator 1 isoform X1 K15309 CRTC1; CREB-regulated transcription coactivator 1 D 100983185 EP300; histone acetyltransferase p300 isoform X2 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48] D 100984888 CREBBP; CREB-binding protein isoform X3 K04498 EP300; E1A/CREB-binding protein [EC:2.3.1.48] C Proteins involved in Fe-S cluster biogenesis D 100988455 NFS1; cysteine desulfurase, mitochondrial isoform X3 K04487 iscS; cysteine desulfurase [EC:2.8.1.7] D 100991951 ISCU; iron-sulfur cluster assembly enzyme ISCU, mitochondrial K22068 ISCU; iron-sulfur cluster assembly enzyme ISCU, mitochondrial D 100978722 LYRM4; LYR motif-containing protein 4 isoform X2 K22069 LYRM4; LYR motif-containing protein 4 D 100981926 FXN; frataxin, mitochondrial isoform X1 K19054 FXN; frataxin [EC:1.16.3.1] D 112440837 frataxin, mitochondrial-like K19054 FXN; frataxin [EC:1.16.3.1] D 100989965 FDX1; adrenodoxin, mitochondrial isoform X1 K22070 FDX1; ferredoxin-1, mitochondrial D 100980818 FDX2; ferredoxin-2, mitochondrial K22071 FDX2; ferredoxin-2, mitochondrial D 100974527 FDXR; NADPH:adrenodoxin oxidoreductase, mitochondrial isoform X13 K18914 FDXR; adrenodoxin-NADP+ reductase [EC:1.18.1.6] D 100987639 HSPA9; stress-70 protein, mitochondrial K04043 dnaK; molecular chaperone DnaK D 100976127 HSCB; iron-sulfur cluster co-chaperone protein HscB isoform X1 K04082 hscB; molecular chaperone HscB D 100984527 SIL1; nucleotide exchange factor SIL1 isoform X1 K14001 SIL1; nucleotide exchange factor SIL1 D 100986326 GLRX5; glutaredoxin-related protein 5, mitochondrial K07390 grxD; monothiol glutaredoxin D 100990980 ISCA1; iron-sulfur cluster assembly 1 homolog, mitochondrial K22063 ISCA1; iron-sulfur cluster assembly 1 D 100969980 iron-sulfur cluster assembly 1 homolog, mitochondrial-like K22063 ISCA1; iron-sulfur cluster assembly 1 D 103783268 iron-sulfur cluster assembly 1 homolog, mitochondrial-like K22063 ISCA1; iron-sulfur cluster assembly 1 D 100974839 iron-sulfur cluster assembly 1 homolog, mitochondrial-like K22063 ISCA1; iron-sulfur cluster assembly 1 D 100980907 ISCA2; iron-sulfur cluster assembly 2 homolog, mitochondrial K22072 ISCA2; iron-sulfur cluster assembly 2 D 117977511 iron-sulfur cluster assembly 2 homolog, mitochondrial-like K22072 ISCA2; iron-sulfur cluster assembly 2 D 100978501 IBA57; putative transferase CAF17, mitochondrial isoform X1 K22073 IBA57; transferase CAF17, mitochondrial [EC:2.1.-.-] D 100994720 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial isoform X1 K22074 NFU1; NFU1 iron-sulfur cluster scaffold homolog, mitochondrial D 100986105 BOLA1; bolA-like protein 1 K22066 BOLA1; BolA-like protein 1 D 100995586 BOLA3; bolA-like protein 3 isoform X1 K22075 BOLA3; BolA-like protein 3 D 100973240 SFXN3; sideroflexin-3 isoform X2 K23500 SFXN1_3; sideroflexin-1/3 D 100988675 SFXN1; sideroflexin-1 isoform X1 K23500 SFXN1_3; sideroflexin-1/3 D 100988296 SFXN2; sideroflexin-2 isoform X2 K23501 SFXN2; sideroflexin-2 D 100974160 SFXN4; sideroflexin-4 isoform X1 K23502 SFXN4; sideroflexin-4 D 100992348 SFXN5; sideroflexin-5 isoform X2 K23503 SFXN5; sideroflexin-5 C Other regulator of mitochondrial biogenesis D 100969017 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform K08765 CPT1A; carnitine O-palmitoyltransferase 1, liver isoform [EC:2.3.1.21] D 100977928 CPT1B; carnitine O-palmitoyltransferase 1, muscle isoform isoform X1 K19523 CPT1B; carnitine O-palmitoyltransferase 1, muscle isoform [EC:2.3.1.21] D 100978250 CPT1C; carnitine O-palmitoyltransferase 1, brain isoform isoform X1 K19524 CPT1C; carnitine O-palmitoyltransferase 1, brain isoform [EC:2.3.1.21] D 100977202 DHTKD1; probable 2-oxoglutarate dehydrogenase E1 component DHKTD1, mitochondrial isoform X1 K15791 DHKTD1; 2-oxoadipate dehydrogenase E1 component [EC:1.2.4.-] D 100991418 FBXL4; F-box/LRR-repeat protein 4 isoform X1 K10270 FBXL4; F-box and leucine-rich repeat protein 4 D 100968960 HCFC1; host cell factor 1 isoform X5 K14966 HCFC1; host cell factor 1 D 100978797 HCFC2; host cell factor 2 isoform X1 K27390 HCFC2; host cell factor 2 D 100978882 HTT; huntingtin isoform X1 K04533 HD; huntingtin D 100984753 ESRRA; steroid hormone receptor ERR1 K08552 NR3B1; estrogen-related receptor alpha D 100979994 ESRRB; steroid hormone receptor ERR2 isoform X1 K08553 NR3B2; estrogen-related receptor beta D 100987874 ESRRG; estrogen-related receptor gamma isoform X3 K08554 NR3B3; estrogen-related receptor gamma D 100987796 NRIP1; nuclear receptor-interacting protein 1 K17965 NRIP1; nuclear receptor-interacting protein 1 D 100975618 PRKAA1; 5'-AMP-activated protein kinase catalytic subunit alpha-1 isoform X2 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31] D 100991417 PRKAA2; 5'-AMP-activated protein kinase catalytic subunit alpha-2 isoform X2 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31] D 100976253 LONP1; lon protease homolog, mitochondrial isoform X1 K08675 PRSS15; ATP-dependent Lon protease [EC:3.4.21.53] D 100984983 SIRT1; NAD-dependent protein deacetylase sirtuin-1 isoform X2 K11411 SIRT1; NAD-dependent protein deacetylase sirtuin 1 [EC:2.3.1.286] D 100976374 SERAC1; protein SERAC1 isoform X1 K23504 SERAC1; protein SERAC1 D 100992840 UXT; protein UXT isoform X3 K26537 UXT; protein UXT D 100974239 PERM1; PGC-1 and ERR-induced regulator in muscle protein 1 K26738 PERM1; PGC-1 and ERR-induced regulator in muscle protein 1 B Mitochondrial respiratory chain complex assembly factors C Complex-I assembly factors D 100985055 NDUFAF1; complex I intermediate-associated protein 30, mitochondrial K18159 NDUFAF1; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 1 D 100974737 NDUFAF2; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2 K18160 NDUFAF2; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2 D 100973525 NDUFAF3; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3 isoform X1 K09008 NDUFAF3; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 3 D 100993519 NDUFAF4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4 K18161 NDUFAF4; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4 D 100988527 NDUFAF5; arginine-hydroxylase NDUFAF5, mitochondrial isoform X1 K18162 NDUFAF5; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 5 [EC:2.1.1.-] D 100982455 NDUFAF6; NADH dehydrogenase (ubiquinone) complex I, assembly factor 6 isoform X1 K18163 NDUFAF6; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 6 D 100980761 NDUFAF7; protein arginine methyltransferase NDUFAF7, mitochondrial isoform X1 K18164 NDUFAF7; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 7 D 117976645 NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 8 K24726 NDUFAF8; NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 8 D 100977453 TMEM126B; complex I assembly factor TMEM126B, mitochondrial isoform X1 K18165 TMEM126B; complex I assembly factor TMEM126B D 100985422 complex I assembly factor TMEM126B, mitochondrial K18165 TMEM126B; complex I assembly factor TMEM126B D 100982723 ECSIT; evolutionarily conserved signaling intermediate in Toll pathway, mitochondrial isoform X1 K04405 ECSIT; evolutionarily conserved signaling intermediate in Toll pathway D 100984976 ACAD9; complex I assembly factor ACAD9, mitochondrial isoform X2 K15980 ACAD9; acyl-CoA dehydrogenase family member 9 [EC:1.3.99.-] D 100992671 NUBPL; iron-sulfur protein NUBPL isoform X1 K03593 mrp; ATP-binding protein involved in chromosome partitioning D 100977027 FOXRED1; FAD-dependent oxidoreductase domain-containing protein 1 isoform X1 K18166 FOXRED1; FAD-dependent oxidoreductase domain-containing protein 1 D 100977734 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial isoform X3 K23164 RTN4IP1; reticulon-4-interacting protein 1, mitochondrial D 100967378 TIMMDC1; complex I assembly factor TIMMDC1, mitochondrial K23505 TIMMDC1; complex I assembly factor TIMMDC1 C Complex-II assembly factors D 100973415 SDHAF1; succinate dehydrogenase assembly factor 1, mitochondrial K18167 SDHAF1; succinate dehydrogenase assembly factor 1 D 103783311 SDHAF2; succinate dehydrogenase assembly factor 2, mitochondrial K18168 SDHAF2; succinate dehydrogenase assembly factor 2 C Complex-III assembly factors D 100988698 mitochondrial chaperone BCS1 isoform X1 K08900 BCS1; mitochondrial chaperone BCS1 D 100992903 TTC19; tetratricopeptide repeat protein 19, mitochondrial isoform X1 K18169 TTC19; tetratricopeptide repeat protein 19, mitochondrial D 100971777 LYRM7; complex III assembly factor LYRM7 K18170 LYRM7; complex III assembly factor LYRM7 D 100983071 ubiquinol-cytochrome-c reductase complex assembly factor 1 isoform X4 K17662 CBP3; cytochrome b pre-mRNA-processing protein 3 D 100982351 ubiquinol-cytochrome-c reductase complex assembly factor 2 K17682 MNF1; mitochondrial nucleoid factor 1 D 100993556 ubiquinol-cytochrome-c reductase complex assembly factor 3 K23165 UQCC3; ubiquinol-cytochrome-c reductase complex assembly factor 3 D 100990880 C16H16orf91; protein CCSMST1 K27339 UQCC4; ubiquinol-cytochrome c reductase complex assembly factor 4 D 100991966 SMIM4; small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5 D 100979023 C12H12orf73; uncharacterized protein C12orf73 homolog K27341 UQCC6; ubiquinol-cytochrome c reductase complex assembly factor 6 D 100991811 STMP1; short transmembrane mitochondrial protein 1 K27319 STMP1; short transmembrane mitochondrial protein 1 D 100986346 short transmembrane mitochondrial protein 1-like K27319 STMP1; short transmembrane mitochondrial protein 1 D 117980973 short transmembrane mitochondrial protein 1-like K27319 STMP1; short transmembrane mitochondrial protein 1 C Complex-IV assembly factors D 100988179 CMC1; COX assembly mitochondrial protein homolog isoform X1 K18171 CMC1; COX assembly mitochondrial protein 1 D 100990402 CMC2; COX assembly mitochondrial protein 2 homolog isoform X3 K18172 CMC2; COX assembly mitochondrial protein 2 D 100977063 cytochrome c oxidase assembly factor 1 homolog isoform X1 K18173 COA1; cytochrome c oxidase assembly factor 1 D 100970874 cytochrome c oxidase assembly factor 3 homolog, mitochondrial K18175 CCDC56; cytochrome c oxidase assembly factor 3, animal type D 100974206 cytochrome c oxidase assembly factor 4 homolog, mitochondrial K18177 COA4; cytochrome c oxidase assembly factor 4 D 103785089 cytochrome c oxidase assembly factor 4 homolog, mitochondrial-like K18177 COA4; cytochrome c oxidase assembly factor 4 D 100967703 cytochrome c oxidase assembly factor 5 K18178 COA5; cytochrome c oxidase assembly factor 5 D 100973340 uncharacterized protein LOC100973340 K18179 COA6; cytochrome c oxidase assembly factor 6 D 100990610 cytochrome c oxidase assembly factor 7 K18180 COA7; cytochrome c oxidase assembly factor 7 D 100980340 protoheme IX farnesyltransferase, mitochondrial K02257 COX10; heme o synthase [EC:2.5.1.141] D 100976343 cytochrome c oxidase assembly protein COX11, mitochondrial isoform X1 K02258 COX11; cytochrome c oxidase assembly protein subunit 11 D 100981933 cytochrome c oxidase assembly protein COX14 K18181 COX14; cytochrome c oxidase assembly factor 14 D 100993532 cytochrome c oxidase assembly protein COX15 homolog isoform X1 K02259 COX15; heme a synthase [EC:1.17.99.9] D 103787041 cytochrome c oxidase assembly protein COX16 homolog, mitochondrial isoform X1 K18182 COX16; cytochrome c oxidase assembly protein subunit 16 D 100970363 cytochrome c oxidase copper chaperone K02260 COX17; cytochrome c oxidase assembly protein subunit 17 D 106635428 cytochrome c oxidase copper chaperone-like K02260 COX17; cytochrome c oxidase assembly protein subunit 17 D 100993710 cytochrome c oxidase assembly protein COX18, mitochondrial isoform X2 K17797 COX18; mitochondrial inner membrane protein COX18 D 100995989 cytochrome c oxidase assembly protein COX19 K18183 COX19; cytochrome c oxidase assembly protein subunit 19 D 100992118 cytochrome c oxidase assembly protein COX20, mitochondrial K18184 COX20; cytochrome c oxidase assembly protein subunit 20 D 100967316 MSS51; putative protein MSS51 homolog, mitochondrial K17656 MSS51; mitochondrial splicing suppressor protein 51 D 100983712 protein PET100 homolog, mitochondrial K18186 PET100; protein PET100, animal type D 100993393 protein PET100 homolog, mitochondrial-like K18186 PET100; protein PET100, animal type D 100971353 LOW QUALITY PROTEIN: protein PET117 homolog, mitochondrial K18188 PET117; protein PET117 D 103784797 protein PET117 homolog, mitochondrial K18188 PET117; protein PET117 D 100991546 OXA1L; mitochondrial inner membrane protein OXA1L K03217 yidC; YidC/Oxa1 family membrane protein insertase D 100983451 surfeit locus protein 1 K14998 SURF1; surfeit locus 1 family protein D 100976808 protein SCO2 homolog, mitochondrial K23755 SCO2; protein SCO2 D 100995944 translational activator of cytochrome c oxidase 1 K18189 TACO1; translational activator of cytochrome c oxidase 1 D 100969437 LRPPRC; leucine-rich PPR motif-containing protein, mitochondrial K17964 LRPPRC; leucine-rich PPR motif-containing protein, mitochondrial D 100994669 cytochrome c oxidase assembly factor 8 isoform X1 K23506 APOPT1; apoptogenic protein 1 D 100991811 STMP1; short transmembrane mitochondrial protein 1 K27319 STMP1; short transmembrane mitochondrial protein 1 D 100986346 short transmembrane mitochondrial protein 1-like K27319 STMP1; short transmembrane mitochondrial protein 1 D 117980973 short transmembrane mitochondrial protein 1-like K27319 STMP1; short transmembrane mitochondrial protein 1 D 100991966 SMIM4; small integral membrane protein 4 K27340 UQCC5; ubiquinol-cytochrome c reductase complex assembly factor 5 D 100968433 TMEM223; transmembrane protein 223 K27342 TMEM223; transmembrane protein 223 C Complex-V assembly factors D 103786383 ATP synthase mitochondrial F1 complex assembly factor 1 K07555 ATPeAF1; ATP synthase mitochondrial F1 complex assembly factor 1 D 100973613 ATPAF1; ATP synthase mitochondrial F1 complex assembly factor 1 isoform X1 K07555 ATPeAF1; ATP synthase mitochondrial F1 complex assembly factor 1 D 100977186 ATPAF2; ATP synthase mitochondrial F1 complex assembly factor 2 isoform X1 K07556 ATPeAF2; ATP synthase mitochondrial F1 complex assembly factor 2 D 100994022 TMEM70; transmembrane protein 70, mitochondrial isoform X1 K17966 TMEM70; transmembrane protein 70, mitochondrial D 100972751 ATP5MPL; ATP synthase subunit ATP5MPL, mitochondrial K18193 MP68; 6.8 kDa mitochondrial proteolipid D 100974862 LOW QUALITY PROTEIN: ATP synthase subunit ATP5MPL, mitochondrial K18193 MP68; 6.8 kDa mitochondrial proteolipid D 100993870 ATP5MD; ATP synthase membrane subunit DAPIT, mitochondrial K18194 USMG5; up-regulated during skeletal muscle growth protein 5 D 112438207 ATP synthase membrane subunit DAPIT, mitochondrial-like K18194 USMG5; up-regulated during skeletal muscle growth protein 5 B Mitochondrial dynamics C Fission and Fusion factors D 100967429 MFN1; mitofusin-1 K21356 MFN1; mitofusin 1 [EC:3.6.5.-] D 100973903 MFN2; mitofusin-2 K06030 MFN2; mitofusin 2 [EC:3.6.5.-] D 100976837 OPA1; dynamin-like 120 kDa protein, mitochondrial isoform X4 K17079 OPA1; optic atrophy protein 1 [EC:3.6.5.5] D 100987559 OPA3; optic atrophy 3 protein isoform X2 K23166 OPA3; optic atrophy 3 protein D 100968594 TRIAP1; TP53-regulated inhibitor of apoptosis 1 K17968 TRIAP1; TRIAP1/MDM35 family protein D 100981191 PARL; presenilins-associated rhomboid-like protein, mitochondrial isoform X1 K09650 PARL; rhomboid-like protein [EC:3.4.21.105] D 100983246 BAK1; bcl-2 homologous antagonist/killer isoform X1 K14021 BAK; Bcl-2 homologous antagonist/killer D 100992204 bcl-2 homologous antagonist/killer-like K14021 BAK; Bcl-2 homologous antagonist/killer D 100991820 BAX; apoptosis regulator BAX isoform X3 K02159 BAX; apoptosis regulator BAX D 100972805 DNM1L; dynamin-1-like protein isoform X3 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5] D 100972410 FIS1; mitochondrial fission 1 protein K17969 FIS1; mitochondrial fission 1 protein D 100992834 SUMO4; small ubiquitin-related modifier 4 K12160 SUMO; small ubiquitin-related modifier D 100994911 small ubiquitin-related modifier 2 K12160 SUMO; small ubiquitin-related modifier D 100970998 small ubiquitin-related modifier 3 K12160 SUMO; small ubiquitin-related modifier D 100985119 SUMO1; small ubiquitin-related modifier 1 isoform X1 K12160 SUMO; small ubiquitin-related modifier D 100988108 SUMO2; small ubiquitin-related modifier 2 K12160 SUMO; small ubiquitin-related modifier D 103785019 small ubiquitin-related modifier 1-like K12160 SUMO; small ubiquitin-related modifier D 117976708 small ubiquitin-related modifier 2-like K12160 SUMO; small ubiquitin-related modifier D 100981897 small ubiquitin-related modifier 2-like K12160 SUMO; small ubiquitin-related modifier D 117977164 small ubiquitin-related modifier 5 K12160 SUMO; small ubiquitin-related modifier D 117977302 SUMO3; small ubiquitin-related modifier 3 K12160 SUMO; small ubiquitin-related modifier D 100982561 SH3GLB1; endophilin-B1 isoform X4 K11248 SH3GLB1; endophilin-B1 D 100995393 MTCH2; mitochondrial carrier homolog 2 isoform X1 K17885 MTCH; mitochondrial carrier D 100967676 MTCH1; mitochondrial carrier homolog 1 isoform X2 K17885 MTCH; mitochondrial carrier D 100973553 MFF; mitochondrial fission factor isoform X7 K22076 MFF; mitochondrial fission factor D 100975386 GDAP1L1; ganglioside-induced differentiation-associated protein 1-like 1 isoform X1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1 D 100992763 GDAP1; ganglioside-induced differentiation-associated protein 1 isoform X1 K22077 GDAP1; ganglioside-induced differentiation-associated protein 1 D 100976213 VAT1; synaptic vesicle membrane protein VAT-1 homolog K23167 VAT1; synaptic vesicle membrane protein VAT-1 D 100971414 MIEF2; mitochondrial dynamics protein MID49 K23507 MIEF1_2; mitochondrial dynamics protein MID51/49 D 100987580 MIEF1; mitochondrial dynamics protein MID51 K23507 MIEF1_2; mitochondrial dynamics protein MID51/49 D 100969225 PLD6; mitochondrial cardiolipin hydrolase K16862 PLD6; mitochondrial cardiolipin hydrolase [EC:3.1.4.-] D 100986813 MIGA1; mitoguardin 1 isoform X1 K27289 MIGA; mitoguardin D 100982789 MIGA2; mitoguardin 2 isoform X1 K27289 MIGA; mitoguardin C Actin cytoskeleton organization D 100970542 ACTG1; actin, cytoplasmic 2 K05692 ACTB_G1; actin beta/gamma 1 D 100990579 actin, cytoplasmic 1 K05692 ACTB_G1; actin beta/gamma 1 D 103784606 actin, alpha skeletal muscle-like K05692 ACTB_G1; actin beta/gamma 1 D 100987964 LOW QUALITY PROTEIN: actin-like K05692 ACTB_G1; actin beta/gamma 1 D 100978440 NAA20; N-alpha-acetyltransferase 20 K17972 NAA20; N-terminal acetyltransferase B complex catalytic subunit [EC:2.3.1.254] D 100971221 NAA25; N-alpha-acetyltransferase 25, NatB auxiliary subunit isoform X1 K17973 NAA25; N-terminal acetyltransferase B complex non-catalytic subunit C Mitochondrial movement D 100967501 PHB; prohibitin K17080 PHB1; prohibitin 1 D 117981690 prohibitin-like isoform X1 K17080 PHB1; prohibitin 1 D 100992543 PHB2; prohibitin-2 K17081 PHB2; prohibitin 2 D 100985417 KTN1; kinectin isoform X1 K17975 KTN1; kinectin C Retention of mitochondria D 100972805 DNM1L; dynamin-1-like protein isoform X3 K17065 DNM1L; dynamin 1-like protein [EC:3.6.5.5] D 100983158 MYO5C; unconventional myosin-Vc isoform X1 K10357 MYO5; myosin V D 100983500 MYO5A; unconventional myosin-Va isoform X1 K10357 MYO5; myosin V D 100986174 MYO5B; unconventional myosin-Vb isoform X1 K10357 MYO5; myosin V D 100993738 XIAP; E3 ubiquitin-protein ligase XIAP K04725 XIAP; E3 ubiquitin-protein ligase XIAP [EC:2.3.2.27] D 100971253 LOW QUALITY PROTEIN: E3 ubiquitin-protein ligase XIAP K04725 XIAP; E3 ubiquitin-protein ligase XIAP [EC:2.3.2.27] D 100970113 LOW QUALITY PROTEIN: baculoviral IAP repeat-containing protein 8 K04725 XIAP; E3 ubiquitin-protein ligase XIAP [EC:2.3.2.27] D 100981646 DIABLO; diablo homolog, mitochondrial isoform X1 K10522 DIABLO; diablo C Morphogenesis factors D 100978725 SNX25; sorting nexin-25 isoform X1 K17887 SNX25; sorting nexin-25 D 100987561 RHOT1; mitochondrial Rho GTPase 1 isoform X9 K07870 RHOT1; mitochondrial Rho GTPase 1 [EC:3.6.5.-] D 100973643 IMMT; MICOS complex subunit MIC60 isoform X3 K17785 IMMT; MICOS complex subunit MIC60 D 100973608 MTFP1; mitochondrial fission process protein 1 isoform X1 K17981 MTFP1; mitochondrial fission process protein 1 D 100987924 DAP3; 28S ribosomal protein S29, mitochondrial isoform X1 K17408 DAP3; small subunit ribosomal protein S29 D 100969945 NEDD4; E3 ubiquitin-protein ligase NEDD4 isoform X2 K10591 NEDD4; E3 ubiquitin-protein ligase NEDD4 [EC:2.3.2.26] D 100988157 OXR1; oxidation resistance protein 1 isoform X7 K25437 OXR1; oxidation resistance protein 1 D 112439315 protein misato homolog 1 isoform X1 K27320 MSTO1; protein misato D 100988711 LOW QUALITY PROTEIN: protein misato homolog 1 K27320 MSTO1; protein misato B Mitophagy factors C Autophagy-related proteins D 100968213 ATG2A; autophagy-related protein 2 homolog A isoform X2 K17906 ATG2; autophagy-related protein 2 D 100974220 ATG2B; autophagy-related protein 2 homolog B isoform X1 K17906 ATG2; autophagy-related protein 2 D 100974819 ATG3; ubiquitin-like-conjugating enzyme ATG3 isoform X2 K08343 ATG3; ubiquitin-like-conjugating enzyme ATG3 D 100981140 ATG4C; cysteine protease ATG4C isoform X1 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 100977632 ATG4D; cysteine protease ATG4D isoform X1 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 100983856 ATG4B; cysteine protease ATG4B isoform X1 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 100985006 ATG4A; cysteine protease ATG4A isoform X1 K08342 ATG4; cysteine protease ATG4 [EC:3.4.22.-] D 100978850 ATG5; autophagy protein 5 isoform X1 K08339 ATG5; autophagy-related protein 5 D 100971207 BECN1; beclin-1 isoform X1 K08334 BECN; beclin D 100994779 BECN2; beclin-2 K08334 BECN; beclin D 100977190 ATG7; ubiquitin-like modifier-activating enzyme ATG7 isoform X4 K08337 ATG7; ubiquitin-like modifier-activating enzyme ATG7 D 100989538 GABARAP; gamma-aminobutyric acid receptor-associated protein K08341 GABARAP; GABA(A) receptor-associated protein D 100992751 GABARAPL1; gamma-aminobutyric acid receptor-associated protein-like 1 isoform X2 K08341 GABARAP; GABA(A) receptor-associated protein D 100973730 GABARAPL2; gamma-aminobutyric acid receptor-associated protein-like 2 K08341 GABARAP; GABA(A) receptor-associated protein D 100980803 gamma-aminobutyric acid receptor-associated protein-like 3 K08341 GABARAP; GABA(A) receptor-associated protein D 100994389 ATG9A; autophagy-related protein 9A isoform X1 K17907 ATG9; autophagy-related protein 9 D 100985541 ATG9B; autophagy-related protein 9B isoform X1 K17907 ATG9; autophagy-related protein 9 D 100967589 ATG10; ubiquitin-like-conjugating enzyme ATG10 isoform X1 K17888 ATG10L; ubiquitin-like-conjugating enzyme ATG10 D 100986285 ATG12; ubiquitin-like protein ATG12 isoform X2 K08336 ATG12; ubiquitin-like protein ATG12 D 100990903 LOW QUALITY PROTEIN: ubiquitin-like protein ATG12 K08336 ATG12; ubiquitin-like protein ATG12 D 100986419 ATG14; beclin 1-associated autophagy-related key regulator K17889 ATG14L; beclin 1-associated autophagy-related key regulator D 100988004 ATG16L1; autophagy-related protein 16-1 isoform X5 K17890 ATG16L1; autophagy-related protein 16-1 D 100987334 ATG16L2; autophagy-related protein 16-2 isoform X1 K20868 ATG16L2; autophagy-related protein 16-2 D 100968649 WIPI1; WD repeat domain phosphoinositide-interacting protein 1 isoform X2 K17908 WIPI1_2; autophagy-related protein 18 D 100985903 WIPI2; WD repeat domain phosphoinositide-interacting protein 2 isoform X3 K17908 WIPI1_2; autophagy-related protein 18 C Parkin-dependent mechanism factors D 100978701 PRKN; E3 ubiquitin-protein ligase parkin isoform X1 K04556 PARK2; parkin [EC:2.3.2.31] D 100975482 RNF41; E3 ubiquitin-protein ligase NRDP1 K11981 RNF41; E3 ubiquitin-protein ligase NRDP1 [EC:2.3.2.27] D 100972539 CLEC16A; protein CLEC16A isoform X6 K19513 CLEC16A; protein CLEC16A D 100991148 PINK1; serine/threonine-protein kinase PINK1, mitochondrial K05688 PINK1; PTEN induced putative kinase 1 [EC:2.7.11.1] D 100981191 PARL; presenilins-associated rhomboid-like protein, mitochondrial isoform X1 K09650 PARL; rhomboid-like protein [EC:3.4.21.105] D 100981358 SQSTM1; sequestosome-1 isoform X2 K14381 SQSTM1; sequestosome 1 D 100974039 TAX1BP1; tax1-binding protein 1 isoform X7 K21347 TAX1BP1; Tax1-binding protein 1 D 100969354 CALCOCO2; calcium-binding and coiled-coil domain-containing protein 2 isoform X1 K21348 CALCOCO2; calcium-binding and coiled-coil domain-containing protein 2 D 100976893 AMBRA1; activating molecule in BECN1-regulated autophagy protein 1 isoform X9 K17985 AMBRA1; activating molecule in BECN1-regulated autophagy protein 1 C Parkin-independent mechanism factors D 100978003 ATG13; autophagy-related protein 13 isoform X2 K08331 ATG13; autophagy-related protein 13 D 100970765 ULK1; serine/threonine-protein kinase ULK1 isoform X1 K21357 ULK1; serine/threonine-protein kinase ULK1 [EC:2.7.11.1] D 100971519 ULK2; serine/threonine-protein kinase ULK2 isoform X1 K08269 ULK2; serine/threonine-protein kinase ULK2 [EC:2.7.11.1] D 100974589 RB1CC1; RB1-inducible coiled-coil protein 1 isoform X1 K17589 RB1CC1; RB1-inducible coiled-coil protein 1 D 100973292 HSP90AB1; heat shock protein HSP 90-beta K04079 HSP90A; molecular chaperone HtpG D 100979779 LOW QUALITY PROTEIN: putative heat shock protein HSP 90-beta 4 K04079 HSP90A; molecular chaperone HtpG D 100983575 HSP90AA1; heat shock protein HSP 90-alpha K04079 HSP90A; molecular chaperone HtpG D 100979428 CDC37; hsp90 co-chaperone Cdc37 K09554 CDC37; cell division cycle protein 37 D 100977875 SMURF2; E3 ubiquitin-protein ligase SMURF2 isoform X1 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26] D 100995165 SMURF1; E3 ubiquitin-protein ligase SMURF1 isoform X1 K04678 SMURF; E3 ubiquitin ligase SMURF1/2 [EC:2.3.2.26] D 100988169 BNIP3L; BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like isoform X1 K15465 BNIP3L; BCL2/adenovirus E1B 19 kDa protein-interacting protein 3-like D 100983132 FUNDC1; FUN14 domain-containing protein 1 K17986 FUNDC1; FUN14 domain-containing protein 1 C Other mitophagy factors D 100975618 PRKAA1; 5'-AMP-activated protein kinase catalytic subunit alpha-1 isoform X2 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31] D 100991417 PRKAA2; 5'-AMP-activated protein kinase catalytic subunit alpha-2 isoform X2 K07198 PRKAA; 5'-AMP-activated protein kinase, catalytic alpha subunit [EC:2.7.11.31] D 100995110 MAP1LC3C; microtubule-associated proteins 1A/1B light chain 3C K10435 MAP1LC; microtubule-associated protein 1 light chain D 100975984 MAP1LC3A; microtubule-associated proteins 1A/1B light chain 3A K10435 MAP1LC; microtubule-associated protein 1 light chain D 100984209 MAP1LC3B2; microtubule-associated proteins 1A/1B light chain 3 beta 2 K10435 MAP1LC; microtubule-associated protein 1 light chain D 100994071 microtubule-associated proteins 1A/1B light chain 3B K10435 MAP1LC; microtubule-associated protein 1 light chain D 100968020 MAP1LC3B; microtubule-associated proteins 1A/1B light chain 3B isoform X1 K10435 MAP1LC; microtubule-associated protein 1 light chain D 100977780 NBR1; next to BRCA1 gene 1 protein isoform X4 K17987 NBR1; next to BRCA1 gene 1 protein D 100971333 TECPR1; tectonin beta-propeller repeat-containing protein 1 isoform X1 K17988 TECPR1; tectonin beta-propeller repeat-containing protein 1 D 100968296 ZFYVE1; zinc finger FYVE domain-containing protein 1 K17603 ZFYVE1; zinc finger FYVE domain-containing protein 1 D 100991461 COASY; bifunctional coenzyme A synthase isoform X2 K02318 COASY; phosphopantetheine adenylyltransferase / dephospho-CoA kinase [EC:2.7.7.3 2.7.1.24] D 100973899 PLA2G6; 85/88 kDa calcium-independent phospholipase A2 isoform X6 K16343 PLA2G6; calcium-independent phospholipase A2 [EC:3.1.1.4] D 100972704 C19H19orf12; protein C19orf12 homolog isoform X1 K23168 MPAN; protein MPAN D 100992471 FUNDC2; FUN14 domain-containing protein 2 K24308 FUNDC2; FUN14 domain-containing protein 2 D 117980728 LOW QUALITY PROTEIN: FUN14 domain-containing protein 2-like K24308 FUNDC2; FUN14 domain-containing protein 2 D 100967735 FUN14 domain-containing protein 2-like K24308 FUNDC2; FUN14 domain-containing protein 2 ! #
#[ BRITE | KEGG2 | KEGG ]
#Last updated: March 14, 2024